scholarly journals Removal of Koos IV acoustic neuroma and auditory brainstem implant in NF2 patient

2021 ◽  
Vol 5 (2) ◽  
pp. V16
Author(s):  
Maria Rosaria Scala ◽  
Pietro Spennato ◽  
Antonio Della Volpe ◽  
Claudia Santoro ◽  
Stefania Picariello ◽  
...  
Keyword(s):  
Acoustic Neuroma ◽  
Cerebellopontine Angle ◽  
Neurofibromatosis Type ◽  
Auditory Brainstem ◽  
Neurofibromatosis Type 2 ◽  
Retrosigmoid Approach ◽  
Residual Hearing ◽  
Auditory Brainstem Implant ◽  
Link Type

The authors present the case of removal of a Koos grade IV right acoustic neuroma in a neurofibromatosis type 2 (NF2) patient, already operated on for left cerebellopontine angle meningioma at 7 years of age and a left acoustic neuroma at 16 years of age. A transpetrosal approach allowed cochlear sensor implantation to detect residual hearing. An enlarged retrosigmoid approach then allowed subtotal microsurgical removal of the lesion; consequently, the authors illustrate the technical nuances of an auditory brainstem implant (ABI). One month after surgery, the ABI was successfully switched on, giving back hearing perception to the patient. The video can be found here: https://stream.cadmore.media/r10.3171/2021.7.FOCVID2188

The Auditory Brainstem Implant in Neurofibromatosis Type 2: Experience from the Manchester Programme

Skull Base ◽  
2008 ◽  
Vol 18 (S 01) ◽  
Author(s):  
Simon Freeman ◽  
Richard Ramsden ◽  
Shakeel Saeed ◽  
Martin O'Driscoll ◽  
Deborah Mawman ◽  
...  
Keyword(s):  
Neurofibromatosis Type ◽  
Auditory Brainstem ◽  
Neurofibromatosis Type 2 ◽  
Auditory Brainstem Implant

scholarly journals Restoration of Hearing with an Auditory Brainstem Implant in a Patient with Neurofibromatosis Type 2

2000 ◽  
Vol 40 (10) ◽  
pp. 524-527 ◽  
Author(s):  
Yojiro SEKI ◽  
Hiromichi UMEZU ◽  
Masaaki USUI ◽  
Kozo KUMAKAWA ◽  
Fumiai KUMAGAI ◽  
...  
Keyword(s):  
Neurofibromatosis Type ◽  
Auditory Brainstem ◽  
Neurofibromatosis Type 2 ◽  
Auditory Brainstem Implant

Auditory Brainstem Implant: I. Issues in Surgical Implantation

1993 ◽  
Vol 108 (6) ◽  
pp. 624-633 ◽  
Author(s):  
Derald E. Brackmann ◽  
William E. Hitselberger ◽  
Ralph A. Nelson ◽  
Jean Moore ◽  
Michael D. Waring ◽  
...  
Keyword(s):  
Single Channel ◽  
Cranial Nerves ◽  
Neurofibromatosis Type ◽  
Auditory Brainstem ◽  
Neurofibromatosis Type 2 ◽  
Electrode Placement ◽  
Anatomic Landmarks ◽  
Auditory Evoked Response ◽  
Auditory Brainstem Implant

Most patients with neurofibromatosis type 2 (NF2) are totally deaf after removal of their bilateral acoustic neuromas. Twenty-five patients with neurofibromatosis type 2 have been implanted with a brainstem electrode during surgery to remove an acoustic neuroma. The electrode is positioned in the lateral recess of the fourth ventricle, adjacent to the cochlear nuclei. The present electrode consists of three platinum plates mounted on a Dacron mesh backing, a design that has been demonstrated to be biocompatible and positionally stable in an animal model. Correct electrode placement depends on accurate identification of anatomic landmarks from the translabyrinthine surgical approach and also on Intrasurglcal electrophysiologic monitoring. Some tumors and their removal can result in significant distortion of the brainstem and surrounding structures. Even in the absence of Identifiable anatomic landmarks, electrode location can be adjusted during surgical placement to find the location that maximizes the auditory evoked response and minimizes activation of other monitored cranial nerves. Stimulation of the electrodes produces auditory sensations in most patients, with results similar to those of single-channel cochlear Implants. A coordinated multldlscipllnary team is essential for successful application of an auditory brainstem implant.

Use of a Multichannel Auditory Brainstem Implant for Neurofibromatosis Type 2

2003 ◽  
Vol 81 (1-4) ◽  
pp. 110-114 ◽  
Author(s):  
Marc S. Schwartz ◽  
Steven R. Otto ◽  
Derald E. Brackmann ◽  
William E. Hitselberger ◽  
Robert V. Shannon
Keyword(s):  
Neurofibromatosis Type ◽  
Auditory Brainstem ◽  
Neurofibromatosis Type 2 ◽  
Auditory Brainstem Implant

scholarly journals Cochlear Implantation in Patients with Neurofibromatosis Type 2 and Patients with Vestibular Schwannoma in the Only Hearing Ear

2012 ◽  
Vol 2012 ◽  
pp. 1-12 ◽  
Author(s):  
Erika Celis-Aguilar ◽  
Luis Lassaletta ◽  
Javier Gavilán
Keyword(s):  
Cochlear Implants ◽  
Vestibular Schwannoma ◽  
Cochlear Implantation ◽  
Neurofibromatosis Type ◽  
Auditory Brainstem ◽  
Neurofibromatosis Type 2 ◽  
Environmental Sound ◽  
Auditory Brainstem Implant ◽  
Surgical Option

Cochlear implants are a new surgical option in the hearing rehabilitation of patients with neurofibromatosis type 2 (NF2) and patients with vestibular schwannoma (VS) in the only hearing ear. Auditory brainstem implant (ABI) has been the standard surgical treatment for these patients. We performed a literature review of patients with NF2 and patients with VS in the only hearing ear. Cochlear implantation (CI) provided some auditory benefit in all patients. Preservation of cochlear nerve integrity is crucial after VS resection. Results ranged from environmental sound awareness to excellent benefit with telephone use. Promontory stimulation is recommended although not crucial. MRI can be performed safely in cochlear implanted patients.

The restoration of hearing in neurofibromatosis type 2

1995 ◽  
Vol 109 (5) ◽  
pp. 385-389 ◽  
Author(s):  
R. Laszig ◽  
W. P. Sollmann ◽  
N. Marangos
Keyword(s):  
Electrical Stimulation ◽  
Auditory Nerve ◽  
Signal Transmission ◽  
Neurofibromatosis Type ◽  
Auditory Pathway ◽  
Auditory Brainstem ◽  
Neurofibromatosis Type 2 ◽  
Auditory Brainstem Implant ◽  
Stimulation Of

AbstractCentral electrical stimulation of the auditory pathway can allow hearing in patients sufferingfrom deafness localized in the auditory nerve. Developments in a multi-channel auditory brainstem implant based on the Nucleus Mini 22 Cochlear implant with transcutaneous signal transmission is discussed. The devices have been implanted in nine European patients suffering from Neurofibromatosis Type 2. Preliminary speech perception results and patient satisfaction are encouraging, and the data presented include some limited open speech recognition.

Translabyrinthine resection of neurofibromatosis type 2 associated vestibular and facial schwannomas, repair of facial nerve, and placement of auditory brainstem implant

2014 ◽  
Vol 36 (v1supplement) ◽  
pp. 1 ◽  
Author(s):  
Marc S. Schwartz ◽  
Gregory P. Lekovic ◽  
Derald E. Brackmann ◽  
Courtney C. J. Voelker
Keyword(s):  
Facial Nerve ◽  
Vocal Cord Paralysis ◽  
Neurofibromatosis Type ◽  
Auditory Brainstem ◽  
Neurofibromatosis Type 2 ◽  
Facial Nerve Function ◽  
Ipsilateral Side ◽  
Total Resection ◽  
Auditory Brainstem Implant

We present video of gross-total resection of a large cerebellopontine angle tumor consisting of both vestibular and facial schwannoma components via the translabyrinthine route in a patient with neurofibromatosis type 2. The facial nerve is reconstructed using a greater auricular nerve graft, and an auditory brainstem implant is placed. Prior to surgery the patient had no facial nerve function on the operative side and had lost useful hearing. He also had usable vision only on the ipsilateral side and had contralateral vocal cord paralysis.The video can be found here: http://youtu.be/IOkEND-0vhI.

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