scholarly journals Unilateral Papillitis as the Initial Presentation of Hemifacial Atrophy: Case Report and Review of Literature

2020 ◽  
Vol 10 (1) ◽  
pp. 97-101
Author(s):  
Akhlaque Hossain Khan ◽  
Nazmin Ahmed ◽  
Vijay Kumar Raut
Keyword(s):  
Neurologic Manifestations ◽  
Review Of Literature ◽  
Hemifacial Atrophy ◽  
Plastic And Reconstructive Surgery ◽  
Visual Improvement ◽  
Progressive Hemifacial Atrophy ◽  
Threatening Condition ◽  
Parry Romberg Syndrome ◽  
The Right ◽  
Fundoscopic Examination

Papillitis is a vision threatening condition, characterized by inflammation of the optic disc which often mimicked the features of papilledema; hence these patients often referred to the Neurosurgeon to exclude any intracranial pathology. This entity is associated with a number of intracranial, as well as extracranial pathologies. Among them, Parry–Romberg syndrome, also known as progressive hemifacial atrophy (PHA) possesses multiple ophthalmologic and neurologic manifestations. Here we report the case of a 14-year-old girl, who presented with the feature of progressive dimness of vision involving the right eye. Thorough physical examination demonstrated features of PHA overlapping with papillitis on fundoscopic examination. The patient treated with steroids, following which there was visual improvement. After evaluation in our facility, she was referred to department of plastic and reconstructive surgery for aesthetic improvement. Bang. J Neurosurgery 2020; 10(1): 97-101

scholarly journals Parry– Romberg Syndrome: A Case Report

2014 ◽  
Vol 4 (1) ◽  
pp. 67-70 ◽  
Author(s):  
P Devani ◽  
Hira Lal ◽  
A Thakral
Keyword(s):  
Rare Case ◽  
Final Diagnosis ◽  
Rare Entity ◽  
Review Of Literature ◽  
Mri Findings ◽  
Hemifacial Atrophy ◽  
Radiological Features ◽  
Progressive Hemifacial Atrophy ◽  
Parry Romberg Syndrome ◽  
Ct And Mri

The purpose of this report is to present radiological features of a rare entity called Parry-Romberg syndrome (also known as Progressive hemifacial atrophy). The authors report one rare case of a 18 year old female patient with Parry-Romberg syndrome, accompanied by a brief review of literature and various radiological features of this entity. Final diagnosis of a Parry-Romberg syndrome was made on clinical and radiological grounds. Radiologists should be familiar with various radiographic, CT and MRI findings observed in this disorder. DOI: http://dx.doi.org/10.3126/njr.v4i1.11571 Nepalese Journal of Radiology, Vol.4(1) 2014: 67-70

scholarly journals Autologous Fat Transfer to Improve Aesthetic Appearance in Facial Asymmetry from Parry-Romberg Syndrome: A Case Report

2019 ◽  
Vol 34 (2) ◽  
pp. 47-51
Author(s):  
Ma. Nina Kristine Sison ◽  
Emmanuel Tadeus Cruz ◽  
Mark Arjan Fernandez
Keyword(s):  
Facial Asymmetry ◽  
Hemifacial Atrophy ◽  
Fat Transfer ◽  
Autologous Fat ◽  
Autologous Fat Transfer ◽  
Aesthetic Appearance ◽  
Progressive Hemifacial Atrophy ◽  
Parry Romberg Syndrome ◽  
The Right

Objective: To present a case of progressive hemifacial atrophy in a young woman with Parry-Romberg Syndrome and the role of autologous fat transfer to improve her aesthetic appearance and lessen facial asymmetry. Methods: Design:           Case Report Setting:           Tertiary Government Training Hospital Patient:           One Results: A 20-year old woman consulted because of drooping of the right eyelid and gradual thinning of right cheek muscles since age 16.  On examination, the right facial muscles were hypoplastic with prominent facial bony ridges. An MRI scan showed atrophy of the right medial pterygoid and masseter. She underwent autologous fat transfer on the right side of the face to augment the cheek, improve cosmetic appearance and lessen facial asymmetry.   Conclusion: Our patient is satisfied and happy with the outcome and cosmetic appearance of her autologous fat transfer and is ready to undergo the same procedure if the need arises in the future. Although no definite cure exists for Parry Romberg syndrome, our report illustrates the role of autologous fat transfer as an inexpensive, easily harvested and biocompatible material to improve facial asymmetry. The procedure yielded encouraging results, although long-term benefits remain uncertain.   Keywords: Parry-Romberg syndrome; progressive hemifacial atrophy; autologous transplantation  

Unilateral Retinal Vasculitis as the Presenting Manifestation of Parry-Romberg Syndrome (Progressive Hemifacial Atrophy)

2021 ◽  
pp. 247412642110155
Author(s):  
Elizabeth A. Atchison ◽  
Aimee J. Szewka ◽  
Pauline T. Merrill
Keyword(s):  
Soft Tissues ◽  
Retinal Vasculitis ◽  
Subcortical White Matter ◽  
Hemifacial Atrophy ◽  
Progressive Hemifacial Atrophy ◽  
Oral Steroids ◽  
Linear Band ◽  
Parry Romberg Syndrome ◽  
Vitreous Cell ◽  
The Right

Purpose: This work aims to present a case of retinal vasculitis associated with Parry-Romberg syndrome. Method: A case report is presented. Results: A 17-year-old man with new floaters was found to have 20/40 vision with 1+ vitreous cell and retinal vasculitis in the right eye only. Workup for infectious etiologies did not reveal an explanation for the retinal vasculitis. However, magnetic resonance imaging of the head showed areas of linear band-like atrophy and scarring of the scalp and soft tissues as well as areas of gliosis and encephalomalacia in the subcortical white matter, all of which were consistent with Parry-Romberg syndrome. The patient was prescribed oral steroids and methotrexate, and the retinal vasculitis improved. Conclusions: Parry-Romberg syndrome is a rarely reported cause of retinal vasculitis and should be kept in the differential for retinal vasculitis.

Craniofacial Syndromes Part II: Atypical Facial Clefts, Romberg Syndrome, Moebius Syndrome, Fibrous Dysplasia, and Neurofibromatosis

2020 ◽  
Author(s):  
Francesca Saldanha ◽  
Cory M. Resnick ◽  
Carolyn R. Rogers-Vizena
Keyword(s):  
Fibrous Dysplasia ◽  
Treatment Plan ◽  
Moebius Syndrome ◽  
Hemifacial Atrophy ◽  
Mccune Albright Syndrome ◽  
Facial Clefts ◽  
Progressive Hemifacial Atrophy ◽  
Parry Romberg Syndrome ◽  
Albright Syndrome ◽  
Craniofacial Syndromes

This final article of the two-part craniofacial series continues to provide the embryologic and developmental foundations necessary to understand congenital craniofacial pathology. Clinical characteristics and molecular genetics needed to make an accurate diagnosis and formulate a treatment plan will be detailed for atypical craniofacial clefts, Moebius Syndrome, Fibrous Dysplasia, Progressive Hemifacial Atrophy (Parry-Romberg syndrome) and Neurofibromatosis. Details of the operations applied in treatment of these disorders are discussed in separate Scientific American: Plastic Surgery (SAPS) articles as referenced. This review contains 3 tables, and 10 figures, and 42 references. Keywords: craniofacial, Tessier cleft, atypical facial cleft, Romberg syndrome, Parry-Romberg syndrome, Moebius syndrome, fibrous dysplasia, McCune Albright syndrome, neurofibromatosis

scholarly journals Parry Romberg Syndrome with contralateral iridocorneal endothelial syndrome: a unique case

2021 ◽  
Vol 8 (12) ◽  
pp. 1873
Author(s):  
Usha K. Raina ◽  
Shruti Bhattacharya ◽  
Prateeksha Sharma ◽  
Varun Saini
Keyword(s):  
Corneal Edema ◽  
Rare Disorder ◽  
Specular Microscopy ◽  
Unique Case ◽  
Hemifacial Atrophy ◽  
Normal Side ◽  
Ocular Manifestations ◽  
Iridocorneal Endothelial Syndrome ◽  
Progressive Hemifacial Atrophy ◽  
Parry Romberg Syndrome

Parry-Romberg syndrome (PRS) is a rare disorder which causes progressive hemifacial atrophy, with ocular manifestations like hypotony, enophthalmos and corneal edema on the ipsilateral atrophic side. This is a report of a unique case of PRS with contalateral manifestations like ectropion uvea, correctopia and endothelial deposits, along with polymegathism and pleomorphism seen on specular microscopy suggestive of Iridocorneal Endothelial (ICE) Syndrome. ICE syndrome and PRS have not been reported together in any literature so far. This case highlights the importance of a thorough glaucoma workup and corneal examination on the atrophic facial side as well as on the apparently normal side in all cases of PRS.

scholarly journals Progressive hemifacial atrophy Parry Romberg syndrome characteristics of craniofacial morphology

2007 ◽  
Vol 54 (1) ◽  
pp. 52-61
Author(s):  
Angelina Nikodijevic-Latinovic
Keyword(s):  
Subcutaneous Tissue ◽  
Treatment Plan ◽  
Rehabilitation Program ◽  
Craniofacial Morphology ◽  
Dental Arch ◽  
Mandibular Ramus ◽  
Hemifacial Atrophy ◽  
Parry Romberg Syndrome ◽  
The Right ◽  
Facial Hemiatrophy

The aim of this case report was to analyze clinical finding in a patient with rare, Parry Romberg syndrome. The patient was diagnosed with progressive facial hemiatrophy that affected skin, subcutaneous tissue and underlying bony structures. Analysis of study models and cephalometric radiographs confirmed there was insufficient development of the facial right side: asymmetric narrow upper jaw, shorter mandibular ramus and corpus, upper frontal teeth asymmetry, crowding of the upper dental arch on the right side. An orthodontic treatment plan was proposed within the entire rehabilitation program that included collaboration with a maxillofacial and plastic surgeon.

TREATMENT OF PROGRESSIVE HEMIFACIALATROPHY (PARRYROMBERG SYNDROME) WITH POLYMETHYL METHACRYLATE: A CASE REPORT.

2020 ◽  
pp. 1-2
Author(s):  
Roberto Chacur ◽  
Honório Sampaio Menezes ◽  
Nívea Maria Bordin da Silva Chacur ◽  
Danuza Dias Alves ◽  
Rodrigo Cadore Mafaldo ◽  
...  
Keyword(s):  
Case Report ◽  
Polymethyl Methacrylate ◽  
Hemifacial Atrophy ◽  
Aesthetic Result ◽  
Tissue Augmentation ◽  
Progressive Hemifacial Atrophy ◽  
Subcutaneous Layer ◽  
Parry Romberg Syndrome ◽  
Good Aesthetic Result

Progressive hemifacial atrophy, also called Parry-Romberg Syndrome (PRS), is a craniofacial disorder that typically involves the subcutaneous layer of one side of the face.This article We reports a case of a patient treated with polymethylmethacrylate for tissue augmentation and facial volume recovering asymmetry. Polymethylmethacrylate is effective and safe for treating progressive hemifacial atrophy and can leads a good aesthetic result.

Sign in / Sign up

Export Citation Format

Share Document