Choristoma: A rare congenital tumor of the tongue

Head and neck dermoid cysts are lesions relatively rare, which usually occur during childhood as solitary lesions. They are often identified and surgically removed at birth, being uncommon in adults. A 23-year-old male presented with a congenital tumor of the anterior fontanelle, which histopathological examination revealed a dermoid cyst. Surgical intervention is the treatment of choice to remove this lesion. The objective of this study is to report the case, once this type of lesion is rare in adults.

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Congenital Tumor of the Hand and Upper Limb

Plastic and Reconstructive Surgery - Congenital Deformities of the Hand and Upper Limb ◽

10.1007/978-981-10-5101-2_13 ◽

2017 ◽

pp. 445-470

Author(s):

Jinghong Xu ◽

Jialiang Chen ◽

Qifang He ◽

Liulong Zhu ◽

Jianmin Yao

Keyword(s):

Upper Limb ◽

Congenital Tumor

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Intraocular Medulloepithelioma

Archives of Pathology & Laboratory Medicine ◽

10.5858/arpa.2010-0669-rs ◽

2012 ◽

Vol 136 (2) ◽

pp. 212-216 ◽

Cited By ~ 28

Author(s):

Timothy Saunders ◽

Curtis E. Margo

Keyword(s):

Fine Needle Aspiration Biopsy ◽

Needle Aspiration ◽

Good Prognosis ◽

Definitive Diagnosis ◽

Ciliary Epithelium ◽

Histologic Diagnosis ◽

Fine Needle ◽

Congenital Tumor ◽

Mesenchymal Tissue ◽

The Central Nervous System

Intraocular medulloepithelioma is a congenital tumor of the ciliary epithelium that typically presents during the first decade of life. The histologic diagnosis is based on characteristic ribbons of pseudostratified neuroepithelium admixed with loose mesenchymal tissue rich in hyaluronic acid, vaguely resembling developing retina and vitreous. More than a third of medulloepitheliomas contain heteroplastic tissue, which in some cases makes up most of the tumor. Malignant medulloepitheliomas consist of a proliferation of neuroblasts, which in areas can be indistinguishable from retinoblastoma. Unlike its highly malignant counterpart in the central nervous system, intraocular medulloepithelioma has a good prognosis as long as tumor has not spread beyond the eye. Definitive diagnosis and eye-conserving therapy is possible with fine-needle aspiration biopsy. The histologic differential diagnosis of medulloepithelioma is broad, ranging from retinoblastoma and sarcoma to ciliary epithelial adenoma and adenocarcinoma.

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