scholarly journals Genetics of Biliary Atresia: A Work in Progress for a Disease with an Unavoidable Sequela into Liver Cirrhosis following Failure of Hepatic Portoenterostomy

2019 ◽  
Author(s):  
Consolato M. Sergi
Keyword(s):  
Liver Cirrhosis ◽  
Biliary Atresia ◽  
Work In Progress ◽  
Hepatic Portoenterostomy

Intrahepatic biliary cysts after hepatic portoenterostomy in four children with biliary atresia

1989 ◽  
Vol 19 (6-7) ◽  
pp. 471-473 ◽  
Author(s):  
K. Ishii ◽  
S. Matsuo ◽  
Y. Hirayama ◽  
T. Taguchi ◽  
S. Yakabe ◽  
...  
Keyword(s):  
Biliary Atresia ◽  
Hepatic Portoenterostomy

Incidence of intrahepatic biliary cysts in biliary atresia after hepatic portoenterostomy and associated histopathologic findings in the liver and porta hepatis at diagnosis

1999 ◽  
Vol 34 (9) ◽  
pp. 1364-1368 ◽  
Author(s):  
Atsushi Takahashi ◽  
Yoshiaki Tsuchida ◽  
Norio Suzuki ◽  
Minoru Kuroiwa ◽  
Hitoshi Ikeda ◽  
...  
Keyword(s):  
Biliary Atresia ◽  
Porta Hepatis ◽  
Hepatic Portoenterostomy ◽  
Histopathologic Findings

Biliary Atresia

1989 ◽  
Vol 11 (2) ◽  
pp. 57-62
Author(s):  
Elizabeth A. Wanek ◽  
Frederick M. Karrer ◽  
Carlos T. Brandt ◽  
John R. Lilly
Keyword(s):  
Biliary Atresia ◽  
Biliary Obstruction ◽  
Bile Flow ◽  
Bile Ducts ◽  
Current Treatment ◽  
Histopathologic Examination ◽  
The Past ◽  
The World ◽  
Hepatic Portoenterostomy ◽  
Extrahepatic Bile Ducts

Biliary atresia is a pathologic entity in which there is obliteration of some portion of the extrahepatic bile ducts. In the past, occlusion of the proximal ducts (at the liver hilus) was referred to as "noncorrectable" (Fig 1). If only the distal duct is occluded (and the proximal duct is patent), the lesion was referred to as "correctable." The distinction is academic because current treatment and prognosis are identical. The disease is panductular, ie, both extrahepatic and intrahepatic ducts are involved. Early in the disease, however, occlusion is complete only in the extrahepatic system. Without intervention, intrahepatic biliary obstruction and, subsequently, cirrhosis supervene. In the past, except for a few cases of the correctable variant, surgical procedures were unsuccessful until Morio Kasai performed a hepatic portoenterostomy, which was first reported in English in 1968. Bile flow was effectively reestablished in both correctable and noncorrectable forms of biliary atresia. The operation was only successful when done before the patient was 4 months of age. Subsequent confirmation of Kasai's results were reported throughout the world. ETIOLOGY/PATHOLOGY Biliary atresia was originally thought to be a congenital malformation. Careful histopathologic examination of excised surgical specimens indicate that this is not the case; instead, the disease is a dynamic, progressive panductular sclerotic process that may continue in the intrahepatic ducts even after surgical relief of biliary obstruction.

Newly Formed Hepatic Masses in Children with Biliary Atresia after Kasai Hepatic Portoenterostomy

2011 ◽  
Vol 45 (2) ◽  
pp. 160
Author(s):  
Hye Jong Song ◽  
Yeon-Lim Suh
Keyword(s):  
Biliary Atresia ◽  
Hepatic Portoenterostomy

Intrahepatic Biliary Cysts Presenting before Hepatic Portoenterostomy in Biliary Atresia

2006 ◽  
Vol 42 (4) ◽  
pp. 440-442 ◽  
Author(s):  
Emmanuel Mas ◽  
Fernando Alvarez ◽  
Luc L. Oligny ◽  
Steven Martin
Keyword(s):  
Biliary Atresia ◽  
Hepatic Portoenterostomy

Hepatic calcification in an anicteric patient with biliary atresia after hepatic portoenterostomy

1994 ◽  
Vol 36 (3) ◽  
pp. 294-296 ◽  
Author(s):  
AKIRA MATSUI ◽  
MICHIRU NAKAMURA ◽  
TOSHINORI AIHARA ◽  
MAKOTO FURUSE ◽  
NOBUHIKO SASAKI ◽  
...  
Keyword(s):  
Biliary Atresia ◽  
Hepatic Portoenterostomy

Indication for redo hepatic portoenterostomy for insufficient bile drainage in biliary atresia: re-evaluation in the era of liver transplantation

2003 ◽  
Vol 19 (4) ◽  
pp. 256-259 ◽  
Author(s):  
T. Hasegawa ◽  
T. Kimura ◽  
T. Sasaki ◽  
A. Okada ◽  
S. Mushiake
Keyword(s):  
Liver Transplantation ◽  
Biliary Atresia ◽  
Bile Drainage ◽  
Hepatic Portoenterostomy
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