Upper and lower airway compromise in the apert syndrome

1992 ◽  
Vol 44 (1) ◽  
pp. 90-93 ◽  
Author(s):  
M. Michael Cohen ◽  
Sven Kreiborg
Keyword(s):  
Apert Syndrome ◽  
Lower Airway ◽  
Airway Compromise

scholarly journals Anaesthesia management in a child with Apert syndrome with craniosynostosis

2016 ◽  
Vol 06 (03) ◽  
pp. 45-47
Author(s):  
Leena Harshad Parate ◽  
M.C. Nagaraj
Keyword(s):  
Apert Syndrome ◽  
Lower Airway ◽  
Posterior Sagittal Anorectoplasty ◽  
Airway Anatomy ◽  
Multisystem Involvement ◽  
Midfacial Hypoplasia ◽  
Multiple Repeat

AbstractApert syndrome is a rare congenial anomaly with multisystem involvement. It is characterized by craniosynostosis, midfacial hypoplasia and global syndactyly. Altered upper and lower airway anatomy, multiple visceral anomalies and multiple repeat surgeries are main anaesthetic challenges. Here we report a case of seven month old child with Apert syndrome who was posted for posterior sagittal anorectoplasty.

scholarly journals Craniosynostosis: Acrocephalosyndactyly (Apert Syndrome) Diagnosed in a Newborn

PRILOZI ◽  
2017 ◽  
Vol 38 (3) ◽  
pp. 153-155
Author(s):  
Orhideja Stomnaroska ◽  
Dragan Danilovski ◽  
Sanja Ivanovska
Keyword(s):  
Autosomal Dominant ◽  
Ultrasound Examination ◽  
Distal Phalanx ◽  
Apert Syndrome ◽  
Complete Fusion ◽  
Coronal Suture ◽  
Airway Compromise ◽  
Midfacial Hypoplasia ◽  
Hearing Difficulties

AbstractWe report a 10 days old newborn with brachycephaly, midfacial hypoplasia, syndactyly and broad distal phalanx of thumb and big toe. At the 20th gestational weeks an enlargement of the left cerebral ventricle and malformation of the fingers of the hands and toes were noticed on a regular ultrasound examination. The aforementioned malformations were observed at birth and at the age of 11 months. The large fontal was closed; the small one was palpable at the tip of the finger. Brachycephaly was evident with high full forehead, flat occiput, and irregular craniosynostosis especially at the coronal suture. Cutaneous syndactyly was present at both hands (fingers II-V), with almost complete fusion of the second, third and fourth fingers. Distal phalanges of the thumbs were broad as well as distal hallux. There was cutaneous syndactyly of the feet. Mental development at the age of 11 months was normal.Apert syndrome is a sporadic disorder. Rarely, inheritance is autosomal dominant. Appropriate management includes surgical treatment of the syndactylies, follow up of the eventual airway compromise and hearing difficulties. This is a report of a patient identified as a newborn.

Acne in Apert Syndrome

1991 ◽  
Vol 18 (2) ◽  
pp. 407 ◽  
Author(s):  
Bernice Krafchik
Keyword(s):  
Apert Syndrome

Surgical Correction of the Craniofacial Anomalies in Apert Syndrome

1991 ◽  
Vol 18 (2) ◽  
pp. 277-289 ◽  
Author(s):  
John B. Mulliken ◽  
Richard J. Bruneteau
Keyword(s):  
Surgical Correction ◽  
Apert Syndrome ◽  
Craniofacial Anomalies

The Foot in Apert Syndrome

1991 ◽  
Vol 18 (2) ◽  
pp. 391-397 ◽  
Author(s):  
Jung Mah ◽  
James Kasser ◽  
Joseph Upton
Keyword(s):  
Apert Syndrome

The Craniofacial Anatomy of Apert Syndrome

1991 ◽  
Vol 18 (2) ◽  
pp. 237-249 ◽  
Author(s):  
Jeffrey L. Marsh ◽  
Miroslav Galic ◽  
Michael W. Vannier
Keyword(s):  
Apert Syndrome

The Anatomy and Management of the Thumb in Apert Syndrome

1991 ◽  
Vol 18 (2) ◽  
pp. 365-380 ◽  
Author(s):  
Shake Fereshetian ◽  
Joseph Upton
Keyword(s):  
Apert Syndrome

Ocular Aspects of Apert Syndrome

1991 ◽  
Vol 18 (2) ◽  
pp. 315-319 ◽  
Author(s):  
J.R. Bunde
Keyword(s):  
Apert Syndrome

Effect of Surgical Versus Pharmacological Decompression of Ludwig’s Angina on Airway Compromise among Nigerian Patients

2020 ◽  
Author(s):  
Ekaniyere EB
Keyword(s):  
Length Of Hospital Stay ◽  
Surgical Decompression ◽  
Airway Compromise ◽  
Inclusion Criteria ◽  
Hospital Stays ◽  
Ludwig’S Angina ◽  
The Mean ◽  
The University ◽  
Ludwig's Angina ◽  
Gender Type

Background: Even though the decompression of the cellulitis phase of Ludwig’s angina (LA) by surgical or pharmacological approach is well documented, it is unclear which approach is more effective. Objective: We aim to compare the outcome of treatment between surgical versus pharmacological decompression in patients with LA. Subjects and Methods: A retrospective cohort study was designed. Data were collected from the case notes of patients that met the inclusion criteria from 2004 to 2018 at the University of Benin Teaching Hospital, Nigeria.The data were age, gender, type of decompression approach, length of hospital stay (LOS) and airway compromise. Result: A total of 62 patients comprising 37(59.7%) surgical decompression group and 25(40.3%) pharmacological decompression group were studied. Thirty-six (58.1%) males and 26 (41.9%) females were studied. Their mean age and standard deviation were 40.6 years and 11.9 years respectively. The mean length of hospital stays between the pharmacological and surgical decompression groups were 8.05 days and 13.8 days respectively. The incidence of airway compromise in the surgical decompression group was 19.9% lower than that of the pharmacological decompression group (P=0.47), which was not significant. The type of decompression approach also failed to influence the incidence of airway compromise (P = 0.41). Conclusion: The use of surgical versus pharmacological decompression does not significantly alter the incidence of airway compromise in the management of LA. The Patients that had surgical decompression had a shorter stay in the hospital as compared to those who had pharmacological decompression. This was not statistically significant.

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