Noncytotoxic drug therapy for intra-abdominal desmoid tumor in patients with familial adenomatous polyposis

1992 ◽  
Vol 35 (1) ◽  
pp. 29-33 ◽  
Author(s):  
Kunio Tsukada ◽  
James M. Church ◽  
David G. Jagelman ◽  
Victor W. Fazio ◽  
Ellen McGannon ◽  
...  
Keyword(s):  
Drug Therapy ◽  
Familial Adenomatous Polyposis ◽  
Desmoid Tumor ◽  
Adenomatous Polyposis ◽  
Abdominal Desmoid Tumor

Successful treatment of an intra-abdominal desmoid tumor with irinotecan, fluorouracil, and leucovorin plus bevacizumab in a patient with familial adenomatous polyposis

2011 ◽  
Vol 27 (2) ◽  
pp. 257-259 ◽  
Author(s):  
Leonardo Atem Costa ◽  
Loureno Cezana ◽  
Thiago Bueno Oliveira ◽  
Aldo Lourenço Dettino ◽  
Maria Dirlei Begnami ◽  
...  
Keyword(s):  
Familial Adenomatous Polyposis ◽  
Successful Treatment ◽  
Desmoid Tumor ◽  
Adenomatous Polyposis ◽  
Abdominal Desmoid Tumor

Intra-Abdominal Desmoid Tumor as Initial Presentation of Familial Adenomatous Polyposis

2016 ◽  
Vol 111 ◽  
pp. S620-S621
Author(s):  
Fady G. Haddad ◽  
Sandy El Bitar ◽  
Iskandar Barakat ◽  
Liliane Deeb
Keyword(s):  
Familial Adenomatous Polyposis ◽  
Desmoid Tumor ◽  
Initial Presentation ◽  
Adenomatous Polyposis ◽  
Abdominal Desmoid Tumor

scholarly journals Giant Intra-Abdominal Desmoid Tumor in a Young Male without History of Surgery, Trauma, or Familial Adenomatous Polyposis

2018 ◽  
Vol 2018 ◽  
pp. 1-5
Author(s):  
Noritoshi Mizuta ◽  
Kozo Tsunemi
Keyword(s):  
Familial Adenomatous Polyposis ◽  
Desmoid Tumor ◽  
Treatment Plan ◽  
Abdominal Cavity ◽  
Beta Catenin ◽  
Desmoid Tumors ◽  
Adenomatous Polyposis ◽  
History Of Surgery ◽  
History Of ◽  
Abdominal Desmoid Tumor

Desmoid tumors are rare, monoclonal myofibroblastic neoplasms that occur in the extremities, the trunk, and the abdominal cavity. We present a case that is significant for its rarity and for consideration of its treatment plan. A 17-year-old male reported swelling of his abdomen and abdominal pain. He was referred to our hospital with no history of surgery, trauma, or familial adenomatous polyposis. A large tumor in the abdominal cavity was detected by computed tomography, and surgical resection was performed. The tumor was thought to have developed from the anterior lobe of the transverse colon mesentery. It weighed 5.9 kg. Tumor cells with collagen fibers were observed in histopathological examination, but heteromorphism and the nuclear fission image were not apparent. Immunostaining revealed beta-catenin expression in the tumor cell nucleus. Diagnosis was an intra-abdominal desmoid tumor. Currently, there are no signs of recurrence. In this case, preoperative diagnosis was difficult, but surgery was the optimal treatment according to the symptoms. Desmoid tumors have invasive development and common local recurrence, so sufficient range of resection including normal tissue and strict follow-up are necessary.

Desmoid Tumor in Familial Adenomatous Polyposis (FAP)

2008 ◽  
Vol 24 (1) ◽  
pp. 20 ◽  
Author(s):  
Dae Dong Kim ◽  
Chang Sik Yu ◽  
Dong Hyun Hong ◽  
Sang Hun Jung ◽  
Pyong Wha Choi ◽  
...  
Keyword(s):  
Familial Adenomatous Polyposis ◽  
Desmoid Tumor ◽  
Adenomatous Polyposis

scholarly journals Desmoid Tumor Associated With Familial Adenomatous Polyposis: Evaluation With 64-Detector CT Enterography

2012 ◽  
Vol 9 (1) ◽  
pp. 32-6 ◽  
Author(s):  
Oktay Algin ◽  
Sehnaz Evrimler ◽  
Evrim Ozmen ◽  
Melike Metin ◽  
Osman Ersoy ◽  
...  
Keyword(s):  
Familial Adenomatous Polyposis ◽  
Desmoid Tumor ◽  
Adenomatous Polyposis ◽  
Ct Enterography

scholarly journals Variables affecting desmoid tumor risk in Familial Adenomatous Polyposis: A critical review

2021 ◽  
Vol 5 (1) ◽  
Author(s):  
Campos FG ◽  
Bustamante-Lopez L ◽  
Kotze PG ◽  
Martinez CAR
Keyword(s):  
Familial Adenomatous Polyposis ◽  
Critical Review ◽  
Desmoid Tumor ◽  
Adenomatous Polyposis ◽  
Tumor Risk

Giant Desmoid Tumor of the Abdominal Wall Associated with Familial Adenomatous Polyposis

2003 ◽  
Vol 89 (3) ◽  
pp. 331-332 ◽  
Author(s):  
Ugo Marone ◽  
Alfonso Amore ◽  
Luciano Pezzullo ◽  
Nicola Mozzillo
Keyword(s):  
Familial Adenomatous Polyposis ◽  
Abdominal Wall ◽  
Desmoid Tumor ◽  
Complementary Therapies ◽  
Surgical Excision ◽  
Metastatic Potential ◽  
Tumor Type ◽  
Desmoid Tumors ◽  
Adenomatous Polyposis ◽  
Benign Histology

In this paper a case of vast desmoid tumor of the abdominal wall associated with familial adenomatous polyposis is reported. Desmoid tumors represent a particular type of fibrous neoplasms with a higher prevalence in females. They are extremely rare in the sporadic form, while they are found in about 10% of patients affected by familial adenomatous polyposis. Despite their benign histology and the absence of metastatic potential, they can be considered as fibrosarcomas with a low level of malignancy because of their locally invasive nature. The treatment of choice is surgical excision, as wide as possible, aimed at preventing recurrences, which are frequent in this tumor type. The usefulness of complementary therapies such as radiotherapy, hormone or chemotherapy, is not entirely clear.

Patterns of Adenoma Recurrence in Familial Adenomatous Polyposis Patients after Ileal Pouch-Anal Anastomosis

2015 ◽  
Vol 32 (6) ◽  
pp. 421-425 ◽  
Author(s):  
Adam L. Goldstein ◽  
Revital Kariv ◽  
Joseph M. Klausner ◽  
Hagit Tulchinsky
Keyword(s):  
Familial Adenomatous Polyposis ◽  
Desmoid Tumor ◽  
Ileal Pouch ◽  
Medical Center ◽  
Colonic Polyps ◽  
Ileal Pouch Anal Anastomosis ◽  
Adenomatous Polyposis ◽  
Adenoma Recurrence ◽  
Duodenal Adenomas ◽  
Anal Anastomosis

Aim: This study aims at identifying the risk factors for the development of pre-cancerous pouch and/or cuff adenomas post ileal pouch anal anastomosis (IPAA) in familial adenomatous polyposis patients. Method: We retrospectively studied 59 patients operated at a single medical center during a 26-year period. Data on the timing and location of adenoma recurrence were recorded and possible correlations with patients' gender, age, presence of desmoid tumor, duodenal adenomas, type of anastomosis and number of operation stages were analyzed. Results: Thirty-five (59%) patients had at least one adenoma in either the cuff or the pouch, including 20 with isolated cuff adenomas, 4 with isolated pouch adenomas and 11 patients with adenomas in both the pouch and cuff. There was no significant correlation between gender, age at surgery, type of anastomosis, number of operative stages and the development of pouch or cuff adenomas. Desmoid tumor and pouch adenomas were significantly correlated with cuff adenomas formation. Duodenal adenomas were associated with pouch adenomas. There was some relationship between the development of cuff adenomas and the burden of colonic polyps, as well as the presence of duodenal adenomas. Conclusion: Adenomas in both the pouch and cuff commonly occur following IPAA, mandating lifelong annual endoscopic surveillance.

Desmoid tumor of mesentery in familial adenomatous polyposis: a case report

2010 ◽  
Vol 14 (S1) ◽  
pp. 61-62 ◽  
Author(s):  
G. Basdanis ◽  
V. N. Papadopoulos ◽  
S. Panidis ◽  
I. Tzeveleki ◽  
E. Karamanlis ◽  
...  
Keyword(s):  
Case Report ◽  
Familial Adenomatous Polyposis ◽  
Desmoid Tumor ◽  
Adenomatous Polyposis
Sign in / Sign up

Export Citation Format

Share Document