Desmoid Tumor in Familial Adenomatous Polyposis (FAP)

2008 ◽  
Vol 24 (1) ◽  
pp. 20 ◽  
Author(s):  
Dae Dong Kim ◽  
Chang Sik Yu ◽  
Dong Hyun Hong ◽  
Sang Hun Jung ◽  
Pyong Wha Choi ◽  
...  
Keyword(s):  
Familial Adenomatous Polyposis ◽  
Desmoid Tumor ◽  
Adenomatous Polyposis

scholarly journals Desmoid Tumor Associated With Familial Adenomatous Polyposis: Evaluation With 64-Detector CT Enterography

2012 ◽  
Vol 9 (1) ◽  
pp. 32-6 ◽  
Author(s):  
Oktay Algin ◽  
Sehnaz Evrimler ◽  
Evrim Ozmen ◽  
Melike Metin ◽  
Osman Ersoy ◽  
...  
Keyword(s):  
Familial Adenomatous Polyposis ◽  
Desmoid Tumor ◽  
Adenomatous Polyposis ◽  
Ct Enterography

scholarly journals Variables affecting desmoid tumor risk in Familial Adenomatous Polyposis: A critical review

2021 ◽  
Vol 5 (1) ◽  
Author(s):  
Campos FG ◽  
Bustamante-Lopez L ◽  
Kotze PG ◽  
Martinez CAR
Keyword(s):  
Familial Adenomatous Polyposis ◽  
Critical Review ◽  
Desmoid Tumor ◽  
Adenomatous Polyposis ◽  
Tumor Risk

Giant Desmoid Tumor of the Abdominal Wall Associated with Familial Adenomatous Polyposis

2003 ◽  
Vol 89 (3) ◽  
pp. 331-332 ◽  
Author(s):  
Ugo Marone ◽  
Alfonso Amore ◽  
Luciano Pezzullo ◽  
Nicola Mozzillo
Keyword(s):  
Familial Adenomatous Polyposis ◽  
Abdominal Wall ◽  
Desmoid Tumor ◽  
Complementary Therapies ◽  
Surgical Excision ◽  
Metastatic Potential ◽  
Tumor Type ◽  
Desmoid Tumors ◽  
Adenomatous Polyposis ◽  
Benign Histology

In this paper a case of vast desmoid tumor of the abdominal wall associated with familial adenomatous polyposis is reported. Desmoid tumors represent a particular type of fibrous neoplasms with a higher prevalence in females. They are extremely rare in the sporadic form, while they are found in about 10% of patients affected by familial adenomatous polyposis. Despite their benign histology and the absence of metastatic potential, they can be considered as fibrosarcomas with a low level of malignancy because of their locally invasive nature. The treatment of choice is surgical excision, as wide as possible, aimed at preventing recurrences, which are frequent in this tumor type. The usefulness of complementary therapies such as radiotherapy, hormone or chemotherapy, is not entirely clear.

Patterns of Adenoma Recurrence in Familial Adenomatous Polyposis Patients after Ileal Pouch-Anal Anastomosis

2015 ◽  
Vol 32 (6) ◽  
pp. 421-425 ◽  
Author(s):  
Adam L. Goldstein ◽  
Revital Kariv ◽  
Joseph M. Klausner ◽  
Hagit Tulchinsky
Keyword(s):  
Familial Adenomatous Polyposis ◽  
Desmoid Tumor ◽  
Ileal Pouch ◽  
Medical Center ◽  
Colonic Polyps ◽  
Ileal Pouch Anal Anastomosis ◽  
Adenomatous Polyposis ◽  
Adenoma Recurrence ◽  
Duodenal Adenomas ◽  
Anal Anastomosis

Aim: This study aims at identifying the risk factors for the development of pre-cancerous pouch and/or cuff adenomas post ileal pouch anal anastomosis (IPAA) in familial adenomatous polyposis patients. Method: We retrospectively studied 59 patients operated at a single medical center during a 26-year period. Data on the timing and location of adenoma recurrence were recorded and possible correlations with patients' gender, age, presence of desmoid tumor, duodenal adenomas, type of anastomosis and number of operation stages were analyzed. Results: Thirty-five (59%) patients had at least one adenoma in either the cuff or the pouch, including 20 with isolated cuff adenomas, 4 with isolated pouch adenomas and 11 patients with adenomas in both the pouch and cuff. There was no significant correlation between gender, age at surgery, type of anastomosis, number of operative stages and the development of pouch or cuff adenomas. Desmoid tumor and pouch adenomas were significantly correlated with cuff adenomas formation. Duodenal adenomas were associated with pouch adenomas. There was some relationship between the development of cuff adenomas and the burden of colonic polyps, as well as the presence of duodenal adenomas. Conclusion: Adenomas in both the pouch and cuff commonly occur following IPAA, mandating lifelong annual endoscopic surveillance.

Desmoid tumor of mesentery in familial adenomatous polyposis: a case report

2010 ◽  
Vol 14 (S1) ◽  
pp. 61-62 ◽  
Author(s):  
G. Basdanis ◽  
V. N. Papadopoulos ◽  
S. Panidis ◽  
I. Tzeveleki ◽  
E. Karamanlis ◽  
...  
Keyword(s):  
Case Report ◽  
Familial Adenomatous Polyposis ◽  
Desmoid Tumor ◽  
Adenomatous Polyposis

Risk Factors for the Development of Desmoid Tumor After Colectomy in Patients with Familial Adenomatous Polyposis: Multicenter Retrospective Cohort Study in Japan

2016 ◽  
Vol 23 (S4) ◽  
pp. 559-565 ◽  
Author(s):  
Yasufumi Saito ◽  
Takao Hinoi ◽  
Hideki Ueno ◽  
Hirotoshi Kobayashi ◽  
Tsuyoshi Konishi ◽  
...  
Keyword(s):  
Risk Factors ◽  
Cohort Study ◽  
Familial Adenomatous Polyposis ◽  
Retrospective Cohort Study ◽  
Desmoid Tumor ◽  
Retrospective Cohort ◽  
Adenomatous Polyposis

Cranial desmoid tumor associated with homozygous inactivation of the adenomatous polyposis coli gene in a 2-year-old girl with familial adenomatous polyposis

Cancer ◽  
1996 ◽  
Vol 77 (5) ◽  
pp. 972-976 ◽  
Author(s):  
Deepthi C. de Silva ◽  
Morag F. Wright ◽  
David A. J. Stevenson ◽  
Caroline Clark ◽  
Elizabeth S. Gray ◽  
...  
Keyword(s):  
Familial Adenomatous Polyposis ◽  
Adenomatous Polyposis Coli ◽  
Desmoid Tumor ◽  
Adenomatous Polyposis Coli Gene ◽  
Adenomatous Polyposis ◽  
Polyposis Coli

Noncytotoxic drug therapy for intra-abdominal desmoid tumor in patients with familial adenomatous polyposis

1992 ◽  
Vol 35 (1) ◽  
pp. 29-33 ◽  
Author(s):  
Kunio Tsukada ◽  
James M. Church ◽  
David G. Jagelman ◽  
Victor W. Fazio ◽  
Ellen McGannon ◽  
...  
Keyword(s):  
Drug Therapy ◽  
Familial Adenomatous Polyposis ◽  
Desmoid Tumor ◽  
Adenomatous Polyposis ◽  
Abdominal Desmoid Tumor

scholarly journals A Case of Mesenteric Desmoid Tumor of the Small Intestine Associated with Familial Adenomatous Polyposis (FAP)

2007 ◽  
Vol 60 (8) ◽  
pp. 462-466 ◽  
Author(s):  
H. Tokita ◽  
Y. Mori ◽  
K. Katsumata ◽  
H. Saitou ◽  
T. Aoki
Keyword(s):  
Small Intestine ◽  
Familial Adenomatous Polyposis ◽  
Desmoid Tumor ◽  
Adenomatous Polyposis

scholarly journals Turcot Syndrome : A Case of Familial Adenomatous Polyposis with Medulloblastoma, Thyroid Carcinoma and Desmoid Tumor

2020 ◽  
Vol 73 (7) ◽  
pp. 313-319
Author(s):  
Mayu Mikamo ◽  
Masayoshi Yamamoto ◽  
Kosuke Sugiyama ◽  
Katsunori Suzuki ◽  
Yuhi Suzuki ◽  
...  
Keyword(s):  
Familial Adenomatous Polyposis ◽  
Thyroid Carcinoma ◽  
Desmoid Tumor ◽  
Adenomatous Polyposis ◽  
Turcot Syndrome
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