Gastric volvulus associated with congenital diaphragmatic hernia, wandering spleen, and intrathoracic left kidney: CT findings

AbstractCongenital diaphragmatic hernia (CDH) is a rare and severe disorder with a high mortality rate among infants. Unilateral renal agenesis (URA) is a relatively common congenital urinary malformation. Here, we present the case of a newborn infant with left CDH associated with ipsilateral renal agenesis. The male patient was born weighing 3.850 g through normal spontaneous vaginal delivery at 38 weeks and 6 days of gestational age at a maternity hospital. He was transferred to our neonatal intensive care unit due to respiratory distress with tachypnea, grunting and cyanosis after birth. A chest radiography indicated parts of the bowel in the thoracic cavity, consistent with CDH. Renal ultrasonography indicated no kidney structure on the left side and a 5.6 cm right kidney with normal echogenicity. Repair of the diaphragmatic hernia was performed three days after birth. Most of the colon, small bowel, stomach and spleen were located in the left pleural cavity, but the left kidney was not seen. Subsequent dimercaptosuccinic acid scintigraphy indicated non-visualized functional cortical uptake in the left kidney on day 13 after birth. Thus, we report the successful treatment of a patient with CDH accompanied by URA.

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Congenital diaphragmatic hernia with gastric volvulus

Indian Journal of Surgery ◽

10.1007/s12262-007-0039-8 ◽

2007 ◽

Vol 69 (6) ◽

pp. 260-263 ◽

Cited By ~ 5

Author(s):

Prashant Jain ◽

Beejal Sanghavi ◽

Hemanshi Sanghani ◽

S. V. Parelkar ◽

S. S. Borwankar

Keyword(s):

Congenital Diaphragmatic Hernia ◽

Diaphragmatic Hernia ◽

Gastric Volvulus

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Wandering Spleen and Organoaxial Gastric Volvulus after Morgagni Hernia Repair: A Case Report and Review of the Literature

Case Reports in Surgery ◽

10.1155/2016/6450765 ◽

2016 ◽

Vol 2016 ◽

pp. 1-9

Author(s):

Noemi Cantone ◽

Caterina Gulia ◽

Vittorio Miele ◽

Margherita Trinci ◽

Vito Briganti

Keyword(s):

Case Report ◽

Diaphragmatic Hernia ◽

Clinical Presentation ◽

Treatment Options ◽

Gastric Volvulus ◽

Diagnostic Assessment ◽

Wandering Spleen ◽

Review Of The Literature ◽

Morgagni Hernia ◽

Assessment And Treatment

Wandering spleen and gastric volvulus are two rare entities that have been described in association with congenital diaphragmatic hernia. The diagnosis is difficult and any delay can result in ischemia and necrosis of both organs. We present a case of a 13-year-old girl, previously operated on for anterior diaphragmatic hernia and intrathoracic gastric volvulus, that presented to our service for a subdiaphragmatic gastric volvulus recurrence associated with a wandering spleen. In this report we reviewed the literature, analyzing the clinical presentation, diagnostic assessment, and treatment options of both conditions, in particular in the case associated with diaphragmatic hernia.

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Congenital diaphragmatic hernia with ectopic intrathoracic kidney and wandering spleen in a preterm infant

The Internet Journal of Pediatrics and Neonatology ◽

10.5580/438 ◽

2008 ◽

Vol 8 (1) ◽

Keyword(s):

Congenital Diaphragmatic Hernia ◽

Preterm Infant ◽

Diaphragmatic Hernia ◽

Wandering Spleen ◽

Intrathoracic Kidney

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A Case of Fatal Pulmonary Hypoplasia with Congenital Diaphragmatic Hernia, Thoracic Myelomeningocele, and Thoracic Dysplasia

American Journal of Perinatology Reports ◽

10.1055/s-0037-1615791 ◽

2017 ◽

Vol 07 (04) ◽

pp. e234-e237

Author(s):

Ai Ito ◽

Hideshi Fujinaga ◽

Sachiko Matsui ◽

Kumiko Tago ◽

Yuka Iwasaki ◽

...

Keyword(s):

Congenital Diaphragmatic Hernia ◽

Diaphragmatic Hernia ◽

Neonatal Intensive Care ◽

Pulmonary Hypoplasia ◽

Left Kidney ◽

Fatal Case ◽

Male Infant ◽

Skeletal Deformity ◽

Severe Scoliosis ◽

Severe Hydrocephalus

Background Congenital diaphragmatic hernia (CDH) is fatal in severe cases of pulmonary hypoplasia. We experienced a fatal case of pulmonary hypoplasia due to CDH, thoracic myelomeningocele (MMC), and thoracic dysplasia. This constellation of anomalies has not been previously reported. Case Report A male infant with a prenatal diagnosis of thoracic MMC with severe hydrocephalus and scoliosis was born at 36 weeks of gestation. CDH was found after birth and the patient died of respiratory failure due to pulmonary hypoplasia and persistent pulmonary hypertension of the newborn at 30 hours of age despite neonatal intensive care. An autopsy revealed a left CDH without herniation of the liver or stomach into the thoracic cavity, severe hydrocephalus, Chiari malformation type II, MMC with spina bifida from Th4 to Th12, hemivertebrae, fused ribs, deformities of the thoracic cage and legs, short trunk, and agenesis of the left kidney. Conclusion We speculate that two factors may be associated with the severe pulmonary hypoplasia: decreased thoracic space due to the herniation of visceral organs caused by CDH and thoracic dysplasia due to skeletal deformity and severe scoliosis.

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