The utility of liver transplantation to treat acute liver failure caused by adult-onset Still’s disease: case reports

2021 ◽  
Author(s):  
Yuri Ogasawara ◽  
Tomomi Kogiso ◽  
Yoshihito Kotera ◽  
Akiko Omori ◽  
Naoko Konda ◽  
...  
Keyword(s):  
Liver Transplantation ◽  
Liver Failure ◽  
Acute Liver Failure ◽  
Case Reports ◽  
Adult Onset Still’S Disease ◽  
Adult Onset ◽  
Still’S Disease ◽  
Still's Disease ◽  
Disease Case ◽  
Adult Onset Still's Disease

scholarly journals An Adult-Onset Still’s Disease During Pregnancy that Delivered a Neonate with Hemophagocytic Lymphohistiocytosis and Severe Liver Failure Requiring Liver Transplantation: A Case Report and Literature Review

2021 ◽  
Author(s):  
Eri Watanabe ◽  
Yohei Sugiyama ◽  
Hiroaki Sato ◽  
Toshiyuki Imanishi ◽  
Akinari Fukuda ◽  
...  
Keyword(s):  
Liver Transplantation ◽  
Liver Failure ◽  
Acute Liver Failure ◽  
Hemophagocytic Lymphohistiocytosis ◽  
Adult Onset Still’S Disease ◽  
Adult Onset ◽  
Still’S Disease ◽  
Severe Liver ◽  
Still's Disease ◽  
Adult Onset Still's Disease

Abstract Adult-onset Still’s disease (AOSD) is a rare systemic inflammatory disorder of unknown etiology that is categorized as a non-hereditary disease. Neonatal hemophagocytic lymphohistiocytosis (HLH) is also a rare, but potentially fatal condition. Neonatal HLH is one of the causes of neonatal acute liver failure that often requires urgent liver transplantation. The relationship between AOSD during pregnancy and neonatal HLH currently remains unclear. We encountered a case of AOSD that developed during pregnancy, and an offspring was born with neonatal HLH resulting in severe liver failure. The mother with AOSD only presented with liver dysfunction during pregnancy; however, disease activity was exacerbated after delivery. The maternal clinical course was quite severe and refractory that she required biological therapy in addition to high-dose corticosteroids and immunosuppressants. Additionally, the severe condition of the neonate with HLH and acute liver failure required intensive care with the administration of steroids and intravenous immunoglobulin treatments, and ultimately liver transplantation. This is the first case that severe maternal AOSD associated with a neonatal HLH resulted in severe clinical courses. Physicians need to be aware of the risk of a mother with AOSD delivering an offspring with neonatal HLH with potentially acute liver failure.

scholarly journals An autopsy of a case of acute liver failure associated with adult-onset Still's disease.

Kanzo ◽  
1996 ◽  
Vol 37 (3) ◽  
pp. 176-181
Author(s):  
Teruaki KIMURA ◽  
Takahiro YAMASAKI ◽  
Michiari OKUDA ◽  
Shyuji MIZUMACHI ◽  
Mitsuru YASUNAGA ◽  
...  
Keyword(s):  
Liver Failure ◽  
Acute Liver Failure ◽  
Adult Onset Still’S Disease ◽  
Adult Onset ◽  
Still’S Disease ◽  
Still's Disease ◽  
Adult Onset Still's Disease

scholarly journals A case of adult-onset Still's disease with macrophage activation syndrome and acute liver failure

Kanzo ◽  
2012 ◽  
Vol 53 (3) ◽  
pp. 155-163
Author(s):  
Hideki Fujii ◽  
Shogo Takeda ◽  
Satoru Asai ◽  
Yoshiki Hayashi ◽  
Hisayoshi Imanishi ◽  
...  
Keyword(s):  
Liver Failure ◽  
Acute Liver Failure ◽  
Macrophage Activation Syndrome ◽  
Macrophage Activation ◽  
Adult Onset Still’S Disease ◽  
Adult Onset ◽  
Still’S Disease ◽  
Still's Disease ◽  
Adult Onset Still's Disease ◽  
Activation Syndrome

scholarly journals Acute liver transplantation in a 41-year-old male patient presenting symptoms of adult-onset Still's disease

2011 ◽  
Vol 3 (1) ◽  
pp. 9-13
Author(s):  
Fanni Gelley ◽  
Attila Doros ◽  
Tamás Micsik ◽  
János Fazakas ◽  
Imre Fehérvári ◽  
...  
Keyword(s):  
Liver Transplantation ◽  
Male Patient ◽  
Adult Onset Still’S Disease ◽  
Adult Onset ◽  
Still’S Disease ◽  
Presenting Symptoms ◽  
Still's Disease ◽  
Adult Onset Still's Disease

scholarly journals THU0636 Canakinumab treatment in adult-onset still’s disease: case series

2018 ◽  
Author(s):  
S. Ugurlu ◽  
G. Guzelant ◽  
B. Yurttas ◽  
B. Ergezen ◽  
E. Dalkilic ◽  
...  
Keyword(s):  
Case Series ◽  
Adult Onset Still’S Disease ◽  
Adult Onset ◽  
Still’S Disease ◽  
Still's Disease ◽  
Disease Case ◽  
Adult Onset Still's Disease

scholarly journals Adult-Onset Still’s Disease: Case Report

2014 ◽  
Vol 5 (4) ◽  
pp. 120-122
Author(s):  
Ercan Gunduz ◽  
Mehmet Nezir Gullu ◽  
Yilmaz Zengin ◽  
Recep Dursun ◽  
Mustafa Icer ◽  
...  
Keyword(s):  
Case Report ◽  
Adult Onset Still’S Disease ◽  
Adult Onset ◽  
Still’S Disease ◽  
Still's Disease ◽  
Disease Case ◽  
Adult Onset Still's Disease

Prurigo pigmentosa as an atypical persistent plaque-like skin rash in adult-onset Still’s disease: case report and literature review

2013 ◽  
Vol 8 (5) ◽  
pp. 521-529 ◽  
Author(s):  
Asha S Muthalaly ◽  
Joshua Bradish ◽  
Roy Sampson ◽  
Steven T Hugenberg ◽  
Dennis C Ang ◽  
...  
Keyword(s):  
Case Report ◽  
Literature Review ◽  
Skin Rash ◽  
Adult Onset Still’S Disease ◽  
Adult Onset ◽  
Still’S Disease ◽  
Still's Disease ◽  
Disease Case ◽  
Adult Onset Still's Disease
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