scholarly journals Cerebral fat embolism syndrome in sickle cell disease without evidence of shunt

2019 ◽  
Vol 14 ◽  
pp. 19-20 ◽  
Author(s):  
Cody L. Nathan ◽  
Whitley W. Aamodt ◽  
Tanuja Yalamarti ◽  
Calli Dogon ◽  
Paul Kinniry
Keyword(s):  
Sickle Cell Disease ◽  
Sickle Cell ◽  
Fat Embolism ◽  
Cell Disease ◽  
Fat Embolism Syndrome ◽  
Embolism Syndrome ◽  
Cerebral Fat Embolism Syndrome

scholarly journals Successful outcome of three patients with sickle-cell disease and fat embolism syndrome treated with intensive exchange transfusion

2016 ◽  
Vol 5 (1) ◽  
pp. 39-43 ◽  
Author(s):  
Paul Greaves ◽  
Vivek Mathew ◽  
Catherine Peters ◽  
Susan Rowe ◽  
Roger J. Amos ◽  
...  
Keyword(s):  
Sickle Cell Disease ◽  
Sickle Cell ◽  
Exchange Transfusion ◽  
Fat Embolism ◽  
Successful Outcome ◽  
Cell Disease ◽  
Fat Embolism Syndrome ◽  
Embolism Syndrome

scholarly journals Bone marrow necrosis and fat embolism syndrome: a dreadful complication of hemoglobin sickle cell disease

2017 ◽  
Vol 7 (4) ◽  
pp. 42-50 ◽  
Author(s):  
Eduardo Pelegrineti Targueta ◽  
André Carramenha de Góes Hirano ◽  
Fernando Peixoto Ferraz de Campos ◽  
João Augusto dos Santos Martines ◽  
Silvana Maria Lovisolo ◽  
...  
Keyword(s):  
Bone Marrow ◽  
Sickle Cell Disease ◽  
Sickle Cell ◽  
Fat Embolism ◽  
Cell Disease ◽  
Bone Marrow Necrosis ◽  
Fat Embolism Syndrome ◽  
Embolism Syndrome

scholarly journals Sickle cell disease, fat embolism syndrome, and “starfield” pattern on MRI

2018 ◽  
Vol 8 (2) ◽  
pp. 162-164 ◽  
Author(s):  
Jennifer H. Kang ◽  
Charles William Hargett ◽  
Theresa Sevilis ◽  
Matthew Luedke
Keyword(s):  
Sickle Cell Disease ◽  
Sickle Cell ◽  
Fat Embolism ◽  
Cell Disease ◽  
Fat Embolism Syndrome ◽  
Embolism Syndrome

scholarly journals Fat Embolism Syndrome in a Child with Sickle Cell Disease

2019 ◽  
Vol 214 ◽  
pp. 236
Author(s):  
Arielle Maroni ◽  
Stéphane Dauger ◽  
Maryline Chomton
Keyword(s):  
Sickle Cell Disease ◽  
Sickle Cell ◽  
Fat Embolism ◽  
Cell Disease ◽  
Fat Embolism Syndrome ◽  
Embolism Syndrome

Integrating Fat Embolism Syndrome Scoring Indices in Sickle Cell Disease: A Practice Management Review

2017 ◽  
Vol 34 (10) ◽  
pp. 797-804 ◽  
Author(s):  
Keneisha Bailey ◽  
Jagila Wesley ◽  
Adebayo Adeyinka ◽  
Louisdon Pierre
Keyword(s):  
Sickle Cell Disease ◽  
Sickle Cell ◽  
Clinical Course ◽  
Fat Embolism ◽  
Diagnostic Tools ◽  
Acute Chest Syndrome ◽  
Extensive Literature ◽  
Cell Disease ◽  
Fat Embolism Syndrome ◽  
Embolism Syndrome

Fat embolism syndrome (FES) has been described in the literature as a rare complication of sickle cell disease (SCD). A review article published in 2005 reported 24 cases of FES associated with SCD. In many cases, a definitive diagnosis of FES in SCD is made on autopsy because of the lack of early recognition and the paucity of sensitive and specific testing for this syndrome. Patients with FES usually have a fulminant, rapidly deteriorating clinical course with mortality occurring within the first 24 hours. We postulate that FES is not well recognized in SCD and that FES scores are useful diagnostic tools in patients with SCD. We queried the electronic medical records with the diagnostic codes for SCD with acute chest syndrome (ACS), pulmonary embolism, or acute respiratory distress syndrome admitted to our hospital from 2008 to 2016 to identify patients suspected of having FES. In addition, we performed an extensive literature review to evaluate the management practice of pediatric patients with FES and SCD from 1966 to 2016. Six patients met our selection criteria from the hospital records, and 4 case reports from the literature search were also included. We applied the Gurd and Wilson criteria and the Schonfeld Fat Embolism Index to identify patients who met the criteria for FES. Nine patients fulfilled Gurd and Wilson criteria, and 9 patients who were evaluable met the Schonfeld criteria for FES. A rapidly deteriorating clinical course in a patient with SCD presenting with ACS or severe vaso-occlusive crisis should trigger a high index of suspicion for FES. Gurd and Wilson criteria or the Schonfeld Fat Embolism Index are useful diagnostic tools for FES in SCD.

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