Tumor de células claras «sugar tumor» pulmonar. Neoplasia de diagnóstico inusual

The primary clear cell tumor of the lung is an extremely rare benign tumor, which is called “sugar tumor”, because of the large content of glycogen. Here we are presenting essential thrombocythemia and lung clear cell tumor which was not reported before to the best of our knowledge.A 44 years old woman admitted to the clinic with complaint of lassitude lasting for 2 months. In her physical examination the spleen was 3 cm palpable from the costa arch In laboratory findings number of platelet was 1014000 mm³. A 3.5 cm in diameter pulmonary nodule is detected in right upper lobe in the graphy of the lungs. Subsequently computed tomography (CT ) of thorax was carried out. Due to the benign features in the display of the detected nodule, a total excision with curative and diagnostic intentions was performed. Microscopically the tumor were composed of nests of rounded or oval cells with distinct cell borders and optically clear cytoplasm. The nuclei were small. Immunohistochemically the tumor cells expressed HMB-45, NSE and focal S100 antigen. It was diagnosed as clear “sugar” cell tumor. In conclusion, in lung clear cell tumor, it is important to make evaluation in terms of myeloproliferative disease in adults whose thrombocytosis continue after the treatment.

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Clear Cell Sugar Tumor

Soft Tissue Tumors ◽

10.1007/978-3-030-58710-9_53 ◽

2020 ◽

pp. 177-178

Author(s):

Simone Mocellin

Keyword(s):

Clear Cell ◽

Sugar Tumor

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Cathepsin K expression in clear cell “sugar” tumor (PEComa) of the lung

Virchows Archiv ◽

10.1007/s00428-018-2325-1 ◽

2018 ◽

Vol 473 (1) ◽

pp. 55-59 ◽

Cited By ~ 2

Author(s):

Anna Caliò ◽

Maria Cecilia Mengoli ◽

Alberto Cavazza ◽

Giulio Rossi ◽

Claudio Ghimenton ◽

...

Keyword(s):

Clear Cell ◽

Cathepsin K ◽

Sugar Tumor

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Clear cell (“sugar”) tumor of the lung is a lesion strictly related to angiomyolipoma— The concept of a family of lesions characterized by the presence of the perivascular epithelioid cells (PEC)

Pathology ◽

10.1080/00313029400169561 ◽

1994 ◽

Vol 26 (3) ◽

pp. 230-236 ◽

Cited By ~ 205

Author(s):

F. Bonetti ◽

M. Pea ◽

G. Martignoni ◽

G. Zamboni ◽

P. Capelli ◽

...

Keyword(s):

Clear Cell ◽

Epithelioid Cells ◽

Sugar Tumor

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An Inguinal Perivascular Epithelioid Cell Tumor Metastatic to the Orbit

Case Reports in Pathology ◽

10.1155/2018/5749421 ◽

2018 ◽

Vol 2018 ◽

pp. 1-5

Author(s):

Zofia Tynski ◽

Way Chiang ◽

Albert Barrett

Keyword(s):

Clear Cell ◽

Middle Age ◽

Epithelioid Cell ◽

Ligamentum Teres ◽

Cell Tumor ◽

The Third ◽

Perivascular Epithelioid Cell ◽

Mesenchymal Neoplasms ◽

First Case ◽

Sugar Tumor

Malignant PEComas are rare mesenchymal neoplasms. These tumors harbor distinct myomelanocytic phenotype. The PEComa family of tumors includes lymphangioleiomyomatosis, angiomyolipoma, clear cell sugar tumor of the lung, and myomelanocytic tumor of the falciparum ligament/ligamentum teres. PEComas have no known normal cell counterpart. Majority of PEComas are benign and occur predominantly in the middle-age women. These tumors are commonly encountered in the uterus. Herein, we report a 20-year-old woman with a left inguinal mass metastatic to orbit, brain, lumbar spine, and skin at presentation. To our knowledge, this is the first case of metastatic PEComa to the orbit. This is the third case of primary PEComa of the inguinal area.

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