Double-Orifice Right Atrioventricular Valve Associated With Partial Atrioventricular Septal Defect

We report two more patients with the association of postaxial polydactyly and atrioventricular septal defects. Additional cardiac findings, not previously described, were tetralogy of Fallot in the first case, and double orifice right atrioventricular valve in the second child.

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Double orifice left atrioventricular valve—diagnosis and management of an unexpected lesion

Cardiology in the Young ◽

10.1017/s104795110000305x ◽

1995 ◽

Vol 5 (3) ◽

pp. 267-271 ◽

Cited By ~ 7

Author(s):

David B. Brieger ◽

Cameron Ward ◽

Stephen G. Cooper ◽

Graham R. Nunn ◽

Timothy B. Cartmill ◽

...

Keyword(s):

Differential Diagnosis ◽

Septal Defect ◽

Color Doppler ◽

Atrioventricular Septal Defect ◽

Atrioventricular Valve ◽

Cross Sectional ◽

Diagnosis And Management ◽

Uncommon Condition ◽

High Index Of Suspicion ◽

Double Orifice

AbstractDouble orifice left atrioventricular valve is an uncommon condition. This paper describes 10 consecutive patients with the anomaly encountered over 20 months. Diagnosis was assisted by cross-sectional echocardiography and supplementary color Doppler, often requiring non-standard views and a high index of suspicion. There were three anatomical variants—those in which the orifices were equal in size (three of 10 patients), those in which they were unequal and associated with an atrioventricular septal defect (four of 10 patients), and those in which they were unequal in the absence of an atrioventricular septal defect (three of 10 patients). The unequal orifice in both anatomical situations was frequently complicated by valvar regurgitation (six of seven patients). Conservative repair was possible in three of the four patients requiring surgery to the left atrioventricular valve. This condition should be thought of more often in the differential diagnosis of left atrioventricular regurgitation in childhood.

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Atrioventricular septal defect and the left atrioventricular valve at reoperation

Cardiology in the Young ◽

10.1017/s1047951100010441 ◽

1991 ◽

Vol 1 (4) ◽

pp. 374-378 ◽

Cited By ~ 1

Author(s):

Pietro A. Abbruzzese ◽

Giancarlo Crupi ◽

Roberto Tumbarello ◽

Alessandra Napoleone ◽

Maurizio Merlo ◽

...

Keyword(s):

Septal Defect ◽

Atrioventricular Septal Defect ◽

Papillary Muscles ◽

Atrioventricular Valve ◽

Atrioventricular Valves ◽

Defect Repair ◽

Double Orifice

SummaryBetween 1968 and December 1990, 29 patients underwent 33 reoperations for dysfunction of the left atrioventricular valve after correction ofatrioventricular septal defect. Repair of the valve was possible in all 10 patients who, initially, had a common atrioventricular orifice, using straightforward procedures such as closure of the septal commissure and annuloplasties according to Wooler. Additional valvar abnormalities (double orifice; fenestration of leaflets; malpositioned or malformed papillary muscles; and additional clefts) were rare in this group of patients. In contrast, these anomalies were frequent in the 19 patients who, initially, had separate right and left atrioventricular valves.

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