scholarly journals IS SIZE A GOOD PREDICTOR OF DISSECTION RISK IN PATIENTS WITH MARFAN SYNDROME OR BICUSPID AORTIC VALVES? INSIGHTS FROM THE INTERNATIONAL REGISTRY OF ACUTE AORTIC DISSECTION (IRAD)

2012 ◽  
Vol 59 (13) ◽  
pp. E1883 ◽  
Author(s):  
Hasan Siddiqi ◽  
Eric Isselbacher ◽  
Toru Suzuki ◽  
Daniel Montgomery ◽  
Linda Pape ◽  
...  
Keyword(s):  
Aortic Dissection ◽  
Marfan Syndrome ◽  
Good Predictor ◽  
Acute Aortic Dissection ◽  
Aortic Valves ◽  
International Registry ◽  
Bicuspid Aortic Valves

scholarly journals Acute Aortic Dissection in Pregnancy in a Woman with Undiagnosed Marfan Syndrome

2012 ◽  
Vol 2012 ◽  
pp. 1-3 ◽  
Author(s):  
Mandana Master ◽  
Gavin Day
Keyword(s):  
Aortic Dissection ◽  
Marfan Syndrome ◽  
Acute Aortic Dissection ◽  
Congenital Abnormalities ◽  
Surgical Repair ◽  
Phenotypic Expression ◽  
Sudden Onset ◽  
Lower Segment Caesarean Section ◽  
Type B Dissection ◽  
Type A Dissection

We report a case of acute aortic dissection in a lady of 28 weeks of gestation with undiagnosed Marfan syndrome. The patient had been seen in our antenatal clinics. Her history documented in her pregnancy record was negative for genetic/congenital abnormalities. There was no family history documented. Subsequently, at 28 weeks of gestation, the patient presented with sudden onset chest, jaw, and back pain. Further history revealed that her father had died at the age of 27 of an aortic dissection. Echocardiography showed aortic root dissection with occlusion of aortic branches. She subsequently underwent an emergency lower segment caesarean section followed by surgical repair of type A dissection. A simultaneous type B dissection was managed conservatively. On later examination, our patient fulfilled the diagnostic criteria for phenotypic expression of Marfan syndrome. Genetic testing also confirmed that she has a mutation of the fibrillin (FBN 1) gene associated with the disease.

scholarly journals AORTIC DISSECTION DURING PREGNANCY: RESULTS FROM THE INTERNATIONAL REGISTRY OF ACUTE AORTIC DISSECTION (IRAD)

2012 ◽  
Vol 59 (13) ◽  
pp. E1903 ◽  
Author(s):  
Alan C. Braverman ◽  
Kevin Harris ◽  
Reed Pyeritz ◽  
Stuart Hutchison ◽  
Linda Pitler ◽  
...  
Keyword(s):  
Aortic Dissection ◽  
Acute Aortic Dissection ◽  
International Registry

scholarly journals The Characteristics of Acute Aortic Dissection among Young Chinese Patients: A Comparison between Marfan Syndrome and Non-Marfan Syndrome Patients

2009 ◽  
Vol 50 (2) ◽  
pp. 239 ◽  
Author(s):  
Shih-Hung Tsai ◽  
Yen-Yue Lin ◽  
Chin-Wang Hsu ◽  
Yu-Long Chen ◽  
Min-Tser Liao ◽  
...  
Keyword(s):  
Aortic Dissection ◽  
Marfan Syndrome ◽  
Acute Aortic Dissection ◽  
Chinese Patients

STABILISE Technique for a Non-A Non-B Acute Aortic Dissection in Marfan Syndrome

2021 ◽  
Vol 70 ◽  
pp. 569.e5-569.e10
Author(s):  
Raphael J. Soler ◽  
Michel A. Bartoli ◽  
Jeremy Bourenne ◽  
Alberto Riberi ◽  
David Lagier ◽  
...  
Keyword(s):  
Aortic Dissection ◽  
Marfan Syndrome ◽  
Acute Aortic Dissection

AORTIC DISSECTION RELATED TO PREGNANCY: THE INTERNATIONAL REGISTRY OF ACUTE AORTIC DISSECTION (IRAD)

2020 ◽  
Vol 75 (11) ◽  
pp. 2213 ◽  
Author(s):  
Eric Mittauer ◽  
Kevin Harris ◽  
Arturo Evangelista-Masip ◽  
Reed E. Pyeritz ◽  
Derek Brinster ◽  
...  
Keyword(s):  
Aortic Dissection ◽  
Acute Aortic Dissection ◽  
International Registry
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