Mitral atresia with transposed great arteries and normal semilunar valves: a rare combination

2015 ◽  
Vol 26 (3) ◽  
pp. 599-601
Author(s):  
Gopalan Nair Rajesh ◽  
Sandeep Mohanan ◽  
Haridasan Vellani
Keyword(s):  
Blood Flow ◽  
Aortic Valve ◽  
Hypoplastic Left Heart Syndrome ◽  
Pulmonary Blood Flow ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Mitral Atresia ◽  
Rare Combination ◽  
Multiple Levels ◽  
Left Heart Syndrome

AbstractMitral atresia is commonly seen as a part of the spectrum of hypoplastic left heart syndrome, and it is usually associated with multiple levels of systemic outflow tract obstruction. Isolated mitral atresia with a normal aortic valve is extremely rare. We report the rare combination of mitral atresia, transposition of the great arteries, and unobstructed systemic and pulmonary blood flow.

scholarly journals Prenatal Diagnosis and Successful Palliation of Absent Aortic Valve with Hypoplastic Left Heart Syndrome: A Case Report and Review of Literature

2019 ◽  
Vol 09 (02) ◽  
pp. e121-e126
Author(s):  
Amna Qasim ◽  
Chelsea Johnson ◽  
Muhammad Aly ◽  
Ashraf Aly
Keyword(s):  
Prenatal Diagnosis ◽  
Aortic Valve ◽  
Hypoplastic Left Heart Syndrome ◽  
Main Pulmonary Artery ◽  
Aortic Insufficiency ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Absent Aortic Valve ◽  
Aortic Valve Leaflets ◽  
Left Heart Syndrome

Introduction Congenital absence of the aortic valve leaflets is a rare association with hypoplastic left heart syndrome (HLHS). Case A 37-year-old pregnant woman was referred for fetal evaluation of possible HLHS at 22 weeks of gestation. The fetal echocardiogram (ECHO) was remarkable for a hypoplastic left atrium, nearly atretic mitral valve, small left ventricle, and a hypoplastic aortic valve with severe aortic insufficiency. A female infant was born at term and postnatal ECHO confirmed the above findings. In addition, there was complete absence of the aortic valve leaflets. The patient underwent Norwood's procedure at day 5 of life with atrial septectomy, over-sewing of the aortic valve annulus, and a 4 mm Sano's shunt between the right ventricle and the main pulmonary artery. She tolerated this surgery well and subsequently underwent a bidirectional Glenn's procedure at 8 months of life. Conclusion Prenatal diagnosis of absent aortic valve should be suspected in the presence of severe aortic insufficiency in the fetal ECHO. Early postnatal intervention is critical as those patients are likely to deteriorate quickly. The over-sewing of the aortic valve may be important to prevent coronary steal and myocardial hypoperfusion which could potentially be detrimental.

scholarly journals Fontan operation for hypoplastic left heart syndrome with absent aortic valve

2004 ◽  
Vol 128 (2) ◽  
pp. 315-316 ◽  
Author(s):  
Narutoshi Hibino ◽  
Yorikazu Harada ◽  
Takeshi Hiramatsu ◽  
Satoshi Yasukochi ◽  
Gengi Satomi
Keyword(s):  
Aortic Valve ◽  
Hypoplastic Left Heart Syndrome ◽  
Fontan Operation ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Absent Aortic Valve ◽  
Left Heart Syndrome

scholarly journals Myocardial blood flow and viability in children post palliation of hypoplastic left heart syndrome assessed with MRI

2015 ◽  
Vol 17 (S1) ◽  
Author(s):  
Philip Wegner ◽  
Michael Jerosch-Herold ◽  
Christopher Hart ◽  
Eileen Pardun ◽  
Hans-Heiner Kramer ◽  
...  
Keyword(s):  
Blood Flow ◽  
Myocardial Blood Flow ◽  
Hypoplastic Left Heart Syndrome ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Left Heart Syndrome
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