Bidirectional coronary venous return in the partial unroofed coronary sinus syndrome complicated by coronary sinus orifice atresia

2020 ◽  
Vol 30 (4) ◽  
pp. 582-584 ◽  
Author(s):  
Dai Asada ◽  
Hisato Ito

AbstractUnroofed coronary sinus syndrome complicated by coronary sinus orifice atresia is a rare congenital anomaly. There are two alternate exits for coronary venous return: unroofed coronary sinus and persistent left superior caval vein. The coronary venous direction could be bidirectional depending on the pressure balance between the left atrium and the systemic vein. This anomaly has the risk of heart failure, paradoxical embolism, and cyanosis.

1998 ◽  
Vol 8 (2) ◽  
pp. 253-255 ◽  
Author(s):  
Jacques A.M. van Son ◽  
Thomas Walther ◽  
Friedrich W. Mohr

AbstractIn a young infant with divided left atrium, unroofed coronary sinus syndrome, and persistent left superior caval vein, the pulmonary venous blood was successfully routed, after atrial septectomy, to the mitral valve by constructing a baffle using the partially detached diaphragm which had initially separated the pulmonary venous and vestibular components of the left atrium. The baffle was augmented with a patch of untreated autologous pericardium.


1998 ◽  
Vol 6 (1) ◽  
pp. 52-53
Author(s):  
Jacques AM van Son ◽  
Jörg Hambsch ◽  
Friedrich W Mohr

A technique for conversion of an intra-atrial baffle repair to an extracardiac repair is described for complex unroofed coronary sinus syndrome (including a complete atrioventricular septal defect) with connection of the left superior caval vein to the roof of the left-sided atrium. The left superior caval vein was divided distally and anastomosed to the right superior caval vein in an end-to-side fashion. In addition, the baffle in the left-sided atrium connecting the pulmonary veins with the left atrioventricular valve orifice was removed and the atria were septated. This extracardiac repair technique avoids the various disadvantages of the intra-atrial baffle technique such as creation of a small left atrium with low compliance.


2016 ◽  
Vol 27 (5) ◽  
pp. 846-850
Author(s):  
Jelena Saundankar ◽  
Andrew B. Ho ◽  
Anthony P. Salmon ◽  
Robert H. Anderson ◽  
Alan G. Magee

AbstractAimsThe pathophysiological entity of a persisting left-sided superior caval vein draining into the roof of the left atrium represents an extreme form of coronary sinus de-roofing. This is an uncommon, but well-documented condition associated with systemic desaturation due to a right-to-left shunt. Depending on the size of the coronary ostium, the defect may also present with right-sided volume loading. We describe two patients, both of whom presented with desaturation, and highlight the important anatomical features underscoring management.Methods and ResultsBoth patients were managed interventionally with previous assessment of the size of the coronary sinus ostium through cross-sectional imaging. This revealed a restrictive interatrial communication at the right atrial mouth of the coronary sinus in both patients, which permitted an interventional approach, as the residual left-to-right shunt subsequent to closure of the aberrant vessel would be negligible. At intervention, test occlusion of the left superior caval vein allowed assessment of decompressing vessels before successful occlusion using an Amplatzer Vascular Plug.ConclusionsPersistence of a left superior caval vein draining to the left atrium may be associated with an interatrial communication at the mouth of the unroofed coronary sinus. The ostium of the de-roofed coronary sinus can be atretic, restrictive, normally sized, or enlarged. Careful assessment of the size of this defect is required before treatment. In view of its importance, which has received little attention in the literature to date, we suggest an additional consideration to the classification of unroofed coronary sinus.


Author(s):  
Eliza Cinteza ◽  
Mihaela Balgradean ◽  
Luca Giugno ◽  
Alessandro Giamberti ◽  
Cristina Filip ◽  
...  

2015 ◽  
Vol 178 ◽  
pp. 178-180
Author(s):  
Alfredo Di Pino ◽  
Elio Caruso ◽  
Placido Gitto ◽  
Luca Costanzo ◽  
Salvatore Patanè ◽  
...  

2000 ◽  
Vol 10 (4) ◽  
pp. 416-418 ◽  
Author(s):  
Hideki Uemura ◽  
Toshikatsu Yagihara ◽  
Osamu Monta

AbstractWe found right-to-left shunts through the cardiac veins postoperatively in 2 patients who had undergone the Fontan procedure. In one of the patients, channels were present through the cardiac veins independent of the coronary sinus. In the other patient, an atretic orifice for the coronary sinus, coupled with a persistent left-sided superior caval vein, complicated the postoperative course.


2003 ◽  
Vol 76 (2) ◽  
pp. 619-621 ◽  
Author(s):  
Federico Brunelli ◽  
Andrea Amaducci ◽  
Zen Mhagna ◽  
Giovanni Troise ◽  
Eugenio Quaini

2019 ◽  
Vol 29 (7) ◽  
pp. 996-998
Author(s):  
Omar Abu-Anza ◽  
Ravi Ashwath

AbstractBiatrial drainage of the right superior caval vein is an extremely rare cardiac anomaly that generally presents in childhood. We present a case of anomalous connection of the right superior caval vein with superior sinus venosus atrial septal defect and partial anomalous pulmonary venous return in a 5-month-old male presenting with unexplained cyanosis and hypoxia.


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