Extracardiac Repair of Complex Unroofed Coronary Sinus

1998 ◽  
Vol 6 (1) ◽  
pp. 52-53
Author(s):  
Jacques AM van Son ◽  
Jörg Hambsch ◽  
Friedrich W Mohr
Keyword(s):  
Coronary Sinus ◽  
Septal Defect ◽  
Pulmonary Veins ◽  
Atrioventricular Septal Defect ◽  
Caval Vein ◽  
Unroofed Coronary Sinus ◽  
Superior Caval Vein ◽  
The Right ◽  
Unroofed Coronary Sinus Syndrome ◽  
Complete Atrioventricular

A technique for conversion of an intra-atrial baffle repair to an extracardiac repair is described for complex unroofed coronary sinus syndrome (including a complete atrioventricular septal defect) with connection of the left superior caval vein to the roof of the left-sided atrium. The left superior caval vein was divided distally and anastomosed to the right superior caval vein in an end-to-side fashion. In addition, the baffle in the left-sided atrium connecting the pulmonary veins with the left atrioventricular valve orifice was removed and the atria were septated. This extracardiac repair technique avoids the various disadvantages of the intra-atrial baffle technique such as creation of a small left atrium with low compliance.

Left-sided hepatic vein connected to the coronary sinus

1996 ◽  
Vol 6 (2) ◽  
pp. 190-192 ◽  
Author(s):  
László Király ◽  
John E. Deanfield ◽  
Marc R. de Leval
Keyword(s):  
Hepatic Vein ◽  
Coronary Sinus ◽  
Left Atrial ◽  
Septal Defect ◽  
Atrioventricular Septal Defect ◽  
Rare Entity ◽  
Biventricular Repair ◽  
Caval Vein ◽  
Inferior Caval Vein ◽  
Complete Atrioventricular

AbstractA left-sided hepatic vein connected to the coronary sinus is reported in a case of a 22-month-old boy with isomerism of the left atrial appendages, complete atrioventricular septal defect and azygous continuation of the inferior caval vein. The diagnosis of the anomalous hepatic vein was made intraoperatively and successful biventricular repair has been accomplished. To the best of our knowledge, this is the first communication on this peculiar entity diagnosed during life, notwithstanding Nabarro's description of a similar autopsy finding in 1903. Aspects of the development of this rare entity are discussed.

Bidirectional coronary venous return in the partial unroofed coronary sinus syndrome complicated by coronary sinus orifice atresia

2020 ◽  
Vol 30 (4) ◽  
pp. 582-584 ◽  
Author(s):  
Dai Asada ◽  
Hisato Ito
Keyword(s):  
Coronary Sinus ◽  
Venous Return ◽  
Paradoxical Embolism ◽  
Pressure Balance ◽  
Caval Vein ◽  
Unroofed Coronary Sinus ◽  
Superior Caval Vein ◽  
Systemic Vein ◽  
Coronary Sinus Orifice Atresia ◽  
Unroofed Coronary Sinus Syndrome

AbstractUnroofed coronary sinus syndrome complicated by coronary sinus orifice atresia is a rare congenital anomaly. There are two alternate exits for coronary venous return: unroofed coronary sinus and persistent left superior caval vein. The coronary venous direction could be bidirectional depending on the pressure balance between the left atrium and the systemic vein. This anomaly has the risk of heart failure, paradoxical embolism, and cyanosis.

Anatomical considerations for the management of a left-sided superior caval vein draining to the roof of the left atrium

2016 ◽  
Vol 27 (5) ◽  
pp. 846-850
Author(s):  
Jelena Saundankar ◽  
Andrew B. Ho ◽  
Anthony P. Salmon ◽  
Robert H. Anderson ◽  
Alan G. Magee
Keyword(s):  
Left Atrium ◽  
Coronary Sinus ◽  
Right Atrial ◽  
Caval Vein ◽  
Cross Sectional ◽  
Interatrial Communication ◽  
Unroofed Coronary Sinus ◽  
Superior Caval Vein ◽  
Coronary Sinus Ostium ◽  
The Right

AbstractAimsThe pathophysiological entity of a persisting left-sided superior caval vein draining into the roof of the left atrium represents an extreme form of coronary sinus de-roofing. This is an uncommon, but well-documented condition associated with systemic desaturation due to a right-to-left shunt. Depending on the size of the coronary ostium, the defect may also present with right-sided volume loading. We describe two patients, both of whom presented with desaturation, and highlight the important anatomical features underscoring management.Methods and ResultsBoth patients were managed interventionally with previous assessment of the size of the coronary sinus ostium through cross-sectional imaging. This revealed a restrictive interatrial communication at the right atrial mouth of the coronary sinus in both patients, which permitted an interventional approach, as the residual left-to-right shunt subsequent to closure of the aberrant vessel would be negligible. At intervention, test occlusion of the left superior caval vein allowed assessment of decompressing vessels before successful occlusion using an Amplatzer Vascular Plug.ConclusionsPersistence of a left superior caval vein draining to the left atrium may be associated with an interatrial communication at the mouth of the unroofed coronary sinus. The ostium of the de-roofed coronary sinus can be atretic, restrictive, normally sized, or enlarged. Careful assessment of the size of this defect is required before treatment. In view of its importance, which has received little attention in the literature to date, we suggest an additional consideration to the classification of unroofed coronary sinus.

Repair of divided left atrium associated with unroofed coronary sinus

1998 ◽  
Vol 8 (2) ◽  
pp. 253-255 ◽  
Author(s):  
Jacques A.M. van Son ◽  
Thomas Walther ◽  
Friedrich W. Mohr
Keyword(s):  
Mitral Valve ◽  
Left Atrium ◽  
Coronary Sinus ◽  
Venous Blood ◽  
Young Infant ◽  
Caval Vein ◽  
Unroofed Coronary Sinus ◽  
Autologous Pericardium ◽  
Superior Caval Vein ◽  
Unroofed Coronary Sinus Syndrome

AbstractIn a young infant with divided left atrium, unroofed coronary sinus syndrome, and persistent left superior caval vein, the pulmonary venous blood was successfully routed, after atrial septectomy, to the mitral valve by constructing a baffle using the partially detached diaphragm which had initially separated the pulmonary venous and vestibular components of the left atrium. The baffle was augmented with a patch of untreated autologous pericardium.

Anatomical Repair of an Unusual Combination of Tetralogy of Fallot and Atrioventricular Septal Defect With Unroofed Coronary Sinus

2015 ◽  
Vol 30 (11) ◽  
pp. 849-852
Author(s):  
Sachin Talwar ◽  
Rakesh Kumar ◽  
Amolkumar Bhoje ◽  
Shiv Kumar Choudhary ◽  
Balram Airan
Keyword(s):  
Tetralogy Of Fallot ◽  
Coronary Sinus ◽  
Septal Defect ◽  
Atrioventricular Septal Defect ◽  
Unroofed Coronary Sinus ◽  
Unusual Combination

Clarifying the anatomy of the superior sinus venosus defect

Heart ◽  
2021 ◽  
pp. heartjnl-2021-319334
Author(s):  
Jay Relan ◽  
Saurabh Kumar Gupta ◽  
Rengarajan Rajagopal ◽  
Sivasubramanian Ramakrishnan ◽  
Gurpreet Singh Gulati ◽  
...  
Keyword(s):  
Left Atrium ◽  
Pulmonary Vein ◽  
Pulmonary Veins ◽  
Interatrial Septum ◽  
Sinus Venosus ◽  
Caval Vein ◽  
Therapeutic Implications ◽  
Superior Caval Vein ◽  
Inferior Pulmonary Vein ◽  
The Right

ObjectivesWe sought to clarify the variations in the anatomy of the superior cavoatrial junction and anomalously connected pulmonary veins in patients with superior sinus venosus defects using computed tomographic (CT) angiography.MethodsCT angiograms of 96 consecutive patients known to have superior sinus venosus defects were analysed.ResultsThe median age of the patients was 34.5 years. In seven (7%) patients, the defect showed significant caudal extension, having a supero-inferior dimension greater than 25 mm. All patients had anomalous connection of the right superior pulmonary vein. The right middle and right inferior pulmonary vein were also connected anomalously in 88 (92%) and 17 (18%) patients, respectively. Anomalous connection of the right inferior pulmonary vein was more common in those with significant caudal extension of the defect (57% vs 15%, p=0.005). Among anomalously connected pulmonary veins, the right superior, middle, and inferior pulmonary veins were committed to the left atrium in 6, 17, and 11 patients, respectively. The superior caval vein over-rode the interatrial septum in 67 (70%) patients, with greater than 50% over-ride in 3 patients.ConclusionAnomalous connection of the right-sided pulmonary veins is universal, but is not limited to the right upper lobe. Not all individuals have over-riding of superior caval vein. In a minority of patients, the defect has significant caudal extension, and anomalously connected pulmonary veins are committed to the left atrium. These findings have significant clinical and therapeutic implications.

Diffuse varices of the right pulmonary veins

2003 ◽  
Vol 13 (3) ◽  
pp. 312-313 ◽  
Author(s):  
Milan Djukic ◽  
Claudius Rotzsch ◽  
Ingo Dähnert
Keyword(s):  
Septal Defect ◽  
Pulmonary Veins ◽  
Atrioventricular Septal Defect ◽  
Arterial Duct ◽  
The Right

We describe a patient with diffuse varices of the right pulmonary veins in association with patency of the arterial duct and an atrioventricular septal defect with separate right and left atrioventricular valvar orifices.

Double outlet right atrium and complete atrioventricular septal defect with abnormal findings of the biopsied lung

1994 ◽  
Vol 4 (4) ◽  
pp. 402-404 ◽  
Author(s):  
Kiyoshi Suzuki ◽  
Toshio Kikuchi ◽  
Shigekazu Mimori
Keyword(s):  
Septal Defect ◽  
Pulmonary Veins ◽  
Pulmonary Arteries ◽  
Atrioventricular Septal Defect ◽  
Pulmonary Trunk ◽  
Atrial Septum ◽  
Corrective Surgery ◽  
Rare Type ◽  
Medial Hypertrophy ◽  
Complete Atrioventricular

SummaryWe describe a rare type of atrioventricular septal defect with common atrioventricular orifice and malaligned atrial septum, the latter feature resulting in severe obstruction of the left atrial egress. Excision of the atrial septum and banding of the pulmonary trunk was performed at the age of thirteen months. Lung biopsy demonstrated marked medial hypertrophy with severe intimal fibrosis in the small pulmonary arteries and mild thickening of the pulmonary veins, considered contraindications for corrective surgery.

Partially Anomalous Pulmonary Venous Connection to Solitary and Persistent Left Superior Caval Vein in Usual Visceroatrial Arrangement

2017 ◽  
Vol 11 (4) ◽  
pp. NP88-NP90
Author(s):  
Anoop Ayyappan ◽  
Arun Gopalakrishnan ◽  
Kapilamoorthy Tirur Raman
Keyword(s):  
Pulmonary Veins ◽  
Caval Vein ◽  
Superior Caval Vein ◽  
The Right ◽  
Anomalous Pulmonary Venous Connection

Although the occurrence of bilateral superior caval veins (SCVs) is not unusual, persistence of the left SCV with atretic right SCV is extremely uncommon in the setting of normal visceroatrial arrangement. We report such a case that was also associated with anomalous pulmonary venous connection of the right pulmonary veins to the solitary left SCV.

Biatrial drainage of right superior caval vein with preferential streaming into the left atrium

2019 ◽  
Vol 29 (7) ◽  
pp. 996-998
Author(s):  
Omar Abu-Anza ◽  
Ravi Ashwath
Keyword(s):  
Atrial Septal Defect ◽  
Left Atrium ◽  
Septal Defect ◽  
Venous Return ◽  
Sinus Venosus ◽  
Cardiac Anomaly ◽  
Caval Vein ◽  
Superior Caval Vein ◽  
Anomalous Pulmonary Venous Return ◽  
The Right

AbstractBiatrial drainage of the right superior caval vein is an extremely rare cardiac anomaly that generally presents in childhood. We present a case of anomalous connection of the right superior caval vein with superior sinus venosus atrial septal defect and partial anomalous pulmonary venous return in a 5-month-old male presenting with unexplained cyanosis and hypoxia.

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