Specific Delay in the Degradation of Mitochondrial ATP Synthase Subunit c in Late Infantile Neuronal Ceroid Lipofuscinosis Is Derived from Cellular Proteolytic Dysfunction Rather than Structural Alteration of Subunit c

2002 ◽  
Vol 67 (4) ◽  
pp. 1677-1687 ◽  
Author(s):  
Junji Ezaki ◽  
Leonhard S. Wolfe ◽  
Eiki Kominami
Keyword(s):  
Atp Synthase ◽  
Neuronal Ceroid Lipofuscinosis ◽  
Structural Alteration ◽  
Subunit C ◽  
Infantile Neuronal Ceroid Lipofuscinosis ◽  
Ceroid Lipofuscinosis ◽  
Mitochondrial Atp Synthase

Accumulation of mitochondrial ATP synthase subunit c in muscle in a patient with neuronal ceroid lipofuscinosis (late infantile form)

1997 ◽  
Vol 93 (6) ◽  
pp. 628-632 ◽  
Author(s):  
F. Umehara ◽  
Itsuro Higuchi ◽  
Kenji Tanaka ◽  
Takahito Niiyama ◽  
Junji Ezaki ◽  
...  
Keyword(s):  
Atp Synthase ◽  
Neuronal Ceroid Lipofuscinosis ◽  
Infantile Form ◽  
Subunit C ◽  
Ceroid Lipofuscinosis ◽  
Mitochondrial Atp Synthase

scholarly journals Lysine methylation of mitochondrial ATP synthase subunit c stored in tissues of dogs with hereditary ceroid lipofuscinosis

1994 ◽  
Vol 269 (13) ◽  
pp. 9906-9911
Author(s):  
M.L. Katz ◽  
J.S. Christianson ◽  
N.E. Norbury ◽  
C.L. Gao ◽  
A.N. Siakotos ◽  
...  
Keyword(s):  
Atp Synthase ◽  
Lysine Methylation ◽  
Subunit C ◽  
Ceroid Lipofuscinosis ◽  
Mitochondrial Atp Synthase
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