Rapid response of IgA pemphigus of subcorneal pustular dermatosis type to treatment with isotretinoin

2000 ◽  
Vol 43 (5) ◽  
pp. 923-926 ◽  
Author(s):  
Claus Gruss ◽  
Detlef Zillikens ◽  
Takashi Hashimoto ◽  
Masayuki Amagai ◽  
Maximilian Kroiss ◽  
...  
Keyword(s):  
Rapid Response ◽  
Iga Pemphigus ◽  
Subcorneal Pustular Dermatosis

Antidesmocollin 1 autoantibody negative subcorneal pustular dermatosis-type IgA pemphigus associated with multiple myeloma

2014 ◽  
Vol 172 (1) ◽  
pp. 296-298 ◽  
Author(s):  
A. España ◽  
A. Gimenez-Azcarate ◽  
N. Ishii ◽  
M.A. Idoate ◽  
C. Panizo ◽  
...  
Keyword(s):  
Multiple Myeloma ◽  
Iga Pemphigus ◽  
Subcorneal Pustular Dermatosis

scholarly journals IgA Pemphigus in a Child – a Case Report

2017 ◽  
Vol 9 (1) ◽  
pp. 14-21
Author(s):  
Branislav Lekić ◽  
Mirjana Gajić-Veljić ◽  
Svetlana Popadić ◽  
Miloš Nikolić
Keyword(s):  
Case Report ◽  
Complete Remission ◽  
Direct Immunofluorescence ◽  
Cell Surfaces ◽  
Bullous Disease ◽  
Autoimmune Bullous Disease ◽  
Iga Pemphigus ◽  
Subcorneal Pustular Dermatosis ◽  
Keratinocyte Cell ◽  
The Face

Abstract IgA pemphigus (IGAP) is a rare autoimmune bullous disease characterized by IgA deposits on keratinocyte cell surfaces. The IGAP is classified into: 1) subcorneal pustular dermatosis (SPD) type, and 2) intraepidermal neutrophilic (IEN) IgA dermatosis type. So far, only 9 children with IGAP have been described in the literature, of whom only 3 with SPD type. We report a 3-year-old boy with SPD type of IGAP. Clinically, he presented with pruritic vesicles, pustules and erosions on the face, trunk, groin area, and extremities. Histopathology showed subcorneal pustules containing a few acantholytic cells. Direct immunofluorescence (DIF) test of Tzanck smear showed intercellular IgA deposits on the surface of the groups of epidermal cells. Oral dapsone and prednisone induced remission after two weeks; the treatment was discontinued 11 months later, and complete remission was achieved during 19 months without any treatment. Direct immunofluorescence of Tzanck smear is a simple, sensitive, rapid and non-aggressive test, very suitable for the diagnosis of IGAP in children.

scholarly journals Human Desmocollin 1 (Dsc1) Is an Autoantigen for the Subcorneal Pustular Dermatosis Type of IgA Pemphigus

1997 ◽  
Vol 109 (2) ◽  
pp. 127-131 ◽  
Author(s):  
Takashi Hashimoto ◽  
Chie Kiyokawa ◽  
Osamu Mori ◽  
Minoru Miyasato ◽  
Martyn A.J. Chidgey ◽  
...  
Keyword(s):  
Iga Pemphigus ◽  
Subcorneal Pustular Dermatosis

Regression of subcorneal pustular dermatosis type of IgA pemphigus lesions with azithromycin

2005 ◽  
Vol 51 (2) ◽  
pp. E31-E34 ◽  
Author(s):  
I BLIZIOTIS ◽  
P RAFAILIDIS ◽  
P VERGIDIS ◽  
M FALAGAS
Keyword(s):  
Iga Pemphigus ◽  
Subcorneal Pustular Dermatosis

scholarly journals Revisiting the question of pemphigus classification

2021 ◽  
Vol 97 (2) ◽  
pp. 9-15
Author(s):  
Alexey V. Samtsov ◽  
Evgeny V. Sokolovskiy ◽  
Natalia P. Teplyuk ◽  
Irena E. Belousova ◽  
Muza M. Kokhan ◽  
...  
Keyword(s):  
Clinical Practice ◽  
Clinical Guidelines ◽  
Pemphigus Vulgaris ◽  
Neutrophilic Dermatosis ◽  
Pemphigus Foliaceus ◽  
Paraneoplastic Pemphigus ◽  
Iga Pemphigus ◽  
Subcorneal Pustular Dermatosis ◽  
Pemphigus Erythematosus

Analysis of various classifications of pemphigus shows that there are no fundamental differences between them. The main distinctions consist in use of diverse terms in naming of some forms of pemphigus and in inclusion or exclusion of certain subtypes from the classifications. Authors propose to use the following classification in the dermatological clinical practice, for educational and scientific purposes and for clinical guidelines: 1) pemphigus vulgaris (1.1. Pemphigu s vegetans); 2) pemphigus foliaceus (2.1. Pemphigus endemic (Fogo selvagem), 2.2. Pemphigus erythematosus (Senear Usher)); 3) herpetiform pemphigus; 4) paraneoplastic pemphigus; 5) IgA pemphigus (5.1. Subcorneal pustular dermatosis, 5.2. Intraepidermal neutrophilic dermatosis).

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