scholarly journals Making complex pathology simple: added value of 3D transthoracic echocardiography in an adult patient with congenitally corrected transposition of great arteries and severe tricuspid regurgitation

2018 ◽  
Vol 19 (11) ◽  
pp. 1311-1311
Author(s):  
Elena Surkova ◽  
Roxy Senior ◽  
Wei Li
Keyword(s):  
Adult Patient ◽  
Tricuspid Regurgitation ◽  
Transthoracic Echocardiography ◽  
Added Value ◽  
Transposition Of Great Arteries ◽  
Severe Tricuspid Regurgitation ◽  
3D Transthoracic Echocardiography ◽  
Congenitally Corrected Transposition ◽  
Corrected Transposition

Double switch operation in a young infant

2004 ◽  
Vol 14 (6) ◽  
pp. 661-663 ◽  
Author(s):  
Nobuyuki Ishibashi ◽  
Mitsuru Aoki ◽  
Tadashi Fujiwara
Keyword(s):  
Tricuspid Regurgitation ◽  
Septal Defect ◽  
Arterial Switch Operation ◽  
Young Infant ◽  
Severe Tricuspid Regurgitation ◽  
Young Infants ◽  
Switch Operation ◽  
Double Switch ◽  
Congenitally Corrected Transposition ◽  
Corrected Transposition

We performed a combined Senning and arterial switch operation on a 2-month-old patient with congenitally corrected transposition, Ebstein's malformation producing severe tricuspid regurgitation, ventricular septal defect, pulmonary hypertension, and congestive heart failure. The tricuspid regurgitation was improved. The double switch operation has the advantage of improving the function of the systemic atrioventricular valve, especially in newborns or young infants in whom the outcome of the valvar repair is poor.

scholarly journals Unguarded Tricuspid Orifice with Congenitally Corrected Transposition of the Great Arteries and Aortic Atresia- A Highly Unusual Case

2021 ◽  
pp. 67-72
Author(s):  
Carolin Puegge ◽  
Isabell Altmann ◽  
Michael Weidenbach
Keyword(s):  
Right Ventricular ◽  
Tricuspid Regurgitation ◽  
Unusual Case ◽  
Pulmonary Atresia ◽  
Right Heart Failure ◽  
Right Heart ◽  
Severe Tricuspid Regurgitation ◽  
Aortic Atresia ◽  
Congenitally Corrected Transposition ◽  
Corrected Transposition

Unguarded tricuspid orifice is a very rare anomaly. It is characterised by the absence of one or more of the tricuspid valve leaflets resulting in severe tricuspid regurgitation and right heart failure. It is rarely an isolated anomaly but more often associated with pulmonary atresia and intact ventricular septum. When the ventricles are inverted however, the result of outflow tract obliteration is not pulmonary atresia, but aortic atresia. This anomaly has been described in the literature in only 2 cases so far. We present a case of a neonate with unguarded tricuspid orifice with absence of all tricuspid leaflets, congenitally corrected transposition of the great arteries and aortic atresia. The severe tricuspid regurgitation and right ventricular enlargement would have required a Norwood-like procedure combined with a right ventricular plication. Due to the complexity of this lesion no surgical therapy was attempted in consent with the parents.

Serial changes of tricuspid regurgitation after anatomic repair for congenitally corrected transposition

2020 ◽  
Vol 58 (1) ◽  
pp. 163-170 ◽  
Author(s):  
Tsubasa Furuya ◽  
Takaya Hoashi ◽  
Masatoshi Shimada ◽  
Kenta Imai ◽  
Motoki Komori ◽  
...  
Keyword(s):  
Tricuspid Regurgitation ◽  
Pacemaker Implantation ◽  
Hospital Death ◽  
Transposition Of Great Arteries ◽  
Anatomic Repair ◽  
Atrial Switch ◽  
The Mean ◽  
Congenitally Corrected Transposition ◽  
Corrected Transposition

Abstract OBJECTIVES The aim of this study was to reveal the serial changes in tricuspid regurgitation (TR) after anatomic repair for congenitally corrected transposition of great arteries. METHODS Between 1995 and 2018, 48 patients underwent anatomic repair (atrial/arterial switch in 14 patients, atrial switch and Rastelli in 34 patients). The mean age and weight of the patients during anatomic repair was 33 (interquartile range 21.8–62.1) months and 12 (10.3–16.3) kg. The preoperative TR was less than mild in 15 patients (31.3%), mild-to-moderate in 29 patients (60.4%) and more-than-moderate in 4 patients (8.3%). Ebsteinoid dysplasia of the tricuspid valve (TV) was observed in 7 patients (14.6%). During the study period, no patient underwent TV surgery or bidirectional Glenn anastomosis at the time of anatomic repair. RESULTS There was 1 in-hospital death and 1 late death. The follow-up was completed by other surviving patients, with a median follow-up period of 12.1 years (5.9–18.1). The overall survival, reoperation-free survival and freedom from permanent pacemaker implantation rate at 15 years were 94.3%, 74.3% and 81.5%, respectively. The mean TR grade was 2.0 (1.0–2.6) preoperatively, 2.0 (1.0–2.0) at 1 year, 2.0 (2.0–2.0) at 5 years and 2.0 (2.0–2.0) at 10 years after anatomic repair. A Cox proportional hazards model showed that association of Ebsteinoid dysplasia of the TV, type of anatomic repair and previous pulmonary artery banding did not affect freedom from death or the more-than-moderate TR rate. There were 2 patients who underwent TV surgery after the anatomic repair for severe TR; TV repair was successfully done for 1 patient, the other required semi-closure of TV and one and one-half ventricle conversion. CONCLUSIONS TR remained subclinical or improved in the majority of patients after anatomic repair without TV repair. However, there were a few patients whose TR progressed to severe or massive, then required TV surgery after anatomic repair. Although exposure was difficult, TR was sometimes repairable following atrial switch, otherwise, one and one-half ventricle repair conversion would be the choice of treatment.

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