scholarly journals Autologous intramuscular transplantation of engineered satellite cells induces exosome-mediated systemic expression of Fukutin-related protein and rescues disease phenotype in a murine model of limb-girdle muscular dystrophy type 2I

2017 ◽  
Vol 26 (19) ◽  
pp. 3682-3698 ◽  
Author(s):  
Paola Frattini ◽  
Chiara Villa ◽  
Francesca De Santis ◽  
Mirella Meregalli ◽  
Marzia Belicchi ◽  
...  
Keyword(s):  
Muscular Dystrophy ◽  
Satellite Cells ◽  
Murine Model ◽  
Limb Girdle Muscular Dystrophy ◽  
Disease Phenotype ◽  
Related Protein

scholarly journals Age-Dependent Effect of Myostatin Blockade on Disease Severity in a Murine Model of Limb-Girdle Muscular Dystrophy

2006 ◽  
Vol 168 (6) ◽  
pp. 1975-1985 ◽  
Author(s):  
Stephanie A. Parsons ◽  
Douglas P. Millay ◽  
Michelle A. Sargent ◽  
Elizabeth M. McNally ◽  
Jeffery D. Molkentin
Keyword(s):  
Muscular Dystrophy ◽  
Disease Severity ◽  
Murine Model ◽  
Limb Girdle Muscular Dystrophy ◽  
Dependent Effect ◽  
Age Dependent

scholarly journals Restriction of Calpain3 Expression to the Skeletal Muscle Prevents Cardiac Toxicity and Corrects Pathology in a Murine Model of Limb-Girdle Muscular Dystrophy

Circulation ◽  
2013 ◽  
Vol 128 (10) ◽  
pp. 1094-1104 ◽  
Author(s):  
Carinne Roudaut ◽  
Florence Le Roy ◽  
Laurence Suel ◽  
Jérôme Poupiot ◽  
Karine Charton ◽  
...  
Keyword(s):  
Skeletal Muscle ◽  
Muscular Dystrophy ◽  
Murine Model ◽  
Cardiac Toxicity ◽  
Limb Girdle Muscular Dystrophy

Limb girdle muscular dystrophy type 2I, fukutin-related protein deficiency

2013 ◽  
pp. 122-124
Author(s):  
John H. J. Wokke ◽  
Pieter A. van Doorn ◽  
Jessica E. Hoogendijk ◽  
Marianne de Visser
Keyword(s):  
Muscular Dystrophy ◽  
Protein Deficiency ◽  
Limb Girdle Muscular Dystrophy ◽  
Related Protein

Diagnostic clues and manifesting carriers in fukutin-related protein (FKRP) limb-girdle muscular dystrophy

2015 ◽  
Vol 348 (1-2) ◽  
pp. 266-268 ◽  
Author(s):  
Lucia V. Schottlaender ◽  
Axel Petzold ◽  
Nicholas Wood ◽  
Henry Houlden
Keyword(s):  
Muscular Dystrophy ◽  
Limb Girdle Muscular Dystrophy ◽  
Related Protein

Myostatin blockade improves function but not histopathology in a murine model of limb-girdle muscular dystrophy 2C

2008 ◽  
Vol 37 (3) ◽  
pp. 308-316 ◽  
Author(s):  
Sasha Bogdanovich ◽  
Elizabeth M. McNally ◽  
Tejvir S. Khurana
Keyword(s):  
Muscular Dystrophy ◽  
Murine Model ◽  
Limb Girdle Muscular Dystrophy
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