Congenital coronary artery anomalies

Author(s):  
Cristina Basso ◽  
Carla Frescura ◽  
Stefania Rizzo ◽  
Gaetano Thiene

Despite the low prevalence in the general population, congenital coronary artery anomalies (CAAs) are well recognized as a major cause of sudden cardiac death (SCD). Not all CAAs have the same prognostic impact and each of them should be discussed individually. Apart from anomalous origin of a coronary artery (CA) from the pulmonary artery, the anomalous origin from the wrong aortic sinus, either the left main CA from the right sinus or the right CA from the left sinus, are traditionally considered as the highest risk of SCD. CAAs with an inter-arterial course carry the highest risk of ischaemia, particularly during exercise. Several pathophysiological mechanisms have been postulated, including compression of the anomalous CA between the aorta and the pulmonary artery, the acute angle take-off, the proximal intra-mural aortic course, and a superimposed CA spasm. The diagnostic work-up, including ischaemia provocation test imaging tools, and current management strategies, from sport restriction to surgical intervention, are discussed.

2018 ◽  
Vol 12 (2) ◽  
pp. 98-101
Author(s):  
Kajal Kumar Karmoker ◽  
Khandaker Aisha Siddika ◽  
Arif Hossain ◽  
Mohammad Adib Al Javed ◽  
Bijoy Datta

Congenital coronary artery anomalies are rare heart defect that has been associated with myocardial ischemia and sudden death. Only 1-2% of population having variation in the origin, course or distribution of the epicardial coronary arteries. Anomalous origin of coronary arteries may be present as isolated defect or as a part of complex congenital heart disease. The clinical presentation, diagnostic work up, prognosis and treatment of these anomalies are highly variable. Most of the patients are asymptomatic but manifestation of these patients are chest pain, dyspnoea, palpitation, dizziness, ventricular fibrillation, syncope and sudden death. It is the second most common cause of sudden death in young athletes. Selective coronary angiography is the gold standard for identification of such type of anomaly. Patients of anomalous origin of coronary artery from the opposite sinus may require medical treatment, coronary angioplasty with stenting or surgical repair.University Heart Journal Vol. 12, No. 2, July 2016; 98-101


Medicina ◽  
2013 ◽  
Vol 49 (10) ◽  
pp. 72
Author(s):  
Domas Golubickas ◽  
Justina Motiejūnaitė ◽  
Antanas Jankauskas ◽  
Rimvydas Šlapikas ◽  
Algidas Basevičius

The incidence of congenital coronary artery anomalies is estimated to range between 1% and 2% in the general population. The separate types of coronary artery anomalies are even rarer – the left main coronary artery arising from the right coronary sinus and passing between the thoracic aorta and the pulmonary artery is one of them. In this case, the segment of the artery that courses between the aorta and the pulmonary artery is prone to compression, especially during heavy exercise. Outcomes may be fatal due to myocardial hypoperfusion, which is associated with sudden cardiac death especially among children, young adults, and athletes. Nowadays, innate coronary artery anomalies may be incidentally diagnosed in older age using new investigation methods such as computed tomography angiography.


2020 ◽  
Vol 11 (4) ◽  
pp. 501-503
Author(s):  
Roman Sekelyk ◽  
Dmytro Kozhokar ◽  
Andrii Kurkevych ◽  
Oleksandra Motrechko ◽  
Illya Yemets

We present a patient with the extremely rare coexistence of two distinct coronary artery malformations: anomalous aortic origin of the right coronary artery from the left aortic sinus with intramural course and anomalous origin of the circumflex coronary artery from the right pulmonary artery. Surgical reimplantation of the anomalous left circumflex coronary artery to the aorta and unroofing of the intramural portion of the anomalous right coronary artery were performed.


2019 ◽  
Vol 10 (4) ◽  
pp. 508-512
Author(s):  
Vishal Agrawal ◽  
Nikunj Vaidhya ◽  
Mrinal Patel ◽  
Amit Mishra ◽  
Dinesh Patel

Anomalous origin of the left coronary artery (LCA) from the right pulmonary artery (ALCARPA) is an extremely rare subset of an already rare entity, anomalous origin of the LCA from the pulmonary artery. Whenever it is diagnosed preoperatively, one should be extremely vigilant about the potential intramural course of the descending part of the LCA in the aorta. Preoperative imaging frequently fails to delineate this intramural course. We report our experience with one such case where we had accidentally injured the LCA during dissection from the right pulmonary artery. Although it was successfully managed, it reinforces our aforementioned point concerning the importance of vigilance in seeking to identify intramurality as a component of this anomaly of coronary artery origin.


2019 ◽  
Vol 29 (1) ◽  
pp. 157-158
Author(s):  
Akira Furutachi ◽  
Kojiro Furukawa ◽  
Aiko Komatsu ◽  
Eijiro Nogami

Abstract Anomalous origin of the right coronary artery (RCA) from the pulmonary artery is a very rare congenital heart disease, and several reports have described long-term events after surgery. We report the case of a 46-year-old woman who underwent reimplantation of the RCA for anomalous origin of the right coronary artery from the pulmonary artery 16 years ago. An RCA aneurysm gradually developed and dilated over time, and we resected the aneurysm and also grafted the right gastroepiploic artery graft to the distal RCA. Careful long-term follow-up is required to avoid overlooking such a rare but life-threatening complication after surgical repair of anomalous origin of the right coronary artery from the pulmonary artery.


Author(s):  
Xhevdet Krasniqi ◽  
Hajdin Çitaku

Coronary arteries supply the heart muscle with blood maintaining myocardial hemostasis and function. Coronary artery anomalies may persist after birth affecting cardiovascular system through haemodynamic impairment caused from shunting, ischaemia, especially in young children or adolescents and young adults. In patients undergoing coronary angiography the incidence of anomalous origination of the left coronary artery from right sinus is 0.15% and the right coronary artery from the left sinus is 0.92%. A recent classification of the coronary anomalies is based on anatomical considerations, recognizing three categories: anomalies of the origin and course, anomalies of the intrinsic coronary artery anatomy, and anomalies of the termination. In the setting of anomalous coronary artery from the opposite sinus, the proximal anomalous CA may run anterior to the pulmonary trunk (prepulmonic), posterior to the aorta (retroaortic), septal (subpulmonic), or between the pulmonary artery and the aorta itself (interarterial). Among them, only those with an interarterial aorta-pulmonary course are regarded as hidden conditions at risk of ischaemia and even sudden death. We presented two cases with anomalous origin of coronary arteries from opposite sinus, and two other cases with anomalous origin of left circumflex artery. The atherosclerotic coronary artery disease leads to the need of coronarography which can find out the presence of coronary artery anomalies. Anomalous origin of coronary artery that is present with atherosclerotic changes continues to exist as a challenge during treatment in interventional cardiology.


2020 ◽  
Vol 30 (10) ◽  
pp. 1510-1511
Author(s):  
Rachel Rosenthal ◽  
Hannah Obasi ◽  
Daniel D. Im

AbstractMyocarditis and coronary artery anomalies are both potentially life-threatening aetiologies of cardiac chest pain in children. We present a case of a young man presenting with non-exertional chest pain and subsequently found to have an anomalous origin of the right coronary artery from the left coronary sinus with an interarterial course in addition to a diagnosis of myocarditis. The patient subsequently was able to undergo surgical correction of his anomalous coronary to mitigate the risk of sudden cardiac death.


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