scholarly journals Severe and persistent facial nerve stimulation after cochlear implantation in a patient with cochlear–facial dehiscence: a case report

2021 ◽  
Vol 49 (11) ◽  
pp. 030006052110578
Author(s):  
Jingyuan Chen ◽  
Biao Chen ◽  
Lifang Zhang ◽  
Yongxin Li

Generally, cochlear implants (CIs) are effective in helping patients improve their hearing performance; however, some patients have poor hearing performance owing to facial nerve stimulation (FNS), which is often associated with cochlear anomalies. We report a case with a normal cochlea and severe and persistent FNS owing to cochlear–facial dehiscence (CFD) that affected the CI outcomes. Preoperatively, a careful review of the computed tomography images before CI surgery is necessary not only for patients with otosclerosis and inner ear malformations but also for patients with normal cochlear structures because facial nerve anomalies could be present.

1991 ◽  
Vol 104 (6) ◽  
pp. 826-830 ◽  
Author(s):  
John K. Niparko ◽  
Dana L. Oviatt ◽  
Newton J. Coker ◽  
Lois Sutton ◽  
Susan B. Waltzman ◽  
...  

2005 ◽  
Vol 115 (6) ◽  
pp. 977-982 ◽  
Author(s):  
Jennifer L. Smullen ◽  
Marek Polak ◽  
Annelle V. Hodges ◽  
Stacy B. Payne ◽  
Fred F. Telischi ◽  
...  

1997 ◽  
Vol 90 (2) ◽  
pp. 147-150
Author(s):  
Harukazu HIRAUMI ◽  
Haruo Takahashi ◽  
Yasushi NAITO ◽  
Makoto MIURA

2015 ◽  
Vol 2015 ◽  
pp. 1-19 ◽  
Author(s):  
Micol Busi ◽  
Monica Rosignoli ◽  
Alessandro Castiglione ◽  
Federica Minazzi ◽  
Patrizia Trevisi ◽  
...  

Background. Specific clinical conditions could compromise cochlear implantation outcomes and drastically reduce the chance of an acceptable development of perceptual and linguistic capabilities. These conditions should certainly include the presence of inner ear malformations or brain abnormalities. The aims of this work were to study the diagnostic value of high resolution computed tomography (HRCT) and magnetic resonance imaging (MRI) in children with sensorineural hearing loss who were candidates for cochlear implants and to analyse the anatomic abnormalities of the ear and brain in patients who underwent cochlear implantation. We also analysed the effects of ear malformations and brain anomalies on the CI outcomes, speculating on their potential role in the management of language developmental disorders.Methods. The present study is a retrospective observational review of cochlear implant outcomes among hearing-impaired children who presented ear and/or brain anomalies at neuroimaging investigations with MRI and HRCT. Furthermore, genetic results from molecular genetic investigations (GJB2/GJB6and, additionally, in selected cases,SLC26A4or mitochondrial-DNA mutations) on this study group were herein described. Longitudinal and cross-sectional analysis was conducted using statistical tests.Results. Between January 1, 1996 and April 1, 2012, at the ENT-Audiology Department of the University Hospital of Ferrara, 620 cochlear implantations were performed. There were 426 implanted children at the time of the present study (who were <18 years). Among these, 143 patients (64 females and 79 males) presented ear and/or brain anomalies/lesions/malformations at neuroimaging investigations with MRI and HRCT. The age of the main study group (143 implanted children) ranged from 9 months and 16 years (average = 4.4; median = 3.0).Conclusions. Good outcomes with cochlear implants are possible in patients who present with inner ear or brain abnormalities, even if central nervous system anomalies represent a negative prognostic factor that is made worse by the concomitant presence of cochlear malformations. Common cavity and stenosis of the internal auditory canal (less than 2 mm) are negative prognostic factors even if brain lesions are absent.


2018 ◽  
Vol 19 (4) ◽  
pp. 193-197 ◽  
Author(s):  
Joana Sanches Pires ◽  
Ana Sofia Melo ◽  
Ricardo Caiado ◽  
Jorge Humberto Martins ◽  
João Elói Moura ◽  
...  

ORL ◽  
2021 ◽  
pp. 1-7
Author(s):  
Dejun Zhang ◽  
Yongyi Yuan ◽  
Yu Su ◽  
Guojian Wang ◽  
Chang Guo ◽  
...  

Cochlear implantation (CI) is a safe and beneficial surgery for children with congenital inner ear malformations, with the exception of cochlear nerve aplasia. The combination of microtia with middle and inner ear abnormalities is extremely uncommon and sufficiently severe to make a surgical approach to the cochlea difficult. We report herein the case of a 2-year-old girl who presented with profound bilateral sensorineural hearing loss, congenital aural atresia, microtia, and inner ear malformations. High-resolution computed tomography revealed poor development of the bilateral middle ear spaces, absence of the incus and stapes, aberrant courses of facial nerves, aplastic lateral semicircular canals, and covered round windows. With intraoperative imaging assistance, sequential bilateral CI was performed using a transmastoid approach with no complication. We propose that CI is feasible in patients with severe external and middle ear malformations. However, major malformations increase the risk of complications. As the facial nerve and cochlea are difficult to locate due to the lack of important anatomical landmarks, detailed planning and adequate preparation, including review of the preoperative imaging data, and the use of facial nerve monitoring and intraoperative imaging are very important. In addition, experienced surgeons should perform CI to ensure the success of the operation.


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