Radionuclide lymphoscintigraphy—Gold standard for assessment of lymphatic malformation: Lymphangioma and primary lymphedema or both?

Lymphedema is a chronic, progressive, and often debilitating condition. Primary lymphedema is a lymphatic malformation developing during the later stage of lymph angiogenesis. Secondary lymphedema is the result of obstruction or disruption of the lymphatic system, which can occur as a consequence of tumors, surgery, trauma, infection, inflammation, and radiation therapy. Here, we report a 64-year-old woman presenting with hyperkeratosis, a lymphedema due to metastatic uterus carcinoma. In this paper, we present the effects of complex decongestive physiotherapy on lymphedema and hyperkeratosis.

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Truncular Lymphatic Malformation (LM): Primary Lymphedema

Congenital Vascular Malformations ◽

10.1007/978-3-662-46709-1_19 ◽

2017 ◽

pp. 121-128 ◽

Cited By ~ 1

Author(s):

Ningfei Liu

Keyword(s):

Lymphatic Malformation ◽

Primary Lymphedema

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Radionuclide Lymphoscintigraphy in the Diagnosis of Idiopathic Congenital Lymphedema– a Case Report

Bangladesh Journal of Nuclear Medicine ◽

10.3329/bjnm.v18i2.35242 ◽

2018 ◽

Vol 18 (2) ◽

pp. 183-185

Author(s):

Shamim MF Begum ◽

Nasreen Sultana ◽

Rahima Parveen ◽

Amardeep Chaudhury ◽

Fatima Begum

Keyword(s):

Family History ◽

De Novo ◽

Primary Diagnosis ◽

Interesting Case ◽

Genetic Event ◽

Live Births ◽

Dysmorphic Features ◽

Primary Lymphedema ◽

History Of ◽

Radionuclide Lymphoscintigraphy

Congenital lymphedema is the rarest form of primary lymphedema, accounting for approximately 1: 60,000 live births. Congenital lymphedema can be classified into familial (hereditary) and idiopathic (non hereditary) subgroups. When congenital lymphedema is of the hereditary form the eponym Milroy disease is applied. Lymphedema without any dysmorphic features and no family history of lymphedema the eponym idiopathic congenital lymphedema is utilized. Etiology of idiopathic primary congenital lymphedema is unknown and a de novo genetic event of genes involved in lymphangiogenesis is a possibility. Radionuclide lymphoscintigraphy is considered as a gold standard for the diagnosis of lymphedema. This reported interesting case was an eleven months old girl having swelling of right lower limb since birth. There was no family history of lymphedema and no any dysmorphic features consistent with Milroy disease. The primary diagnosis was congenital lymphedema of idiopathic (non hereditary) subtype. Lymphoscintigraphic with Technetium-99m (Tc- 99m nanocolloid) revealed no lymphatic channels or inguinal lymph nodes on right side in early or delayed images up to 2 hours views and the diagnosis of primary idiopathic congenital lymphedema was confirmed.Bangladesh J. Nuclear Med. 18(2): 183-185, July 2015

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