scholarly journals Quantitative Relationships between Huntingtin Levels, Polyglutamine Length, Inclusion Body Formation, and Neuronal Death Provide Novel Insight into Huntington's Disease Molecular Pathogenesis

2010 ◽  
Vol 30 (31) ◽  
pp. 10541-10550 ◽  
Author(s):  
J. Miller ◽  
M. Arrasate ◽  
B. A. Shaby ◽  
S. Mitra ◽  
E. Masliah ◽  
...  
Keyword(s):  
Huntington's Disease ◽  
Huntington’S Disease ◽  
Inclusion Body ◽  
Neuronal Death ◽  
Molecular Pathogenesis ◽  
Body Formation ◽  
Inclusion Body Formation ◽  
Insight Into

scholarly journals Inclusion body formation reduces levels of mutant huntingtin and the risk of neuronal death

Nature ◽  
2004 ◽  
Vol 431 (7010) ◽  
pp. 805-810 ◽  
Author(s):  
Montserrat Arrasate ◽  
Siddhartha Mitra ◽  
Erik S. Schweitzer ◽  
Mark R. Segal ◽  
Steven Finkbeiner
Keyword(s):  
Inclusion Body ◽  
Neuronal Death ◽  
Mutant Huntingtin ◽  
Body Formation ◽  
Inclusion Body Formation

scholarly journals Specificity in intracellular protein aggregation and inclusion body formation

2001 ◽  
Vol 98 (23) ◽  
pp. 13060-13065 ◽  
Author(s):  
R. S. Rajan ◽  
M. E. Illing ◽  
N. F. Bence ◽  
R. R. Kopito
Keyword(s):  
Protein Aggregation ◽  
Inclusion Body ◽  
Intracellular Protein ◽  
Body Formation ◽  
Inclusion Body Formation

scholarly journals ‘Tissue’ transglutaminase ablation reduces neuronal death and prolongs survival in a mouse model of Huntington's disease

2002 ◽  
Vol 9 (9) ◽  
pp. 873-880 ◽  
Author(s):  
P G Mastroberardino ◽  
C Iannicola ◽  
R Nardacci ◽  
F Bernassola ◽  
V De Laurenzi ◽  
...  
Keyword(s):  
Mouse Model ◽  
Huntington's Disease ◽  
Huntington’S Disease ◽  
Neuronal Death ◽  
Tissue Transglutaminase
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