scholarly journals Acquired Long QT Syndrome and Electrophysiology of Torsade de Pointes

2019 ◽  
Vol 8 (2) ◽  
pp. 122-130 ◽  
Author(s):  
Nabil El-Sherif ◽  
Gioia Turitto ◽  
Mohamed Boutjdir
Keyword(s):  
Long Qt Syndrome ◽  
Clinical Presentation ◽  
Torsade De Pointes ◽  
Long Qt ◽  
Healthcare Teams ◽  
Acquired Long Qt Syndrome ◽  
Therapeutic Decisions ◽  
Qt Syndrome ◽  
Congenital Lqts ◽  
Congenital Long Qt Syndrome

Congenital long QT syndrome (LQTS) has been the most investigated cardiac ion channelopathy. Although congenital LQTS remains the domain of cardiologists, cardiac electrophysiologists and specialised centres, the much more frequently acquired LQTS is the domain of physicians and other members of healthcare teams required to make therapeutic decisions. This paper reviews the electrophysiological mechanisms of acquired LQTS, its ECG characteristics, clinical presentation, and management. The paper concludes with a comprehensive review of the electrophysiological mechanisms of torsade de pointes.

A rare indication of permanent pacemaker implantation in children: congenital long QT syndrome

2020 ◽  
Vol 30 (12) ◽  
pp. 1880-1881
Author(s):  
Mehmet Taşar ◽  
Nur Dikmen Yaman ◽  
Huseyin Dursin ◽  
Murat Şimşek ◽  
Senem Özgür
Keyword(s):  
Sudden Death ◽  
Long Qt Syndrome ◽  
Pacemaker Implantation ◽  
Torsades De Pointes ◽  
Permanent Pacemaker ◽  
Long Qt ◽  
Permanent Pacemaker Implantation ◽  
Qt Syndrome ◽  
Congenital Lqts ◽  
Congenital Long Qt Syndrome

AbstractCongenital Long QT Syndrome (LQTS) is a dangerous arrhythmic disorder that can be diagnosed in children with bradycardia. It is characterised by a prolonged QT interval and torsades de pointes that may cause sudden death. Long QT syndrome is an ion channelopathy with complex molecular and physiological infrastructure. Unlike the acquired type, congenital LQTS has a genetic inheritance and it may be diagnosed by syncope, stress in activity, cardiac dysfunction, sudden death or sometimes incidentally. Permanent pacemaker implantation is required for LQTS with resistant bradycardia even in children to resolve symptoms and avoid sudden death.

Acquired long QT syndrome and torsade de pointes

2018 ◽  
Vol 41 (4) ◽  
pp. 414-421 ◽  
Author(s):  
Nabil El-Sherif ◽  
Gioia Turitto ◽  
Mohamed Boutjdir
Keyword(s):  
Long Qt Syndrome ◽  
Torsade De Pointes ◽  
Long Qt ◽  
Acquired Long Qt Syndrome ◽  
Qt Syndrome

Torsade de pointes during sevoflurane anesthesia in a child with congenital long QT syndrome

2006 ◽  
Vol 16 (1) ◽  
pp. 63-65 ◽  
Author(s):  
MAX SAUSSINE ◽  
ISLAM MASSAD ◽  
FRANCK RACZKA ◽  
JEAN-MARC DAVY ◽  
JEAN-MARC FRAPIER
Keyword(s):  
Long Qt Syndrome ◽  
Torsade De Pointes ◽  
Sevoflurane Anesthesia ◽  
Long Qt ◽  
Qt Syndrome ◽  
Congenital Long Qt Syndrome

scholarly journals Mode of onset of torsade de pointes in congenital long QT syndrome

1996 ◽  
Vol 28 (5) ◽  
pp. 1262-1268 ◽  
Author(s):  
Sami Viskin ◽  
Srinivasa R. Alla ◽  
Hal V. Barron ◽  
Karin Heller ◽  
Leslie Saxon ◽  
...  
Keyword(s):  
Long Qt Syndrome ◽  
Torsade De Pointes ◽  
Long Qt ◽  
Qt Syndrome ◽  
Congenital Long Qt Syndrome

scholarly journals Chronic Amiodarone Evokes No Torsade de Pointes Arrhythmias Despite QT Lengthening in an Animal Model of Acquired Long-QT Syndrome

Circulation ◽  
2001 ◽  
Vol 104 (22) ◽  
pp. 2722-2727 ◽  
Author(s):  
Jurren M. van Opstal ◽  
Marieke Schoenmakers ◽  
S. Cora Verduyn ◽  
S.H. Marieke de Groot ◽  
Jet D.M. Leunissen ◽  
...  
Keyword(s):  
Animal Model ◽  
Long Qt Syndrome ◽  
Torsade De Pointes ◽  
Long Qt ◽  
Acquired Long Qt Syndrome ◽  
Qt Syndrome

scholarly journals Torsade de Pointes in Amiodarone-associated Acquired Long-QT Syndrome

2015 ◽  
Vol 83 (4) ◽  
pp. 349-351
Author(s):  
Carlos Ferrando ◽  
Federico Rivero ◽  
Federico Machado
Keyword(s):  
Long Qt Syndrome ◽  
Torsade De Pointes ◽  
Long Qt ◽  
Acquired Long Qt Syndrome ◽  
Qt Syndrome

scholarly journals Propofol abolishes torsade de pointes in different models of acquired long QT syndrome

2020 ◽  
Vol 10 (1) ◽  
Author(s):  
Christian Ellermann ◽  
Hilke Könemann ◽  
Julian Wolfes ◽  
Benjamin Rath ◽  
Felix K. Wegner ◽  
...  
Keyword(s):  
Long Qt Syndrome ◽  
Torsade De Pointes ◽  
Long Qt ◽  
Acquired Long Qt Syndrome ◽  
Qt Syndrome
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