Congenital Complete Heart Block

AbstractPermanent pacemaker implantation in low birthweight (LBW) babies with congenital complete heart block is extremely challenging due to a paucity of appropriate pulse generator placement pocket sites. The development of infection following an implantation procedure can pose a life-threatening risk to the patients. With more patients in the younger group receiving these devices than ever before and the rate of infection increasing rapidly, a closer look at the burden of infection and its impact on outcome of these patients is warranted. We report mucormycosis infection at the abdominal pacemaker pocket site of an infant requiring pacemaker explantation and re-insertion into the intrapleural space.

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Transient Congenital Complete Heart Block: A Case Report

Children ◽

10.3390/children8090790 ◽

2021 ◽

Vol 8 (9) ◽

pp. 790

Author(s):

Ying-Tzu Ju ◽

Yu-Jen Wei ◽

Ming-Ling Hsieh ◽

Jieh-Neng Wang ◽

Jing-Ming Wu

Keyword(s):

Heart Block ◽

Rare Case ◽

Complete Heart Block ◽

Normal Sinus Rhythm ◽

Structural Heart Disease ◽

Normal Heart ◽

Complete Atrioventricular Block ◽

Normal Sinus ◽

Congenital Complete Heart Block ◽

Complete Atrioventricular

Congenital complete heart block is defined as a complete atrioventricular block occurring prenatally, at birth, or within the first month of life. Congenital complete heart block has a high mortality rate, and in infants with normal heart morphology, it is often associated with maternal connective tissue disease. In these latter cases, neonatal congenital complete heart block is usually irreversible. We present a rare case of a female neonate who had bradycardia noted at a gestational age of 37 weeks. Her mother had no autoimmune disease history. She had no structural heart disease, and the serology surveys for autoantibodies including SSA/Ro and SSB/La were all negative. Without intervention or medication, her congenital complete heart block completely recovered to a normal sinus rhythm within 5 days. The cause of the transient congenital complete heart block was unknown in this case.

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Congenital complete heart block in pregnancy

Hormone Molecular Biology and Clinical Investigation ◽

10.1515/hmbci-2018-0042 ◽

2018 ◽

Vol 35 (2) ◽

Author(s):

Nurul Iftida Basri ◽

Shuhaila Ahmad

Keyword(s):

Postpartum Period ◽

Heart Block ◽

Multidisciplinary Approach ◽

Complete Heart Block ◽

Breech Presentation ◽

Permanent Pacemaker ◽

External Cephalic Version ◽

Congenital Complete Heart Block ◽

Temporary Pacemaker ◽

In Pregnancy

Abstract Complete heart block (CHB) is infrequently encountered during pregnancy. Its management requires a multidisciplinary approach involving the obstetrician, cardiologist, anesthetist and neonatologist. It varies from conservative, temporary or permanent pacemaker (PPM) insertion (either during the antenatal, intrapartum or postpartum period). We present the case of a 30-year-old, gravida 2 para 1 at the 36-week period of amenorrhea (POA) with congenital CHB. She was asymptomatic throughout her pregnancy despite having a pulse rate between 40 and 50 beats per minute. She delivered a healthy boy via cesarean section due to breech presentation after a failed external cephalic version. A temporary pacemaker was inserted prior to delivery. However, she required permanent insertion of pacemaker during the postpartum period.

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CONGENITAL HEART BLOCK DUE TO A LESION IN THE CONDUCTION SYSTEM

PEDIATRICS ◽

10.1542/peds.45.4.640 ◽

1970 ◽

Vol 45 (4) ◽

pp. 640-650

Author(s):

Cirilo Sotelo-Avila ◽

Harvey S. Rosenberg ◽

Dan G. McNamara

Keyword(s):

Heart Block ◽

Congenital Heart ◽

Complete Heart Block ◽

Fibrous Tissue ◽

Postmortem Examination ◽

Conduction System ◽

Cardiac Conduction ◽

Fibrous Body ◽

Congenital Complete Heart Block ◽

Bundle Of His

The cardiac conduction system of an infant with congenital complete heart block was studied at postmortem examination by subserial sections of the interatrial and interventricular septa. A localized area of necrosis in the central fibrous body interrupted the penetrating portion of the bundle of His. The cardiac structure was intact, with no abnormality other than the lesions in the fibrous tissue. The lesion is interpreted as the result of an acquired inflammation late in intrauterine life, with damage localized to the cardiac central fibrous body.

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