scholarly journals Impaired Autonomic and Repolarization Abnormalities are Observed in Patients with Facioscapulohumeral Dystrophy Despite Normal Myocardial Functions

2018 ◽  
Vol 05 (01) ◽  
Author(s):  
Caglar EC
Keyword(s):  
Facioscapulohumeral Dystrophy ◽  
Repolarization Abnormalities

scholarly journals Impaired autonomic and repolarization abnormalities in patients with facioscapulohumeral dystrophy

2018 ◽  
Vol 35 (3) ◽  
pp. 127-131
Author(s):  
Caglar Emre Cagliyan ◽  
◽  
Hakan Gelincik ◽  
Aziz Inan Celik ◽  
Filiz Koc ◽  
...  
Keyword(s):  
Facioscapulohumeral Dystrophy ◽  
Repolarization Abnormalities

Facioscapulohumeral dystrophy presenting as axial myopathy

2007 ◽  
Vol 34 (S 2) ◽  
Author(s):  
K Traufeller ◽  
K Eger ◽  
J Hobohm ◽  
M Deschauer ◽  
S Zierz
Keyword(s):  
Facioscapulohumeral Dystrophy

scholarly journals B-PO04-153 SUBTLE REPOLARIZATION ABNORMALITIES IN IDIOPATHIC VENTRICULAR FIBRILLATION ARE UNCOVERED BY NONINVASIVE ELECTROCARDIOGRAPHIC IMAGING, BUT NOT THE 12-LEAD ELECTROCARDIOGRAM

Heart Rhythm ◽  
2021 ◽  
Vol 18 (8) ◽  
pp. S340-S341
Author(s):  
Matthijs J. Cluitmans ◽  
Bianca van Rees ◽  
Job Stoks ◽  
Uyen Nguyen ◽  
Rachel M.A. ◽  
...  
Keyword(s):  
Ventricular Fibrillation ◽  
Electrocardiographic Imaging ◽  
Idiopathic Ventricular Fibrillation ◽  
Repolarization Abnormalities

Dynamics of the QT intervals encompassing secondary repolarization abnormalities during sudden but transient lengthening of the RR intervals

2003 ◽  
Vol 91 (7) ◽  
pp. 883-885 ◽  
Author(s):  
Federico Moleiro ◽  
Agustin Castellanos ◽  
Jorge O. Diaz ◽  
Robert J. Myerburg
Keyword(s):  
Rr Intervals ◽  
Qt Intervals ◽  
Repolarization Abnormalities

scholarly journals Pain location and intensity impacts function in persons with myotonic dystrophy type 1 and facioscapulohumeral dystrophy with chronic pain

2014 ◽  
Vol 49 (6) ◽  
pp. 900-905 ◽  
Author(s):  
Jordi Miró ◽  
Kevin J. Gertz ◽  
Gregory T. Carter ◽  
Mark P. Jensen
Keyword(s):  
Chronic Pain ◽  
Myotonic Dystrophy ◽  
Myotonic Dystrophy Type 1 ◽  
Myotonic Dystrophy Type ◽  
Facioscapulohumeral Dystrophy ◽  
Pain Location

Mortality Risk Associated With Bundle Branch Blocks and Related Repolarization Abnormalities (from the Women's Health Initiative [WHI])

2012 ◽  
Vol 110 (10) ◽  
pp. 1489-1495 ◽  
Author(s):  
Zhu-ming Zhang ◽  
Pentti M. Rautaharju ◽  
Elsayed Z. Soliman ◽  
JoAnn E. Manson ◽  
Michael E. Cain ◽  
...  
Keyword(s):  
Women’S Health ◽  
Women's Health ◽  
Mortality Risk ◽  
Women's Health Initiative ◽  
Women’S Health Initiative ◽  
Health Initiative ◽  
Bundle Branch Blocks ◽  
Repolarization Abnormalities ◽  
The Women’S Health Initiative

Scapulothoracic Fixation Orthosis for Facioscapulohumeral Dystrophy

2001 ◽  
Vol 12 (4) ◽  
pp. 106-109 ◽  
Author(s):  
Serap Alsancak ◽  
Haydar Altinkaynak ◽  
Hakan Kinik
Keyword(s):  
Facioscapulohumeral Dystrophy

Abstract 15002: Towards Unmasking Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy in the Early Concealed Stage

Circulation ◽  
2014 ◽  
Vol 130 (suppl_2) ◽  
Author(s):  
Thomas P Mast ◽  
Arco J Teske ◽  
Jeroen F vd Heijden ◽  
Judith A Groeneweg ◽  
Pieter A Doevendans ◽  
...  
Keyword(s):  
Right Ventricular ◽  
Arrhythmogenic Right Ventricular Dysplasia ◽  
Tissue Doppler ◽  
Doppler Imaging ◽  
Apical Region ◽  
Free Wall ◽  
Right Ventricular Dysplasia ◽  
Mutation Carriers ◽  
Increased Risk ◽  
Repolarization Abnormalities

Background: The concealed stage of arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) is associated with increased risk of sudden cardiac death. However, particular at this stage disease detection is hampered by absence of criteria. Activation delay (AD) is a hallmark of arrhythmogenesis in ARVD/C. Echocardiographic tissue Doppler imaging (TDI) may unmask AD in the absence of electrocardiographic (ECG) abnormalities. Methods: Three groups were compared 1) symptomatic definite ARVD/C patients with a mutation in the Plakophilin-2 ( PKP2) gene (n=37), 2) asymptomatic PKP2 mutation carriers (n=20) and 3) healthy controls (n=30). All groups underwent full echocardiographic examination with additional TDI of the right ventricular (RV) free wall and a routine 12-lead ECG recording. As surrogate for AD the electro-mechanical interval (EMI) was measured, defined as time between local first electrical deflection and local onset of mechanical shortening. EMI was measured in the subtricuspid, mid and apical region of the RV free wall. Detailed ECG analysis of depolarization (AD analysis) and repolarization abnormalities was performed in all subjects. Results: EMI was prolonged in all RV segments in ARVD/C patients compared to controls. Abnormal depolarization and repolarization was recorded in respectively 23 and 27 ARVD/C patients. In asymptomatic mutation carriers EMI was significantly prolonged in the subtricuspid area (Table 1). However, the ECG showed in 5/20 subjects only prolonged terminal activation duration and no repolarization abnormalities. Conclusion: TDI unmasks AD in both ARVD/C patients and asymptomatic mutation carriers. In asymptomatic mutation carriers EMI is prolonged in the subtricuspid area, whereas ECG appeared normal in the large majority. AD in the subtricuspid area is an early sign of disease in the concealed ARVD/C stage and may contribute to advanced risk stratification. Table 1: Results

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