Paget's Disease Causing an Arnold-Chiari Type 1 Malformation

2001 ◽  
Vol 176 (3) ◽  
pp. 816-817 ◽  
Author(s):  
Polly S. Richards ◽  
Alexandra Bargiota ◽  
Roger J. M. Corrall
Keyword(s):  
Paget’S Disease ◽  
Paget's Disease ◽  
Chiari Type ◽  
Chiari Type 1 Malformation

scholarly journals Acquired Chiari Type 1 Malformation Secondary to Paget’s Disease of the Bone: A Case Report

2021 ◽  
Author(s):  
Srestha Khan ◽  
Senthil Kumar Aiyappan ◽  
Abinesh Govindarajan ◽  
Vinayagam Shanmugam
Keyword(s):  
Paget’S Disease ◽  
Foramen Magnum ◽  
Paget's Disease ◽  
Cerebellar Tonsil ◽  
Vertebral Collapse ◽  
Chiari Type ◽  
Chiari Type 1 Malformation ◽  
Unsteady Gait ◽  
Magnetic Resonance Imaging Mri

Chiari type 1 malformations are characterised by caudal descent of cerebellar tonsil into foramen magnum. Usually it is congenital. Paget’s disease causing acquired chiari type 1 malformation is rare with only five reported cases in the literature. The diagnosis is primarily by Magnetic Resonance Imaging (MRI). Authors reported a case of acquired chiari type 1 malformation due to paget’s disease in a 58-year-old male patient diagnosed by MRI and Computed Tomography (CT). The patient presented with complaints of headache, unsteady gait, slow movements with weakness in all the four limbs, difficulty in walking which aggravated since three days and stammering of speech. Initially a diagnosis of motor neuron disease was suspected and the patient was subjected for MRI examination of brain and spine. MRI revealed platybasia with cerebellar tonsillar herniation with calvarial thickening and multiple vertebral collapse. The CT of brain and spine was done to evaluate bones specifically in view of thickened cranial vault and multiple vertebral collapse on MRI which revealed features of paget’s disease in the form of widened sclerotic bone with lytic areas and thickened trabeculae. Hence, diagnosis of paget’s disease causing acquired chiari type 1 malformation was made which correlated with biochemical findings. The management is different in primary and acquired chiari type 1 malformation and hence it is important to diagnose this condition which is relatively rare.

scholarly journals Chiari type 1 malformation associated with central sleep apnea after high dose growth hormone (GH) therapy in a 12-year-old boy: A case report

2018 ◽  
Vol 27 (1) ◽  
pp. 45-51 ◽  
Author(s):  
Toshihiko Mori ◽  
Eri Nishino ◽  
Tomomi Jitsukawa ◽  
Emiko Hoshino ◽  
Satoshi Hirakawa ◽  
...  
Keyword(s):  
Growth Hormone ◽  
Case Report ◽  
Sleep Apnea ◽  
Central Sleep Apnea ◽  
High Dose ◽  
Gh Therapy ◽  
Chiari Type ◽  
Chiari Type 1 Malformation

scholarly journals A case report of Arnold Chiari type 1 malformation in acromesomelic dwarf infant

2021 ◽  
Vol 38 ◽  
Author(s):  
Miteshkumar Rajaram Maurya ◽  
Renju Ravi ◽  
Sona Ajit Pungavkar
Keyword(s):  
Case Report ◽  
Chiari Type ◽  
Chiari Type 1 Malformation

One-Year Outcomes of Chiari Type 1 Malformation and Syringomyelia Treated With Posterior Fossa Decompression

2021 ◽  
Vol Publish Ahead of Print ◽  
Author(s):  
Shiyuan Han ◽  
Jun Gao ◽  
Zhimin Li ◽  
Xin Wang ◽  
Yongning Li
Keyword(s):  
Posterior Fossa ◽  
Posterior Fossa Decompression ◽  
Chiari Type ◽  
Chiari Type 1 Malformation ◽  
One Year

The neurophysiological balance in Chiari type 1 malformation (CM1), tethered cord and related syndromes

2011 ◽  
Vol 32 (S3) ◽  
pp. 311-316 ◽  
Author(s):  
Scaioli Vidmer ◽  
Curzi Sergio ◽  
Saletti Veronica ◽  
Tripaldi Flavia ◽  
Esposito Silvia ◽  
...  
Keyword(s):  
Tethered Cord ◽  
Chiari Type ◽  
Chiari Type 1 Malformation

Inverted V sign in hydromyelia with Chiari type 1 malformation

2012 ◽  
Vol 113 (1) ◽  
pp. 79-80 ◽  
Author(s):  
Hung Youl Seok ◽  
Mi-Yeon Eun ◽  
Hyun Woo Yang
Keyword(s):  
Chiari Type ◽  
Chiari Type 1 Malformation
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