scholarly journals Interruption of Left Pulmonary Artery with Right Sided Aortic Arch with TOF: A Complete Anomaly Combination

2012 ◽  
Vol 1 (1) ◽  
pp. 37-40
Author(s):  
Kiran Gangadhar
Keyword(s):  
Pulmonary Artery ◽  
Aortic Arch ◽  
Tetralogy Of Fallot ◽  
Clinical Features ◽  
Clinical Symptoms ◽  
Young Male ◽  
Left Pulmonary Artery ◽  
Congenital Disorder ◽  
Rare Congenital Disorder

Interruption of the pulmonary artery is a rare congenital disorder. The clinical symptoms are non-specific and radiological investigations are the key to diagnosis. We present a case of interruption of the left pulmonary artery associated with Tetralogy of Fallot in a young male. The radiological and clinical features of this condition are also reviewed. DOI: http://dx.doi.org/10.3126/njr.v1i1.6322 Nepalese Journal of Radiology Vol.1(1): 37-40

Anomalous origin of a pulmonary artery in a teenager with tetralogy of Fallot with associated double aortic arch and coronary arteriovenous fistula

2019 ◽  
Vol 29 (5) ◽  
pp. 727-729
Author(s):  
Vishal Agrawal ◽  
Parth Solanki ◽  
Ritesh Shah ◽  
Divyakant Parmar ◽  
Amit Mishra
Keyword(s):  
Pulmonary Artery ◽  
Aortic Arch ◽  
Tetralogy Of Fallot ◽  
Vascular Ring ◽  
Right Ventricular Outflow Tract ◽  
Left Pulmonary Artery ◽  
Ventricular Outflow Tract ◽  
Double Aortic Arch ◽  
Anomalous Origin ◽  
Tract Fistula

AbstractWe report the case of a 14-year-old female who had tetralogy of Fallot along with anomalous origin of the left pulmonary artery from the ascending aorta with co-dominant double aortic arch forming a complete vascular ring compressing the oesophagus along with a left main coronary artery to right ventricular outflow tract fistula. She underwent surgical correction without conduit placement.

scholarly journals CONGENITAL ABSENCE OF THE PULMONARY VALVE IN TETRALOGY OF FALLOT AND ORIGIN OF THE LEFT PULMONARY ARTERY FROM THE AORTIC ARCH

1970 ◽  
Vol 110 (3) ◽  
pp. 505-508 ◽  
Author(s):  
FELIX WYLER ◽  
MARKUS RUTISHAUSER ◽  
ARNI OLAFSSON ◽  
HERBERT J. KAUFMANN
Keyword(s):  
Pulmonary Artery ◽  
Aortic Arch ◽  
Tetralogy Of Fallot ◽  
Pulmonary Valve ◽  
Left Pulmonary Artery ◽  
Congenital Absence

Tetralogy of Fallot With Absent Pulmonary Valve Syndrome, Right Aortic Arch, and Disconnected Left Pulmonary Artery

2013 ◽  
Vol 4 (2) ◽  
pp. 206-209 ◽  
Author(s):  
Ruth Solana-Gracia ◽  
David Crossland ◽  
Leslie Mitchell ◽  
Christopher Wren ◽  
Massimo Griselli
Keyword(s):  
Pulmonary Artery ◽  
Aortic Arch ◽  
Tetralogy Of Fallot ◽  
Pulmonary Valve ◽  
Left Pulmonary Artery ◽  
Right Aortic Arch ◽  
Absent Pulmonary Valve ◽  
Absent Pulmonary Valve Syndrome

Tetralogy of Fallot with double aortic arch and discontinuous left pulmonary artery

2014 ◽  
Vol 31 (2) ◽  
pp. 427-428
Author(s):  
Ananth Ravi ◽  
Shilpa Hegde ◽  
Bruce Greenberg
Keyword(s):  
Pulmonary Artery ◽  
Aortic Arch ◽  
Tetralogy Of Fallot ◽  
Left Pulmonary Artery ◽  
Double Aortic Arch

scholarly journals Unilateral Absence of the Pulmonary Artery Incidentally Found in Adulthood

2012 ◽  
Vol 2012 ◽  
pp. 1-3 ◽  
Author(s):  
Cenk Aypak ◽  
Hülya Yıkılkan ◽  
Zekai Uysal ◽  
Süleyman Görpelioğlu
Keyword(s):  
Pulmonary Artery ◽  
Chest Radiograph ◽  
Rare Case ◽  
Wide Spectrum ◽  
Ct Scanning ◽  
Left Pulmonary Artery ◽  
Congenital Disorder ◽  
Cardiac Anomalies ◽  
Rare Congenital Disorder ◽  
Pulmonary Artery Agenesis

Unilateral absence of the pulmonary artery (UAPA) or pulmonary artery agenesis is a rare congenital disorder presenting with a wide spectrum of symptoms. UAPA is usually associated with cardiac anomalies and surgically treated in childhood. We report a rare case of a 50-year-old woman who was diagnosed with left pulmonary artery agenesis without any other cardiac anomalies. Clinicians should be aware of the possibility of undiagnosed cases of UAPA in patients through a chest radiograph that suggests the diagnosis. Confirmation of the diagnosis and anatomic details can be discerned by CT scanning.

scholarly journals Total correction of tetralogy of Fallot associated with an anomalous left pulmonary artery arising from the aortic arch

1974 ◽  
Vol 68 (1) ◽  
pp. 51-58
Author(s):  
Yasuharu Imai ◽  
Yasushi Nishiya ◽  
Tetsuo Morikawa ◽  
Hiromi Kurosawa ◽  
Souji Konno
Keyword(s):  
Pulmonary Artery ◽  
Aortic Arch ◽  
Tetralogy Of Fallot ◽  
Left Pulmonary Artery ◽  
Total Correction

scholarly journals Salvage surgery for stage IVa thymic carcinoma combined with aortic arch resection – case report

2020 ◽  
Vol 15 (1) ◽  
Author(s):  
Hiroyuki Yamato ◽  
Soichiro Funaki ◽  
Kazuo Shimamura ◽  
Keiwa Kin ◽  
Toru Kuratani ◽  
...  
Keyword(s):  
Pulmonary Artery ◽  
Aortic Arch ◽  
Thymic Carcinoma ◽  
Salvage Surgery ◽  
Radical Resection ◽  
Left Pulmonary Artery ◽  
Aortic Arch Replacement ◽  
Extended Surgery ◽  
Malignant Pericardial Effusion ◽  
Increased Risk

Abstract Background Although complete surgical resection of thymic carcinoma is a prognostic factor, extended surgery combined with a major blood vessel procedure remains controversial because of the increased risk of mortality. We report a case of Stage IVa thymic carcinoma successfully resected with a pneumonectomy along with aortic arch replacement after chemotherapy. Case presentation A 45-year-old male was diagnosed with thymic carcinoma invasion to the aortic arch and left pulmonary artery. Malignant pericardial effusion was also noted, though disappeared after chemotherapy, thus surgical options were considered. A radical resection procedure including left pneumonectomy, aortic arch replacement with total rerouting of the supra-arch vessels, and right pulmonary artery plication was performed. The postoperative course was uneventful and the patient has been disease-free for 3 years. Conclusion Extended salvage surgery might be a valuable option for advanced thymic carcinoma.

scholarly journals Absent Left Pulmonary Artery and Right-sided Aortic Arch in Eisenmenger's Complex

Thorax ◽  
1958 ◽  
Vol 13 (4) ◽  
pp. 272-276 ◽  
Author(s):  
H. A. Fleming
Keyword(s):  
Pulmonary Artery ◽  
Aortic Arch ◽  
Left Pulmonary Artery ◽  
Absent Left Pulmonary Artery

Abstract 12430: Vicious Circle Between Progressive Right Ventricular Dilatation and Pulmonary Regurgitation in Patients After Tetralogy of Fallot Repair? Right Heart Enlargement Promotes Flow Reversal in the Left Pulmonary Artery

Circulation ◽  
2015 ◽  
Vol 132 (suppl_3) ◽  
Author(s):  
Atsuko Kato ◽  
Christian Drolet ◽  
Shi-Joon Yoo ◽  
Andrew Redington ◽  
Lars Grosse-Wortmann
Keyword(s):  
Pulmonary Artery ◽  
Tetralogy Of Fallot ◽  
Left Lung ◽  
Pulmonary Regurgitation ◽  
Left Pulmonary Artery ◽  
Flow Reversal ◽  
Left Hemithorax ◽  
Forward Flow ◽  
Lung Area ◽  
The Right

Introduction: The left pulmonary artery (LPA) contributes more than the right (RPA) to total pulmonary regurgitation (PR) in patients after tetralogy of Fallot (TOF) repair, but the mechanism of this difference is not well known. We hypothesized that unilaterally increased pulmonary vascular resistance (PVR), resulting from lung compression by the enlarged and levorotated heart leads to greater PR in the LPA. This study aimed to analyze the interplay between heart and lung size, mediastinal geometry, and differential PR. Methods: This is a single-center retrospective analysis of 50 magnetic resonance studies in patients after TOF repair. Patients with more than mild discrete branch pulmonary artery stenosis were excluded. Blood flow was measured by phase-contrast velocity encoding within the branch pulmonary arteries. On the axial image with the largest total cardiac surface area, cardiac angle (α) between the thoracic anterior-posterior line and the interventricular septum, right and left lung areas as well as right and left hemithorax areas were measured (Figure). Results: There was no difference in LPA and RPA diameters. The LPA showed significantly less total forward flow (p=0.04), smaller net forward flow (p=<0.001), and greater RF (p=0.001) than the RPA. Left lung area was smaller than the right (p<0.001). RVEDVi correlated with LPA RF (R=0.48, p<0.001), but not with RPA RF. Larger RVEDVi correlated with a larger α angle (R=0.46, p<0.001), i.e. a more leftward cardiac axis and with smaller left lung area (R=-0.58, p<0.001). LPA RF, but not RPA RF, correlated inversely with left lung area indexed to the left hemithorax area (R=-0.34, p=0.02). Conclusions: An enlarged and levorotated heart - as a result of PR - is associated with smaller left lung size, and augments diastolic flow reversal in the LPA, presumably via increased left PVR. By imposing a further volume load on the RV, LPA regurgitation may thus close a positive feed-back loop of PR and RV dilatation.

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