Uterine tumors resembling ovarian sex cord-like tumors (UTROST) are rarely encountered mesenchymal type of uterine tumors with unknown etiology. They usually exhibit nodular and polypoidal growth pattern and are commonly observed in the 4th to 6th decade. UTROSCTs behave benignly however limited data is available to date. Recently these tumors show a novel recurrent gene fusion involving the NCOA2/3 gene. Hysterectomy with bilateral salpingo-oophorectomy or tumor resection is a treatment option. We report a case of a 35 years old female who presented with dysfunctional uterine bleeding. The diagnosis was initially rendered on endometrial curetting’s and further confirmed on the hysterectomy specimen after application of immunohistochemistry.
Mazabraud's Syndrome Coexisting with a Uterine Tumor Resembling an Ovarian Sex Cord Tumor (UTROSCT): a Case Report
