scholarly journals Early Communication Intervention with Young Children with Pierre Robin Sequence

1998 ◽  
Vol 45 (1) ◽  
pp. 51-60 ◽  
Author(s):  
Lisl Fair ◽  
Brenda Louw
Keyword(s):  
Young Children ◽  
Expressive Language ◽  
Extended Period ◽  
Communication Intervention ◽  
Pierre Robin Sequence ◽  
Language Abilities ◽  
Early Communication ◽  
Robin Sequence ◽  
Velopharyngeal Incompetence ◽  
Pierre Robin

Young children with Pierre Robin sequence are at considerable risk to develop delayed or disordered communication development. This study investigated the effectiveness of early communication intervention with four young children with Pierre Robin sequence, aged 5 to 28 months. The Proportional Change Index (Wolery, 1983) was used to determine the amount of child progress that took place during the intervention period. The results indicated that regular early communication intervention sessions over an extended period of time produced positive results, especially for expressive language abilities. The presence of a slight hearing loss due to otitis media, seemed to have influenced the effectiveness of early communication intervention. One subject displayed an associated disorder and evidenced the slowest rate of development for receptive and expressive language abilities as well as a limited phonetic repertoire for consonants. All but one subject had limited phonetic repertoires possibly due to velopharyngeal incompetence. Early communication intervention services should be delivered regularly over an extended period of time and the hearing abilities and speech production skills of young children with Pierre Robin sequence should be followed closely during early communication intervention.

Pierre Robin Sequence With Esophageal Atresia and Congenital Radioulnar Synostosis

2006 ◽  
Vol 43 (3) ◽  
pp. 317 ◽  
Author(s):  
Keramettin Ugur Ozkan ◽  
Yusuf Kenan Coban ◽  
Murat Uzel ◽  
Mehmet Ergun ◽  
Hafize Oksuz
Keyword(s):  
Esophageal Atresia ◽  
Pierre Robin Sequence ◽  
Radioulnar Synostosis ◽  
Robin Sequence ◽  
Congenital Radioulnar Synostosis ◽  
Pierre Robin

scholarly journals Epidemiology of Pierre‐Robin sequence in Europe: A population‐based EUROCAT study

2021 ◽  
Author(s):  
Michele Santoro ◽  
Alessio Coi ◽  
Ingeborg Barišić ◽  
Anna Pierini ◽  
Marie‐Claude Addor ◽  
...  
Keyword(s):  
Population Based ◽  
Pierre Robin Sequence ◽  
Robin Sequence ◽  
Pierre Robin

A Systematic Review of Mandibular Distraction Osteogenesis Versus Orthodontic Airway Plate for Airway Obstruction Treatment in Pierre Robin Sequence

2021 ◽  
pp. 105566562110118
Author(s):  
Darren B. Abbas ◽  
Christopher Lavin ◽  
Evan J. Fahy ◽  
HyeRan Choo ◽  
Mai Thy Truong ◽  
...  
Keyword(s):  
Airway Obstruction ◽  
Distraction Osteogenesis ◽  
Literature Search ◽  
Oral Feeding ◽  
Treatment Modalities ◽  
Pierre Robin Sequence ◽  
Mandibular Distraction ◽  
Robin Sequence ◽  
Mandibular Distraction Osteogenesis ◽  
Pierre Robin

Objective: Mandibular distraction osteogenesis (MDO) is frequently performed to address airway obstruction in patients with Pierre Robin sequence (PRS), though more recently the technique of orthodontic airway plating (OAP) has gained traction. We aimed to evaluate OAP compared to MDO for airway obstruction in PRS. Design: A systematic literature search across PubMed, Embase, and Google Scholar identified all studies published in English, which involved MDO or any form of OAP as treatments for PRS. All relevant articles were reviewed in detail and reported on, adhering to PRISMA guidelines. Main Outcome Measures: Airway (tracheostomy avoidance, decannulation rate), feeding (full oral feeding tolerance). Results: Literature search identified 970 articles, of which 42 MDO studies and 9 OAP studies met criteria for review. A total of 1159 individuals were treated with MDO, and 322 individuals were treated with OAP. Primary outcomes appear similar for MDO and OAP at face value; however, this must be interpreted with different pretreatment contexts in mind. Conclusions: Orthodontic airway plating may be considered for airway obstruction in PRS, as some airway-related and feeding-related outcomes appear similar with MDO, per existing evidence in the literature. However, since PRS severity differed between studies, OAP cannot be uniformly considered a replacement for MDO. Further research is required to more comprehensively assess these treatment modalities inclusive of metrics that allow for direct comparison.

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