Adrenal adenoma in von Hippel–Lindau syndrome: A case report with review of literature

Intravascular Papillary Endothelial Hyperplasia (IPEH) or Masson’s Tumor is a benign vascular tumor, most commonly seen on the skin and usually on the head, neck or extremities. It is more common in women with no age predilection. Visceral involvement is very rare, with about 30 intra-abdominal reports. We present a case report of a 58 year old woman who underwent a CT scan due to dysphagia complaints, with an incidental known finding of growth in the adrenal adenoma, which was 5 cm in diameter on hospitalization. The patient underwent laparoscopic adrenalectomy. Biopsy results demonstrated a brownish yellow lesion, 2.8 cm in diameter, composed of a blood clot and septate. Immunochemical staining for CD31 and CD34 was positive and the lesion was diagnosed as an IPEH of pure form. Our review of literature examines different forms of IPEH, previous reports and characteristics of Masson’s tumors in the adrenal gland and stratifies ways of differentiation it from other benign or malignant lesions of the adrenal.

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Von Hippel-Lindau Disease–A Case Report and Review of Literature

UroToday International Journal ◽

10.3834/uij.1944-5784.2011.10.6 ◽

2011 ◽

Vol 04 (05) ◽

Author(s):

Vedamurthy Pogula Reddy ◽

Dandu Venkata Satya Rambabu

Keyword(s):

Case Report ◽

Review Of Literature ◽

Von Hippel Lindau ◽

Von Hippel Lindau Disease

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Lack of Occupation and Depression Onset in Oncology Patient – Case Report

European Psychiatry ◽

10.1016/j.eurpsy.2016.01.1831 ◽

2016 ◽

Vol 33 (S1) ◽

pp. S497-S498

Author(s):

L. Filipovic-Grcic ◽

F. Đerke ◽

M. Braš ◽

V. Djordjevic

Keyword(s):

Case Report ◽

Support Groups ◽

Psychiatric Treatment ◽

Patient Case ◽

Oncology Patient ◽

Von Hippel Lindau ◽

Cancer Support ◽

Cancer Support Groups ◽

Competing Interest ◽

Von Hippel Lindau Syndrome

Being able to live an active and meaningful life is important for mental health of every individual. In this case report we examine the life of an oncology patient who developed depression six years ago. The patient is a fifty seven year old woman who has been suffering from Von Hippel-Lindau syndrome for the last forty years. Her father and two uncles died from the same disease. She had her first operation when she was seventeen years old and has had numerous operations since then. During this time she has undergone four neurosurgical operations, nephrectomy, spine and pancreas operation and eye enucleation. Despite the fact that by being a chronic oncology patient she was prone to depression, she did not develop depressive symptoms. It did not happen even as her husband went to war and left her to take care of their child. It did not come afterwards as they struggled financially. Only after they moved to a new apartment and as she finished decorating it, did depression finally occur. During entire life she was an active, outgoing person, who took pleasure in socialising and various hobbies. She only developed depression after she was pensioned, left with the responsibility to care for her old mother. Following the psychiatric treatment she regained interest in people and become active in different cancer support groups. This example accentuates the importance of every-day pleasurable activities as a defence mechanism against depression.Disclosure of interestThe authors have not supplied their declaration of competing interest.

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Hemangioblastoma of hippocampus without von Hippel-Lindau disease: Case report and review of literature

Neurology India ◽

10.4103/0028-3886.24718 ◽

2006 ◽

Vol 54 (1) ◽

pp. 89 ◽

Cited By ~ 2

Author(s):

K Ohata ◽

T Takami ◽

N Tsuyuguchi ◽

M Hara ◽

M Haque

Keyword(s):

Case Report ◽

Review Of Literature ◽

Von Hippel Lindau ◽

Disease Case ◽

Von Hippel Lindau Disease

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Ovarian steroid cell tumour in an adolescent with von Hippel-Lindau syndrome: A case report and review of the literature

10.26226/morressier.596dfd56d462b8029238797a ◽

2017 ◽

Author(s):

Ana Marques

Keyword(s):

Case Report ◽

Cell Tumour ◽

Review Of The Literature ◽

Ovarian Steroid ◽

Von Hippel Lindau ◽

Von Hippel Lindau Syndrome

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Paraplegia in a patient with Von Hippel Lindau syndrome: surgical and reconstructive treatment of Marjolin’s ulcer. A case report

Spinal Cord ◽

10.1038/sc.2014.111 ◽

2014 ◽

Vol 52 (S3) ◽

pp. S1-S3 ◽

Cited By ~ 1

Author(s):

A Scalise ◽

C Tartaglione ◽

M Pierangeli ◽

E Bolletta ◽

M Fraccalvieri ◽

...

Keyword(s):

Case Report ◽

Von Hippel Lindau ◽

Marjolin’S Ulcer ◽

Von Hippel Lindau Syndrome

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Bilateral Adrenal Incidentalomas: A Case Report and Review of Diagnostic Challenges

Case Reports in Endocrinology ◽

10.1155/2013/953052 ◽

2013 ◽

Vol 2013 ◽

pp. 1-4

Author(s):

Anders L. Carlson ◽

Annis M. Marney ◽

Scott R. Anderson ◽

Matthew P. Gilbert

Keyword(s):

Case Report ◽

Genetic Testing ◽

Adrenal Mass ◽

Diagnostic Approach ◽

Diagnostic Strategy ◽

Adrenal Incidentalomas ◽

Von Hippel Lindau ◽

Additional Testing ◽

Adrenal Masses ◽

Von Hippel Lindau Syndrome

Incidentally discovered adrenal masses (incidentalomas) are common and present challenges both in diagnosis and management. When incidentally discovered adrenal masses are bilateral, a refined diagnostic approach is warranted since bilateral disease is more likely to be pathologic. We review a case of a 34-year-old man with incidentally discovered bilateral adrenal nodules. A comprehensive diagnostic strategy led to the diagnosis of bilateral pheochromocytoma caused by von Hippel-Lindau syndrome. He was successfully treated with bilateral laparoscopic adrenalectomy and has recovered well. While the initial diagnostic approach is similar to the unilateral incidentaloma, additional testing and/or genetic testing should be considered in the case of the bilateral adrenal mass.

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