scholarly journals A Third Labyrinthine Window: An Overview of Perilymph and Labyrinthine Fistulae and Superior Semicircular Canal Dehiscence

2012 ◽  
Vol 4 (2) ◽  
pp. 100-105 ◽  
Keyword(s):  
Inner Ear ◽  
Semicircular Canal ◽  
Membranous Labyrinth ◽  
Superior Semicircular Canal Dehiscence ◽  
Bony Labyrinth ◽  
Superior Semicircular Canal ◽  
Inner Ear Fluids ◽  
Canal Dehiscence

ABSTRACT The membranous labyrinth is contained within the bony labyrinth and surrounded by perilymph. The only two ‘potentially yielding’ parts of the otherwise solid bony labyrinth are the oval and round windows, which by their relative movements, pressure differentials and resilience are responsible for all the functions attributed to the inner ear. In pathologies, such as trauma, infection or occasionally congenital dehiscence, there may develop a ‘third window’ that may serve as an abnormal communication for the inner ear fluids and manifest with audiovestibular symptoms. Three such distinct entities have been identified, namely ‘superior semicircular canal dehiscence syndrome, perilymphatic fistulae and labyrinthine fistulae’. This overview intends to discuss these above-mentioned entities, as regards their characteristic presentations and principles of management. How to cite this article Hathiram BT, Khattar VS. A Third Labyrinthine Window: An Overview of Perilymph and Labyrinthine Fistulae and Superior Semicircular Canal Dehiscence. Otorhinolaryngol Clin Int J 2012;4(2):100-105.

scholarly journals Posterior semicircular canal dehiscence: a diagnostic and surgical conundrum

2019 ◽  
Vol 12 (7) ◽  
pp. e229573 ◽  
Author(s):  
Ajay Philip ◽  
Manju Deena Mammen ◽  
Anjali Lepcha ◽  
Anu Alex
Keyword(s):  
Conservative Management ◽  
Semicircular Canal ◽  
Posterior Semicircular Canal ◽  
Superior Semicircular Canal Dehiscence ◽  
Bony Labyrinth ◽  
Abnormal Pressure ◽  
Vestibular Symptoms ◽  
Inner Ear Fluids ◽  
Tullio’S Phenomenon ◽  
Canal Dehiscence

Third window defects have increasingly been identified as a cause of vertigo. These defects are bony dehiscences that occur in the bony labyrinth, resulting in abnormal pressure gradient in the inner ear fluids leading to sound (Tullio’s phenomenon) or pressure (Hennebert’s sign) induced vertigo. The superior semicircular canal dehiscence syndrome is a well-described entity in this regard, however defects of the posterior semicircular canal are rare and may have overlapping symptomatology. We describe the history, clinical profile and management of a patient who had importunate symptoms despite being on conservative management for a year and had resolution of vestibular symptoms following surgical management.

scholarly journals The Supine Superior Semicircular Canal Dehiscence Test

2021 ◽  
pp. 1-6
Author(s):  
Carrie W. Hoppes ◽  
Karen H. Lambert ◽  
Chris Zalewski ◽  
Robin Pinto ◽  
Holly Burrows ◽  
...  
Keyword(s):  
Dura Mater ◽  
Semicircular Canal ◽  
False Negative ◽  
New Method ◽  
Superior Semicircular Canal Dehiscence ◽  
Bony Labyrinth ◽  
Superior Semicircular Canal ◽  
Potential Benefits ◽  
Canal Dehiscence

Purpose The purpose of this clinical focus article is to describe a new method for assessment of superior semicircular canal dehiscence by laying the patient supine during Valsalva-induced nystagmus testing. Method The traditional Valsalva-induced nystagmus test is described, followed by a new method for assessment of superior semicircular dehiscence conducted by laying the patient supine during testing. A case study is presented to illustrate this new testing technique known as the Supine Superior Semicircular Canal Dehiscence Test. Results It is hypothesized that during Valsalva-induced nystagmus testing performed in the upright, seated position, the dura mater could potentially seal the superior semicircular canal fistula, thereby concealing a defect in the bony labyrinth and yielding a false-negative test. To circumvent this, the patient should be placed in the supine position during Valsalva-induced nystagmus testing in order to prevent the dura mater from inadvertently sealing itself against the petrous portion of the temporal bone. The Supine Superior Semicircular Canal Dehiscence Test may reveal the defect in the bony labyrinth and improve the sensitivity of the Valsalva-induced nystagmus test. Conclusions The Supine Superior Semicircular Canal Dehiscence Test may be more sensitive for identifying superior semicircular canal dehiscence in patients with traditional symptoms and a negative Valsalva-induced nystagmus test in the seated position. While a case study is presented to illustrate the potential benefits of including the Supine Superior Semicircular Canal Dehiscence Test in the battery of diagnostic tests, further research is needed in larger samples.

Incidence of Pediatric Superior Semicircular Canal Dehiscence and Inner Ear Anomalies

2016 ◽  
Vol 37 (9) ◽  
pp. 1370-1375 ◽  
Author(s):  
Eric M. Sugihara ◽  
Seilesh C. Babu ◽  
Dennis J. Kitsko ◽  
Michael S. Haupert ◽  
Prasad J. Thottam
Keyword(s):  
Inner Ear ◽  
Semicircular Canal ◽  
Superior Semicircular Canal Dehiscence ◽  
Superior Semicircular Canal ◽  
Ear Anomalies ◽  
Canal Dehiscence

Electrocochleography: New Uses for an Old Test and Normative Values

2019 ◽  
Vol 28 (3S) ◽  
pp. 783-795 ◽  
Author(s):  
John A. Ferraro ◽  
Paul R. Kileny ◽  
Signe S. Grasel
Keyword(s):  
Inner Ear ◽  
Tympanic Membrane ◽  
Case Studies ◽  
Semicircular Canal ◽  
Small Sample ◽  
Normative Values ◽  
Superior Semicircular Canal Dehiscence ◽  
Superior Semicircular Canal ◽  
The Status ◽  
Canal Dehiscence

Purpose This article combines the results of 3 studies that were presented at the HeAL 2018 Conference in Lake Como, Italy, in June 2018. Each study involved electrocochleography (ECochG), a neurodiagnostic evaluation that has been used clinically for over 80 years but whose applications continue to expand. The 1st study describes recent research wherein ECochG was recorded from asymptomatic subjects who were siblings or offspring of patients with a confirmed diagnosis of Ménière's disease (MD). Our results provide evidence that ECochG may be helpful in not only diagnosing MD but also predicting it as well. Second, case studies are described where ECochG was important in both diagnosing superior semicircular canal dehiscence and monitoring the repair of this condition during surgery. Finally, although ECochG has been practiced clinically for over 8 decades, the protocols for recording, measuring, and interpreting the electrocochleogram continue to lack standardization among clinicians and scientists. We thus present normative data for some of these features based on noninvasive recordings made from the tympanic membrane from 100 normal hearing subjects. Conclusions Although the primary use of ECochG continues to be in the diagnosis of MD, we report on 2 additional clinical applications for this important test of inner ear/auditory nerve function. First, a preliminary study on a small sample of subjects indicates that ECochG may also be useful in predicting MD prior to the onset of symptoms in individuals who may be genetically predisposed to developing it. Second, through a series of case studies, we demonstrate how ECochG is used to help diagnose superior semicircular canal dehiscence and monitor the status of the inner ear during the surgical repair of this condition. Finally, normative values for clinically important components of the electrocochleogram based on tympanic membrane recordings have been established from a large sample of subjects.

Clinical Outcomes of Middle Fossa Craniotomy for Superior Semicircular Canal Dehiscence Repair

2015 ◽  
Vol 76 (S 01) ◽  
Author(s):  
Lawrance Chung ◽  
Nolan Ung ◽  
Daniel Nagasawa ◽  
Panayiotis Pelargos ◽  
Kimberly Thill ◽  
...  
Keyword(s):  
Clinical Outcomes ◽  
Semicircular Canal ◽  
Middle Fossa ◽  
Superior Semicircular Canal Dehiscence ◽  
Superior Semicircular Canal ◽  
Canal Dehiscence
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