scholarly journals Fetal Autopsy Showing Two Ventral Body Wall Defects: An Unusual Presentation

2020 ◽  
Author(s):  
Anupriya Kaur ◽  
Arun Prasad ◽  
Jessy Jayaraman Pushpaja ◽  
Kanchan Kapoora
Keyword(s):  
Abdominal Wall ◽  
Body Wall ◽  
Abdominal Wall Defect ◽  
Lower Lobe ◽  
The Body ◽  
Unusual Presentation ◽  
Thoracic Wall ◽  
Fetal Autopsy ◽  
Wall Defect ◽  
The Right

Thoracoschisis and gastroschisis are types of ventral body wall defects. Usually thoracoabdominoschisis presents as a continuous defect. Here the authors present the case of autopsy of 18 weeks old fetus with two well-separated ventral body wall defects. Thoracoschisis was a right lateral thoracic wall defect while gastroschisis, a midline infraumblical abdominal wall defect. Through the right lateral thoracic wall parts of two organs appeared to be protruding. On dissection, 8th and 9th ribs with the liver and the lower lobe of the right lung were herniating outside the body. The right lung was haemorrhagic. Various embryological theories on ventral body wall defects have been discussed in view of the present case.

Left-Sided Gastroschisis

2006 ◽  
Vol 72 (7) ◽  
pp. 637-640 ◽  
Author(s):  
Kenneth W. Gow ◽  
Amina Bhatia ◽  
Daniel F. Saad ◽  
Mark L. Wulkan ◽  
Kurt F. Heiss
Keyword(s):  
Abdominal Wall ◽  
Clinical Course ◽  
Abdominal Wall Defect ◽  
Abdominal Wall Defects ◽  
Wall Defect ◽  
The Right

Gastroschisis is a periumbilical, abdominal wall defect arising to the right of the umbilicus. We describe the clinical course of a left-sided gastroschisis in a term female born at 39 weeks’ gestation. To our knowledge, there have been only 14 left-sided abdominal wall defects reported in the literature. We discuss our case and review the literature to try to determine if there is any clinic difference between right- versus left-sided lesions to make recommendations as to management.

Histology of a Paraumbilical Band in a Neonate with Gastroschisis

2011 ◽  
Vol 14 (6) ◽  
pp. 493-495 ◽  
Author(s):  
Ryuji Fukuzawa ◽  
Miki Toma ◽  
Aya Nomura
Keyword(s):  
Small Intestine ◽  
Abdominal Wall ◽  
Abdominal Wall Defect ◽  
Fibrous Tissue ◽  
The Other ◽  
Vascular Structure ◽  
Wall Defect ◽  
The Right

We report a case of gastroschisis in which a paraumbilical band was found at the right margin of the abdominal wall defect and extended into the antimesenteric side of the small intestine. The band consisted of 2 thin cords. Microscopically, 1 band showed a fibrous tissue, and the other 1 revealed a unique vascular structure resembling the vitelline artery and vein, suggesting that the paraumbilical band represents a remnant of the yolk stalk that failed to be incorporated into the umbilical stalk. The origin of the paraumbilical band and an associated pathogenetic hypothesis of gastroschisis are discussed.

scholarly journals Body Stalk Anomaly in a 9-Week Pregnancy

2014 ◽  
Vol 2014 ◽  
pp. 1-3 ◽  
Author(s):  
Fabio E. Quijano ◽  
María Mónica Rey ◽  
Mariana Echeverry ◽  
Roland Axt-Fliedner
Keyword(s):  
Abdominal Wall ◽  
Umbilical Cord ◽  
Abdominal Wall Defect ◽  
Termination Of Pregnancy ◽  
Pathologic Examination ◽  
Trigger Factors ◽  
Wall Defect ◽  
Malformation Syndrome ◽  
The Right

Body stalk anomaly is a rare and severe malformation syndrome in which the exact pathophysiology and trigger factors are still unknown. This is a case of a 30-year-old patient who underwent ultrasound at 9 weeks of gestation. It revealed an abnormal location of the inferior body of the embryo in the coelomic space. The findings suggested a short umbilical cord syndrome. In order to confirm the diagnosis, the patient was scheduled for a second ultrasonography at 11 weeks of gestation. The obtained images, confirmed the location of the inferior body in the coelomic space with no visible bladder, absence of the right leg, severe abdominal wall defect, consistent with an omphalocele, and a short 5 mm umbilical cord. These last ultrasonographic findings were consistent with body stalk anomaly. Because of severe malformation incompatible with life, the patient was offered termination of pregnancy. Pathologic examination confirmed the suspected pathology of body stalk anomaly.

scholarly journals Limb Body Wall Complex with Sacrococcygeal Mass and Agenesis of External Genitalia

2013 ◽  
Vol 2013 ◽  
pp. 1-3
Author(s):  
Prabahita Baruah ◽  
Pradipta Ray Choudhury
Keyword(s):  
Abdominal Wall ◽  
Body Wall ◽  
Abdominal Wall Defect ◽  
External Genitalia ◽  
Wall Defect

Limb body wall complex (LBWC) is a rare clinicopathological entity, characterized by the presence of an abdominal wall defect associated with variable spectrum of limb and visceral anomalies. A stillborn baby of LBWC with placentoabdominal phenotype is reported here. Kyphoscoliosis, sacrococcygeal mass and agenesis of external genitalia are the associated features.

scholarly journals Thoracoschisis associated with Limb Body Wall Complex

2017 ◽  
Vol 8 (3) ◽  
pp. 19 ◽  
Author(s):  
Dragana Vujovic ◽  
Aleksandar Sretenovic ◽  
Maja Raicevic ◽  
Marija Lukac ◽  
Tamara Krstajic ◽  
...  
Keyword(s):  
Chest Wall ◽  
Body Wall ◽  
Rare Condition ◽  
Thoracic Wall ◽  
Liver Lobe ◽  
Wall Defect ◽  
Thoracic Wall Reconstruction ◽  
The Right ◽  
Accessory Liver ◽  
Accessory Liver Lobe

Thoracoschisis is a rare condition. A female newborn presented with right-sided thoracoschisis, associated with diaphragmatic hernia and protrusion of an accessory liver lobe through the chest wall defect along with deformity of the right forearm and hand duplication. Diagnosed as part of the limb-body wall complex (LBWC), management included resection of the exteriorized liver lobe followed by right hemidiaphragm and thoracic wall reconstruction.

Gastroschisis-can be prevented?

2017 ◽  
Vol 6 (8) ◽  
pp. 3679
Author(s):  
Mahesweta Guru ◽  
Shefali Patil
Keyword(s):  
Abdominal Wall ◽  
Anterior Abdominal Wall ◽  
Abdominal Wall Defect ◽  
Tube Feeding ◽  
Wall Defect ◽  
Abdominal Wall Repair ◽  
Male Baby ◽  
The Right ◽  
Umbilical Cord Insertion ◽  
Ryle’S Tube

Gastroschisis is a congenital anterior abdominal wall defect, adjacent and usually to the right of the umbilical cord insertion. Gastroschisis has no covering sac and no associated syndromes. This differentiates it from an omphalocele, which usually is covered by a membranous sac. G4P3L1D2 by date 37 weeks by scan 37 weeks (17.2) Ultrasonography S/O Gastrochisis delivered a male baby of 2.4kg and was shifted to the NICU. The exposed contents were given cellulose dressing. On post-natal day 2 baby was taken for abdominal wall repair. Baby was started on Ryle’s tube feeding and was further managed by the neonatologist. 

scholarly journals The modern methods of X-Ray based diagnostic in cases of ectopia cordis associated with pentalogy of Cantrell

2017 ◽  
Vol 8 (4) ◽  
pp. 92-98
Author(s):  
Elena V. Kosovtsova ◽  
Alexandr V. Pozdnyakov ◽  
Nikolay G. Pilyugov ◽  
Alexey B. Naumov ◽  
Sergey P. Marchenko
Keyword(s):  
Surgical Treatment ◽  
Abdominal Wall ◽  
Abdominal Wall Defect ◽  
The Body ◽  
Ectopia Cordis ◽  
Pentalogy Of Cantrell ◽  
Wall Defect ◽  
X Ray ◽  
Septal Defects ◽  
Collateral Arteries

Pentalogy of Cantrell with ectopia cordis is an extremely rare and lethal congenital anomaly included congenital hearth disease (CHD), midline supraumbilical abdominal wall defect, defect of lower sternum part, deficiency of the anterior diaphragm, a defect in the diaphragmatic pericardium. The complexity of this syndrome is usually incompatible with life. Depending on the location of the protruding heart and on the extent of the body wall defect, ectopia cordis may be grouped into cervical, thoracic, thoracoabdominal, or abdominal types. The heart mostly uncovered, covered with a serous membrane less often, and covered with skin rare. Depending on combination defects pentalogy of Cantrell classified for 3 different classes by Toyama (classified in 1972): 1 class – complete syndrome (all five defects), 2 class – probable syndrome (included intracardial defect and ventral abdominal wall defect) 3 class – incomplete syndrome (with various combinations of defects present, including a sternal abnormality). Presented clinical case newborn pentalogy of Cantrell first Toyama class. We used X-Ray for firstly diagnostic, for visualization CHD was performed CT. For postnatal diagnostic CHD are used Echo and CT. CT allows graphically to see the type of CHD and predict a surgical treatment. The strategy of surgical treatment and further prognose are depend on combination of anomalies within the framework of pentalogy of Cantrell. By CT we determined atresia of the pulmonary artery with major aorto-pulmonary collateral arteries (MAPCA), ventricular and atrial septal defects.

Closed Gastroschisis: A Rare Abdominal Wall Defect

2021 ◽  
pp. 000313482110298
Author(s):  
Hannah Cockrell ◽  
Taylor Shaw ◽  
Michael W. Morris
Keyword(s):  
Prenatal Diagnosis ◽  
Abdominal Wall ◽  
Abdominal Wall Defect ◽  
Intestinal Atresia ◽  
Bowel Ischemia ◽  
Fascial Closure ◽  
Fascial Defect ◽  
Wall Defect ◽  
Emergent Operation ◽  
The Right

Gastroschisis is a rare congenital abdominal wall defect characterized by intestinal evisceration to the right of the umbilical stalk. In less than 6% of cases, the fascial defect closes around the herniated viscera in utero. The mechanism of fascial closure in these cases is unknown; however, the tourniquet effect on the mesenteric vasculature is thought to lead to intestinal atresia and midgut infarction. We report a case of a female neonate with a prenatal diagnosis of gastroschisis who was found to have a closed defect at the time of delivery. She required emergent operation for symptoms of intestinal obstruction and bowel ischemia.

Anesthesia for Gastroschisis or Omphalocele Repair

2021 ◽  
pp. 215-220
Author(s):  
Caitlin Aveyard
Keyword(s):  
Abdominal Wall ◽  
Amniotic Membrane ◽  
Chromosomal Abnormalities ◽  
Abdominal Wall Defect ◽  
Anesthetic Management ◽  
Surgical Correction ◽  
Congenital Defects ◽  
Full Thickness ◽  
Wall Defect ◽  
The Right

Gastroschisis and omphalocele are congenital defects in the abdominal wall. These two conditions have different embryologic origins, but anesthetic management is similar for both. Gastroschisis is a full-thickness abdominal wall defect resulting in extrusion of abdominal viscera into the amniotic space without amniotic membrane coverage. The defect is usually to the right of the umbilicus. Omphalocele is a defect in the abdominal wall in the umbilical area in which the extruded abdominal contents (intestine, liver, spleen, bladder) are covered in a thin sac. Infants with omphalocele often have associated syndromes or chromosomal abnormalities. With either gastroschisis or omphalocele, the extruded abdominal contents must be covered and kept moist before surgical correction.

Unusual presentation of fetus in fetu in triplet pregnancy mimicking abdominal wall defect

2015 ◽  
Vol 4 (2) ◽  
Author(s):  
Emre Erdogdu ◽  
Resul Arısoy ◽  
Pınar Kumru ◽  
Kaan Pakay ◽  
Oya Demirci ◽  
...  
Keyword(s):  
Abdominal Wall ◽  
Abdominal Wall Defect ◽  
The Other ◽  
Unusual Presentation ◽  
Differential Diagnoses ◽  
Triplet Pregnancy ◽  
Rare Form ◽  
Fetus In Fetu ◽  
Wall Defect ◽  
Unusual Condition

AbstractFetus in fetu (FIF) is a rare form of twinning in which an immature twin develops parasitically inside the other twin. The most frequent location of a parasitic fetus is the retroperitoneal region. A FIF located on the abdominal wall is an unusual condition, and it should be kept in mind as one of the differential diagnoses of abdominal wall masses.

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