Pseudocoarctation of the Aorta: A Rare Congenital Aortic Disease.

Aortic pseudocoarctation is a rare congenital aortic anomaly that causes elongation, stenosis and kinking of the aorta at the isthmus level. Although aortic coarctation and pseudocoarctation share a similar clinical spectrum, pseudocoarctation rarely results in a significant gradient in descending aorta and haemodynamic consequence. Therefore, it’s critical to differentiate in coarctation. All imaging modalities but especially cardiac CT angiography and catheterization are very important in the differential diagnosis. Our case highlighted to differences between aortic pseudocoarctation and coarctation, with other cardiac anomalies accompanying pseudocoarctation. And also the importance of cardiac imaging in the differential diagnosis of pseudocoarctation was emphasized.

Modified Aortic Uncrossing Procedure: A Novel Approach for Norwood Palliation of Complex Univentricular Congenital Heart Disease With a Circumflex Aorta

The circumflex aorta is a rare type of true vascular ring anomaly. It consists of a retroesophageal right aortic arch, a left-sided descending thoracic aorta, and a left-sided ligamentum arteriosum. The “aortic uncrossing procedure” described by Planché and Lacour-Gayet is the procedure of choice for managing this aortic anomaly in patients with a biventricular heart. The presence of a circumflex aorta in a patient with heterotaxy syndrome and univentricular congenital heart disease requiring Norwood palliation is highly unusual. We report such a case and describe our approach to its surgical management.