An Examination of the Propositus of Enhanced S-Cone Syndrome 30 Years After Diagnosis

2020 ◽  
Vol 138 (9) ◽  
pp. 1004
Author(s):  
Michael F. Marmor
Keyword(s):  
Enhanced S Cone Syndrome

Recognizable Patterns of Submacular Fibrosis in the Enhanced S-Cone Syndrome

2021 ◽  
Author(s):  
Abrar K. Alsalamah ◽  
Arif O. Khan ◽  
Abdullah Abu Bakar ◽  
Patrik Schatz ◽  
Sawsan R. Nowilaty
Keyword(s):  
Enhanced S Cone Syndrome

Management of a case of Enhanced S-cone syndrome with massive foveoschisis treated with pars plana vitrectomy with silicone oil tamponade

2021 ◽  
pp. 1-4
Author(s):  
Lorane Bechet ◽  
Raphaël Atia ◽  
Christina Zeitz ◽  
Saddek Mohand-Saïd ◽  
José-Alain Sahel ◽  
...  
Keyword(s):  
Pars Plana Vitrectomy ◽  
Silicone Oil ◽  
Pars Plana ◽  
Silicone Oil Tamponade ◽  
Enhanced S Cone Syndrome

MULTIMODAL EVIDENCE OF TYPE 3 NEOVASCULARIZATION IN ENHANCED S-CONE SYNDROME

2019 ◽  
Vol Publish Ahead of Print ◽  
Author(s):  
Ramiro S. Maldonado ◽  
Wadih M. Zein ◽  
Catherine Cukras
Keyword(s):  
Type 3 Neovascularization ◽  
Enhanced S Cone Syndrome ◽  
Type 3 ◽  
Multimodal Evidence

En Face Optical Coherence Tomography Imaging in Enhanced S-Cone Syndrome

Retina ◽  
2020 ◽  
Vol Publish Ahead of Print ◽  
Author(s):  
Manon Ortoli ◽  
Olivia Zambrowski ◽  
Alexandra Miere ◽  
Sylvie Gerber ◽  
Josseline Kaplan ◽  
...  
Keyword(s):  
Optical Coherence Tomography ◽  
Optical Coherence ◽  
Tomography Imaging ◽  
En Face ◽  
Optical Coherence Tomography Imaging ◽  
Enhanced S Cone Syndrome

scholarly journals A 5-Year-Old Case of Choroidal Neovascularization in Enhanced S-Cone Syndrome Treated with Ranibizumab

2018 ◽  
Vol 9 (3) ◽  
pp. 510-515 ◽  
Author(s):  
Federica Bertoli ◽  
Silvia Pignatto ◽  
Francesca Rizzetto ◽  
Paolo Lanzetta
Keyword(s):  
Case Report ◽  
Fluorescein Angiography ◽  
Choroidal Neovascularization ◽  
Subretinal Fluid ◽  
Intravitreal Ranibizumab ◽  
Genetic Studies ◽  
Visual Deterioration ◽  
Retinal Degenerations ◽  
The Right ◽  
Enhanced S Cone Syndrome

Introduction: We describe the youngest case of enhanced S-cone syndrome (ESCS) associated with choroidal neovascularization (CNV) successfully treated with intravitreal ranibizumab injections. Case Report: A 5-year-old boy presented with round-shaped fibrotic subretinal lesions in both eyes with surrounding subretinal fluid and progressive visual deterioration in the right eye. Fine foci of increased autofluorescence were observed along the arcades in both eyes. Fluorescein angiography revealed the presence of CNV in his right eye, and treatment with ranibizumab was initiated, with significant improvement in vision. Subsequent electroretinogram examination and genetic studies of the patient and his two younger siblings confirmed the diagnosis of ESCS. Conclusion: CNV has been reported to occur in different inherited retinal degenerations, including ESCS. Our experience confirms that treatment with ranibizumab in patients with CNV-complicated ESCS can be potentially vision-saving.

Enhanced S-cone syndrome with subfoveal neovascularization

2002 ◽  
Vol 133 (4) ◽  
pp. 575-577 ◽  
Author(s):  
Makoto Nakamura ◽  
Yoshihiro Hotta ◽  
Chang-Hua Piao ◽  
Mineo Kondo ◽  
Hiroko Terasaki ◽  
...  
Keyword(s):  
Enhanced S Cone Syndrome

scholarly journals Incidence and Natural History of Retinochoroidal Neovascularization in Enhanced S-Cone Syndrome

2021 ◽  
Vol 222 ◽  
pp. 174-184
Author(s):  
Sawsan R. Nowilaty ◽  
Abrar K. Alsalamah ◽  
Moustafa S. Magliyah ◽  
Abdulelah A. Alabdullah ◽  
Khabir Ahmad ◽  
...  
Keyword(s):  
Natural History ◽  
History Of ◽  
Enhanced S Cone Syndrome

scholarly journals ISCEV extended protocol for the S-cone ERG

2019 ◽  
Vol 140 (2) ◽  
pp. 95-101 ◽  
Author(s):  
Ido Perlman ◽  
Mineo Kondo ◽  
Enid Chelva ◽  
Anthony G. Robson ◽  
Graham E. Holder
Keyword(s):  
Short Wavelength ◽  
Retinal Function ◽  
Clinical Electrophysiology ◽  
Full Field ◽  
Standard Testing ◽  
Cell Dysfunction ◽  
Retinal Disorders ◽  
Iscev Standard ◽  
Enhanced S Cone Syndrome

AbstractThe International Society for Clinical Electrophysiology of Vision (ISCEV) standard for full-field electroretinography (ERG) describes a minimum procedure for testing generalized retinal function but encourages more extensive testing. This extended protocol describes a method of assessing the function of the short-wavelength-sensitive cone (S-cone) retinal pathway, using a short-wavelength flash superimposed on a background that saturates the rods and adapts the L/M-cones to elicit a response, known as the S-cone ERG. Stimulus parameters such as the strength and luminance of the flash and background, respectively, and their spectral and temporal characteristics are specified. As a complement to the ISCEV standard, testing the S-cone ERG enables further characterization of light-adapted retinal function and may refine diagnosis of some retinal disorders. Typical applications are described including use in the diagnosis of rod monochromacy and S-cone monochromacy, identification and investigation of cone On-bipolar cell dysfunction and use of the technique to confirm the diagnosis of enhanced S-cone syndrome.

scholarly journals The Enhanced S Cone Syndrome: An Analysis of Receptoral and Post-receptoral Changes

1996 ◽  
Vol 36 (22) ◽  
pp. 3711-3722 ◽  
Author(s):  
VIVIENNE C GREENSTEIN ◽  
QASIM ZAIDI ◽  
DONALD C HOOD ◽  
BRANKA SPEHAR ◽  
ARTUR V CIDECIYAN ◽  
...  
Keyword(s):  
Enhanced S Cone Syndrome
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