Endovascular stent implantation in a coronary artery to pulmonary artery fistula in a patient with pulmonary atresia with ventricular septal defect and severe cyanosis

AbstractPulmonary atresia and ventricular septal defect is associated with variable sources of pulmonary blood supply. We present a case of a coronary artery to pulmonary artery collateral as the principal source of pulmonary blood supply.

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Coronary artery–pulmonary artery fistula in pulmonary atresia with ventricular septal defect: report of two surgical cases

Cardiology in the Young ◽

10.1017/s1047951121003796 ◽

2021 ◽

pp. 1-4

Author(s):

Arif Yasin Çakmak ◽

Ilker Kemal Yucel ◽

Ahmet Sasmazel

Keyword(s):

Coronary Artery ◽

Pulmonary Artery ◽

Septal Defect ◽

Left Main Coronary Artery ◽

Ductus Arteriosus ◽

Pulmonary Atresia ◽

Left Main ◽

Aortopulmonary Collateral ◽

The Right ◽

Pulmonary Artery Fistula

Abstract Pulmonary atresia with ventricular septal defect is a complex congenital cardiac anomaly. The blood is supplied to the lungs through a patent ductus arteriosus, a major aortopulmonary collateral artery, or in very rare cases from a coronary artery–pulmonary artery fistula. We present two cases with coronary artery–pulmonary artery fistula which underwent surgical intervention. In our first patient, the main pulmonary artery was supplied from the left main coronary artery. In the second patient, the right pulmonary artery originated from the left main coronary artery and continued to the right lung posteriorly to the aorta, while the left pulmonary artery originated from the patent ductus arteriosus. The difference in our cases is that the coronary artery pulmonary artery fistulas behave like major aortopulmonary collateral arteries originating from the coronary arteries. These fistulas were the main source of pulmonary blood flow.

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Prenatal diagnosis of fetal coronary pulmonary artery fistula with pulmonary atresia and ventricular septal defect

10.22541/au.160071098.80134579 ◽

2020 ◽

Author(s):

Ryo Ishii ◽

Hidekazu Ishida ◽

Fumiko Torigoe ◽

Jun Narita ◽

Keiichi Ozono

Keyword(s):

Prenatal Diagnosis ◽

Ventricular Septal Defect ◽

Pulmonary Artery ◽

Septal Defect ◽

Pulmonary Atresia ◽

Pulmonary Artery Fistula

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Pulmonary Atresia, VSD in Association with Coronary-Pulmonary Artery Fistula

Asian Cardiovascular and Thoracic Annals ◽

10.1177/021849230701500415 ◽

2007 ◽

Vol 15 (4) ◽

pp. 335-338 ◽

Cited By ~ 6

Author(s):

Hani K Najm ◽

Neerod K Jha ◽

Michael Godman ◽

Mansour Al Mutairi ◽

Ahmed I Rezk ◽

...

Keyword(s):

Ventricular Septal Defect ◽

Pulmonary Artery ◽

Septal Defect ◽

Pulmonary Arteries ◽

Pulmonary Atresia ◽

Left Pulmonary Artery ◽

Corrective Surgery ◽

Aortopulmonary Collaterals ◽

One Year ◽

Pulmonary Artery Fistula

Congenital coronary-pulmonary artery fistula is rare in patients with pulmonary atresia and ventricular septal defect. The nomenclature, physiological, clinical, and surgical implications of these fistulas are yet to be defined. We report a one-year-old child with pulmonary atresia, ventricular septal defect, and a right coronary-pulmonary artery fistula who also had a diminutive, disconnected left pulmonary artery in addition to aortopulmonary collaterals. The patient underwent corrective surgery. However, the fate of diminutive pulmonary arteries is unknown. The literature was reviewed to explore the clinical or surgical implications of such fistulas for improved understanding and management in the future.

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