Basal Encephalocele | ScienceGate

Morning Glory Syndrome is a very rare condition. It is characterized by an enlarged and funnel-shaped optic disc excavated and is associated with other craniofacial anomalies such as hypertelorism, cleft lip, cleft palate, and basal encephalocele. CaseReport. A case of a 30 year-old man who came for neurosurgical evaluation after a magnetic resonance imaging (MRI) scan that showed spheno-ethmoidal encephalocele is reported. Conclusions. There is a high association between basal encephalocele,midface abnormalities and Morning Glory Syndrome. A neurosurgical, ophtalmological and endocrinological evaluation must always be done. The patients present with ophtalmic signs and/or strabismus or poor vision. An image study should always be performed to delineate the extent of the lesion and a complete hormone screening should be carried out to exclude pituitary deficiency.

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Endoscopic Endonasal Skull Base Approach for Treatment of a Basal Encephalocele in a Patient with Morning Glory Syndrome

Skull Base ◽

10.1055/s-2009-1242397 ◽

2009 ◽

Vol 19 (03) ◽

Author(s):

Michael Lemole ◽

Stephanie Joe

Keyword(s):

Skull Base ◽

Morning Glory ◽

Endoscopic Endonasal ◽

Base Approach ◽

Morning Glory Syndrome ◽

Basal Encephalocele ◽

Skull Base Approach

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A rare case of upper airway obstruction in an infant caused by basal encephalocele complicating facial midline deformity

Pediatric Anesthesia ◽

10.1046/j.1460-9592.1999.9120288.x ◽

1999 ◽

Vol 9 (1) ◽

pp. 73-76 ◽

Cited By ~ 2

Author(s):

TOMOAKI SHIMIZU ◽

SEIJI KITAMURA ◽

KEIKO KINOUCHI ◽

KAZUO FUKUMITSU

Keyword(s):

Airway Obstruction ◽

Rare Case ◽

Upper Airway ◽

Upper Airway Obstruction ◽

Basal Encephalocele ◽

Facial Midline

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Acquired Anterior Basal Encephalocele in Idiopathic Hypertrophic Pachymeningitis

The Neuroradiology Journal ◽

10.1177/197140090802100606 ◽

2008 ◽

Vol 21 (6) ◽

pp. 791-794 ◽

Cited By ~ 3

Author(s):

C. Singh ◽

C. Kesavadas ◽

M.D. Nair ◽

C. Sarada

Keyword(s):

Intracranial Pressure ◽

Sinus Thrombosis ◽

Cribriform Plate ◽

Dural Sinus ◽

Raised Intracranial Pressure ◽

Elevated Intracranial Pressure ◽

Dural Sinus Thrombosis ◽

Hypertrophic Pachymeningitis ◽

Ethmoid Bone ◽

Basal Encephalocele

This report describes a 49-year-old woman diagnosed as idiopathic hypertrophic pachymeningitis (IHCPM) with imaging evidence of diffuse dural sinus thrombosis. Over the years, secondary to the raised intracranial pressure, she had developed an anterior basal encephalocele through the defects in the cribriform plate of the ethmoid bone. The relation between elevated intracranial pressure and encephalocele is discussed.

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