Long-term outcomes in children with Hirschsprung’s disease and transition zone bowel pull-through: impact of surgical techniques and role for conservative approach

2021 ◽  
Author(s):  
Gowri Shankar ◽  
J. G. Deepak ◽  
Vinay Jadhav ◽  
K. Venkatesh ◽  
Usha Kini ◽  
...  
Keyword(s):  
Transition Zone ◽  
Hirschsprung's Disease ◽  
Hirschsprung’S Disease ◽  
Surgical Techniques ◽  
Conservative Approach ◽  
Long Term Outcomes ◽  
Pull Through

Long-Term Outcomes and Quality of Life in Patients after Soave Pull-Through Operation for Hirschsprung's Disease: An Observational Retrospective Study

2017 ◽  
Vol 28 (05) ◽  
pp. 445-454 ◽  
Author(s):  
Tania Mahler ◽  
Martine Dassonville ◽  
Dinh Truong ◽  
Annie Robert ◽  
Philippe Goyens ◽  
...  
Keyword(s):  
Quality Of Life ◽  
Fecal Incontinence ◽  
Hirschsprung's Disease ◽  
Hirschsprung’S Disease ◽  
Bowel Function ◽  
Long Term Outcomes ◽  
Neurologic Impairment ◽  
Pull Through

Introduction Patients after pull-through operation for Hirschsprung's disease (HD) are at high risk of defecation disorders. This study aimed at investigating their long-term outcomes and quality of life (QoL) in comparison with controls. Patients and Methods Patients older than 5 years operated on for HD were interviewed to complete detailed questionnaires on bowel function. Patients without neurologic impairment were enrolled in a QoL survey to compare with controls matched for sex and age and selected randomly from the general population using sampling set in a ratio of four controls to one case of HD. Results In total, 53 operated patients were enrolled. Mean age of the patients was 16 ± 8 years, with 68% boys. Rectosigmoid aganglionosis was the most seen form of HD in 38 (72%) cases. Open Soave was performed in 40 (75.5%) cases, and minimally invasive surgery Soave (MIS Soave) in 13 (24.5%) cases. At investigation, prevalence of fecal incontinence and constipation were 22.6 and 13.2%, respectively. Regarding QoL survey, 45 patients and 180 controls were enrolled, excluding 8 patients with neurologic impairment. Thirty-seven (82.2%) patients were classified as having a good QoL (score ≥ 9 points); whereas six had a fair QoL (5–8 points) and two had a poor QoL (< 5 points). QoL score in the cases and the controls were 10.2 ± 2.5 and 11.9 ± 0.4 points, respectively. Long aganglionosis form of HD was significantly associated with a low QoL (score < 8 points), adjusted odds ratio = 9, 95% confidence interval [1.3; 64.1] (p < 0.05). In subscales analyses, the prevalence of each dimension including fecal continence, school absenteeism, unhappiness or anxiety, food restriction, and peer rejection was significantly higher in operated patients than in controls (p <0.001). Conclusion Although the QoL of patients operated on for HD in general was with good outcomes, fecal incontinence and constipation still are problematic issues and challenges in a high percentage of patients. Therefore, a long-term and multidisciplinary follow-up is essentially required for these patients.

Colonoscopy as a useful tool in determining the transition zone in transanal endorectal pull-through in Hirschsprung’s disease

2012 ◽  
Vol 27 (11) ◽  
pp. 1547-1548 ◽  
Author(s):  
Pedro Luiz Toledo de Arruda Lourenção ◽  
Érika Veruska Paiva Ortolan ◽  
Rozemeire Garcia Marques ◽  
Felipe Gilberto Valerini ◽  
Maria Aparecida Marchesan Rodrigues ◽  
...  
Keyword(s):  
Transition Zone ◽  
Hirschsprung's Disease ◽  
Hirschsprung’S Disease ◽  
Pull Through

Long-term outcomes of Hirschsprung's disease

2012 ◽  
Vol 21 (4) ◽  
pp. 336-343 ◽  
Author(s):  
Risto J. Rintala ◽  
Mikko P. Pakarinen
Keyword(s):  
Hirschsprung's Disease ◽  
Hirschsprung’S Disease ◽  
Long Term Outcomes

Sa1600 Colonoscopy As a New Tool in Determining the Transition Zone in Endoanal Pull-Through in Hirschsprung's Disease - Preliminary Results

2011 ◽  
Vol 73 (4) ◽  
pp. AB220
Author(s):  
Erika P. Ortolan ◽  
Pedro L. Lourenção ◽  
Gisele O. Orsi ◽  
Bonifácio K. Takegawa
Keyword(s):  
Transition Zone ◽  
Hirschsprung's Disease ◽  
Hirschsprung’S Disease ◽  
Preliminary Results ◽  
Pull Through
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