Robotic Soave pull-through procedure for Hirschsprung’s disease in children under 12-months: long-term outcomes

2021 ◽  
Author(s):  
Carlos Delgado-Miguel ◽  
Juan I. Camps
Keyword(s):  
Hirschsprung's Disease ◽  
Hirschsprung’S Disease ◽  
Long Term Outcomes ◽  
Pull Through

Long-Term Outcomes and Quality of Life in Patients after Soave Pull-Through Operation for Hirschsprung's Disease: An Observational Retrospective Study

2017 ◽  
Vol 28 (05) ◽  
pp. 445-454 ◽  
Author(s):  
Tania Mahler ◽  
Martine Dassonville ◽  
Dinh Truong ◽  
Annie Robert ◽  
Philippe Goyens ◽  
...  
Keyword(s):  
Quality Of Life ◽  
Fecal Incontinence ◽  
Hirschsprung's Disease ◽  
Hirschsprung’S Disease ◽  
Bowel Function ◽  
Long Term Outcomes ◽  
Neurologic Impairment ◽  
Pull Through

Introduction Patients after pull-through operation for Hirschsprung's disease (HD) are at high risk of defecation disorders. This study aimed at investigating their long-term outcomes and quality of life (QoL) in comparison with controls. Patients and Methods Patients older than 5 years operated on for HD were interviewed to complete detailed questionnaires on bowel function. Patients without neurologic impairment were enrolled in a QoL survey to compare with controls matched for sex and age and selected randomly from the general population using sampling set in a ratio of four controls to one case of HD. Results In total, 53 operated patients were enrolled. Mean age of the patients was 16 ± 8 years, with 68% boys. Rectosigmoid aganglionosis was the most seen form of HD in 38 (72%) cases. Open Soave was performed in 40 (75.5%) cases, and minimally invasive surgery Soave (MIS Soave) in 13 (24.5%) cases. At investigation, prevalence of fecal incontinence and constipation were 22.6 and 13.2%, respectively. Regarding QoL survey, 45 patients and 180 controls were enrolled, excluding 8 patients with neurologic impairment. Thirty-seven (82.2%) patients were classified as having a good QoL (score ≥ 9 points); whereas six had a fair QoL (5–8 points) and two had a poor QoL (< 5 points). QoL score in the cases and the controls were 10.2 ± 2.5 and 11.9 ± 0.4 points, respectively. Long aganglionosis form of HD was significantly associated with a low QoL (score < 8 points), adjusted odds ratio = 9, 95% confidence interval [1.3; 64.1] (p < 0.05). In subscales analyses, the prevalence of each dimension including fecal continence, school absenteeism, unhappiness or anxiety, food restriction, and peer rejection was significantly higher in operated patients than in controls (p <0.001). Conclusion Although the QoL of patients operated on for HD in general was with good outcomes, fecal incontinence and constipation still are problematic issues and challenges in a high percentage of patients. Therefore, a long-term and multidisciplinary follow-up is essentially required for these patients.

Long-term outcomes of Hirschsprung's disease

2012 ◽  
Vol 21 (4) ◽  
pp. 336-343 ◽  
Author(s):  
Risto J. Rintala ◽  
Mikko P. Pakarinen
Keyword(s):  
Hirschsprung's Disease ◽  
Hirschsprung’S Disease ◽  
Long Term Outcomes

The impact of Down’s syndrome on the immediate and long-term outcomes of children with Hirschsprung’s disease

2005 ◽  
Vol 22 (2) ◽  
pp. 179-181 ◽  
Author(s):  
Antonino Morabito ◽  
Anupam Lall ◽  
Sobbia Gull ◽  
Amar Mohee ◽  
Adrian Bianchi
Keyword(s):  
Hirschsprung's Disease ◽  
Hirschsprung’S Disease ◽  
Down's Syndrome ◽  
Down’S Syndrome ◽  
Long Term Outcomes ◽  
The Impact
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