Sudden cardiac arrest during adenotonsillectomy in a patient with subclinical Duchenne's muscular dystrophy

1994 ◽  
Vol 28 (2-3) ◽  
pp. 261
Keyword(s):  
Cardiac Arrest ◽  
Muscular Dystrophy ◽  
Sudden Cardiac Arrest ◽  
Duchenne's Muscular Dystrophy

Sudden Cardiac Arrest during Adenotonsillectomy in a Patient with Subclinical Duchenne's Muscular Dystrophy

1993 ◽  
Vol 72 (2) ◽  
pp. 130-131 ◽  
Author(s):  
Nick C. Benton ◽  
Robert A. Wolgat
Keyword(s):  
Cardiac Arrest ◽  
Muscular Dystrophy ◽  
General Anesthesia ◽  
Case Reports ◽  
Sudden Cardiac Arrest ◽  
Elevated Serum ◽  
Serum Creatine Kinase ◽  
Strong Family History ◽  
History Of ◽  
Duchenne's Muscular Dystrophy

We describe a four-year-old boy of Indian descent who had elective adenotonsillectomy for chronic sore throat and partial airway obstruction. About 10 minutes into the procedure, the patient suddenly developed cardiac asystole. After prolonged cardiac resuscitation, recovery was achieved. No permanent neurologic deficits resulted. The child was later found to have a strong family history of Duchenne's muscular dystrophy (DMD) and an elevated serum creatine kinase level documented since shortly after birth. We reviewed several case reports substantiating the risk for cardiac arrest during general anesthesia in DMD patients, and we concluded that DMD is a little-known risk for cardiac arrest during general anesthesia. The otolaryngologist must be aware of this potential complication, because tonsillectomy and adenoidectomy are commonly indicated for children at an age when DMD may be subclinical.

scholarly journals Duchenne Muscular Dystrophy (DMD) with Severe Cardiomyopathy

2018 ◽  
Vol 6 (2) ◽  
Author(s):  
Ji Hyoung Park ◽  
Kwang Ho Lee ◽  
Wi Kwang Wang ◽  
Hyun Kyo Lim
Keyword(s):  
Heart Rate ◽  
Cardiac Arrest ◽  
Mental Retardation ◽  
Duchenne Muscular Dystrophy ◽  
Muscular Dystrophy ◽  
Sudden Cardiac Arrest ◽  
Proper Function ◽  
Organ Perfusion ◽  
Severe Mental Retardation ◽  
Successful Resuscitation

Duchenne muscular dystrophy (DMD) is a progressive myopathy. The development of respiratory therapy has increased the life expectancy of DMD patients. This change has increased the chances of anesthesia administration in DMD patients with advanced cardiomyopathy. We report a severe cardiomyopathy case in a 14-year-old boy with DMD, adrenal insufficiency, and severe mental retardation, who experienced a sudden cardiac arrest with successful resuscitation. The patient underwent feeding gastrostomy surgery to relieve recurrent aspiration pneumonia, during which cardiac index and heart rate decreased. Cardiomyopathy has emerged as a new challenge in DMD patients; it is important to maintain end organ perfusion by proper function of the left ventricle.

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