Pulmonary atresia with intact ventricular septum and right ventricular dependent coronary circulation through the “vessels of Wearn”

2013 ◽  
Vol 22 (4) ◽  
pp. 298-302 ◽  
Author(s):  
Atif Ali Ahmed ◽  
Brett Thomas Snodgrass ◽  
Stephen Kaine
Keyword(s):  
Right Ventricular ◽  
Coronary Circulation ◽  
Pulmonary Atresia ◽  
Ventricular Septum ◽  
Intact Ventricular Septum

A most peculiar coronary circulation in a patient with pulmonary atresia and intact ventricular septum

2000 ◽  
Vol 10 (1) ◽  
pp. 60-63 ◽  
Author(s):  
Robert M. Freedom ◽  
Shi-Joon Yoo ◽  
Alexander Javois
Keyword(s):  
Left Ventricular Function ◽  
Right Ventricular ◽  
Coronary Arteries ◽  
Coronary Circulation ◽  
Pulmonary Atresia ◽  
Left Ventricular ◽  
Ventricular Septum ◽  
Intact Ventricular Septum ◽  
Descending Thoracic Aorta ◽  
Collateral Vessel

AbstractA patient with pulmonary atresia and intact ventricular septum was found to have a right ventricular-dependent coronary circulation. In this infant both coronary arteries lacked their normal proximal connection with the aorta, perhaps the most egregious form of this prejudicial coronary circulation. Even more interesting was a direct collateral vessel originating from the descending thoracic aorta and connecting with the coronary circulation. This patient has undergone bilateral modified Blalock-Taussig shunts, and left ventricular function seems preserved.

Total right ventricular dependent coronary circulation in pulmonary atresia with intact ventricular septum

2004 ◽  
Vol 77 (3) ◽  
pp. 1087-1088 ◽  
Author(s):  
Paul Lajos ◽  
Jon Love ◽  
Mubadda A Salim ◽  
Wenle Wang ◽  
Marcelo G Cardarelli
Keyword(s):  
Right Ventricular ◽  
Coronary Circulation ◽  
Pulmonary Atresia ◽  
Ventricular Septum ◽  
Intact Ventricular Septum

Acquired ventricular septal aneurysm in a patient with pulmonary atresia with intact ventricular septum

2011 ◽  
Vol 22 (2) ◽  
pp. 227-229 ◽  
Author(s):  
Akash R. Patel ◽  
Paul Farrell ◽  
Matthew Harris ◽  
J. William Gaynor ◽  
Matthew J. Gillespie
Keyword(s):  
Right Ventricular ◽  
Myocardial Ischaemia ◽  
Coronary Circulation ◽  
Pulmonary Atresia ◽  
Interesting Case ◽  
Ventricular Septum ◽  
Intact Ventricular Septum

AbstractMyocardial ischaemia and infarction in pulmonary atresia and intact ventricular septum with right ventricular-dependent coronary circulation is a well-established complication. We report an interesting case of an acquired aneurysm in the ventricular septum in a patient who underwent staged palliation.

Pulmonary atresia with intact ventricular septum: Is it possible to improve survival?

1992 ◽  
Vol 2 (4) ◽  
pp. 391-394 ◽  
Author(s):  
Carlo Vosa ◽  
Paolo Arciprete ◽  
Giuseppe Caianiello ◽  
Gaetano Palma
Keyword(s):  
Right Ventricular ◽  
Pulmonary Atresia ◽  
Right Ventricular Outflow Tract ◽  
Ventricular Outflow Tract ◽  
Outflow Tract ◽  
Ventricular Septum ◽  
Intact Ventricular Septum ◽  
Shunt Procedure ◽  
The Right ◽  
Overall Mortality

SummaryBetween February 1986 and December 1991, 41 patients with pulmonary atresia and intact ventricular septum were treated in our institution following a multistage protocol of management. In all cases, the first step was to construct a right modified Blalock-Taussig shunt during the neonatal period regardless of the right ventricular anatomy. Then, in patients with well-developed right ventricles possessing all three components, we proceeded to early surgical repair. In contrast, in patients with right ventricles having obliteration of some components, yet deemed to be recoverable, the next step was to provide palliative relief of obstruction in the right ventricular outflow tract followed, if possible, by subsequent repair. Fontan's operation was performed in patients with right ventricles considered unsuitable from the outset to support the pulmonary circulation. Only one patient died following the initial shunt procedure (mortality of 2.43%). The subsequent program of treatment has now been concluded in 22 patients. In all those deemed to have favorable native anatomy (10 cases), the subsequent complete repair was successful. Among the 24 patients who required palliation of the outflow tract, five died while total repair was subsequently performed in eight. Fontan's operation was performed without mortality in five patients with small right ventricles, although one patient died while waiting for surgery. In all, 89 procedures were performed with an overall mortality of 14%.

Sign in / Sign up

Export Citation Format

Share Document