G.P.14.06 There is no correlation between muscle strength and myotonia in patients with myotonic dystrophy type 1

2007 ◽  
Vol 17 (9-10) ◽  
pp. 855-856
Author(s):  
N. Preisler ◽  
M. Cathrine Orngreen ◽  
G. Andersen ◽  
T. Dysgaard Jeppesen ◽  
E. Colding-Jorgensen ◽  
...  
Keyword(s):  
Muscle Strength ◽  
Myotonic Dystrophy ◽  
Myotonic Dystrophy Type 1 ◽  
Myotonic Dystrophy Type

scholarly journals Targeting DMPK with Antisense Oligonucleotide Improves Muscle Strength in Myotonic Dystrophy Type 1 Mice

2017 ◽  
Vol 7 ◽  
pp. 465-474 ◽  
Author(s):  
Dominic Jauvin ◽  
Jessina Chrétien ◽  
Sanjay K. Pandey ◽  
Laurie Martineau ◽  
Lucille Revillod ◽  
...  
Keyword(s):  
Muscle Strength ◽  
Myotonic Dystrophy ◽  
Antisense Oligonucleotide ◽  
Myotonic Dystrophy Type 1 ◽  
Myotonic Dystrophy Type

A 9-year follow-up study of quantitative muscle strength changes in myotonic dystrophy type 1

2018 ◽  
Vol 265 (7) ◽  
pp. 1698-1705 ◽  
Author(s):  
Cynthia Gagnon ◽  
Émilie Petitclerc ◽  
Marie Kierkegaard ◽  
Jean Mathieu ◽  
Élise Duchesne ◽  
...  
Keyword(s):  
Muscle Strength ◽  
Myotonic Dystrophy ◽  
Myotonic Dystrophy Type 1 ◽  
Myotonic Dystrophy Type ◽  
Follow Up Study

Creatine monohydrate supplementation does not increase muscle strength, lean body mass, or muscle phosphocreatine in patients with myotonic dystrophy type 1

2003 ◽  
Vol 29 (1) ◽  
pp. 51-58 ◽  
Author(s):  
Mark Tarnopolsky ◽  
Douglas Mahoney ◽  
Terry Thompson ◽  
Heather Naylor ◽  
Timothy J. Doherty
Keyword(s):  
Muscle Strength ◽  
Myotonic Dystrophy ◽  
Lean Body Mass ◽  
Body Mass ◽  
Creatine Monohydrate ◽  
Myotonic Dystrophy Type 1 ◽  
Myotonic Dystrophy Type

Lower limb muscle strength impairment in late-onset and adult myotonic dystrophy type 1 phenotypes

2016 ◽  
Vol 56 (1) ◽  
pp. 57-63 ◽  
Author(s):  
Émilie Petitclerc ◽  
Luc J. Hébert ◽  
Jean Mathieu ◽  
Johanne Desrosiers ◽  
Cynthia Gagnon
Keyword(s):  
Muscle Strength ◽  
Myotonic Dystrophy ◽  
Lower Limb ◽  
Late Onset ◽  
Myotonic Dystrophy Type 1 ◽  
Lower Limb Muscle ◽  
Myotonic Dystrophy Type ◽  
Limb Muscle

scholarly journals Is muscle strength related to spatiotemporal gait parameters in adults with myotonic dystrophy type 1?

2018 ◽  
Vol 61 ◽  
pp. e167
Author(s):  
M. Harvey ◽  
M. Gosselin ◽  
M. Vocos ◽  
A.S. Comtois ◽  
L.N. Veilleux ◽  
...  
Keyword(s):  
Muscle Strength ◽  
Myotonic Dystrophy ◽  
Myotonic Dystrophy Type 1 ◽  
Myotonic Dystrophy Type ◽  
Gait Parameters

P.30Reliability of balance, function, and muscle strength measures in myotonic dystrophy type 1

2019 ◽  
Vol 29 ◽  
pp. S50
Author(s):  
K. Knak ◽  
A. Sheikh ◽  
H. Andersen ◽  
N. Witting ◽  
J. Vissing
Keyword(s):  
Muscle Strength ◽  
Myotonic Dystrophy ◽  
Myotonic Dystrophy Type 1 ◽  
Balance Function ◽  
Myotonic Dystrophy Type

Intrarater reliability and validity of outcome measures in myotonic dystrophy type 1

Neurology ◽  
2020 ◽  
Vol 94 (24) ◽  
pp. e2508-e2520
Author(s):  
Kirsten L. Knak ◽  
Aisha M. Sheikh ◽  
Henning Andersen ◽  
Nanna Witting ◽  
John Vissing
Keyword(s):  
Muscle Strength ◽  
Myotonic Dystrophy ◽  
Dynamic Balance ◽  
Reliability And Validity ◽  
Functional Mobility ◽  
Myotonic Dystrophy Type 1 ◽  
Myotonic Dystrophy Type ◽  
Intrarater Reliability ◽  
Balance Tests

ObjectiveTo investigate intrarater reliability and concurrent and construct validity of muscle strength, balance, and functional mobility measures in individuals with noncongenital myotonic dystrophy type 1 (DM1).MethodsSeventy-eight adults with noncongenital DM1 participated in visit 1, and 73 of the them participated in visit 2 separated by 1 to 2 weeks. The assessments consisted of muscle strength tests with handheld dynamometry (HHD) and stationary dynamometry in the lower limb. The balance tests consisted of the step test, Timed Up and Go test, feet-together stance, tandem stance, 1-leg stance, and modified Clinical Test of Sensory Integration and Balance on a balance platform. The functional mobility tests consisted of the 10-m walk test (10mWT) and 10-times Sit-to-Stand test.ResultsThe HHD and stationary dynamometry had sufficient intrarater reliability for most muscle groups on a group (SEM% ≤15%) and individual (minimal detectable difference [MDD95%] ≤30%) level, but the HHD was most reliable. Stationary dynamometry measured a higher torque than HHD for all extensor muscles, but for single individuals, none of the devices were favored. Overall, intrarater reliability and validity were sufficient only for the dynamic balance tests, not the static balance tests. Both functional mobility tests were sufficiently reliable and valid, but the 10mWT was most reliable.ConclusionOverall, HHD is recommended as a reliable and valid tool for single individuals and for flexor muscles on a group level. For balance assessments, the dynamic balance tests are recommended as the most valid and reliable balance tests. Both functional mobility tests are recommended for valid and reliable outcomes, but the 10mWT was superior for reliability.

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