389. Engineered microRNAs Against a C9ORF72 Transgenic Mouse Model To Treat Human Familial Amyotrophic Lateral Sclerosis (FALS)

Molecular Therapy ◽

10.1016/s1525-0016(16)35402-8 ◽

2014 ◽

Vol 22 ◽

pp. S148

Keyword(s):

Amyotrophic Lateral Sclerosis ◽

Mouse Model ◽

Transgenic Mouse ◽

Transgenic Mouse Model ◽

Familial Amyotrophic Lateral Sclerosis ◽

Lateral Sclerosis

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Transgenic mouse model for familial amyotrophic lateral sclerosis with superoxide dismutase-1 mutation

Neuropathology ◽

10.1046/j.1440-1789.2001.00361.x ◽

2001 ◽

Vol 21 (1) ◽

pp. 82-92 ◽

Author(s):

Noriyuki Shibata

Keyword(s):

Amyotrophic Lateral Sclerosis ◽

Superoxide Dismutase ◽

Mouse Model ◽

Transgenic Mouse ◽

Transgenic Mouse Model ◽

Familial Amyotrophic Lateral Sclerosis ◽

Superoxide Dismutase 1 ◽

Lateral Sclerosis

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Bax and Bcl-2 Interaction in a Transgenic Mouse Model of Familial Amyotrophic Lateral Sclerosis

Journal of Neurochemistry ◽

10.1046/j.1471-4159.1999.0732460.x ◽

2002 ◽

Vol 73 (6) ◽

pp. 2460-2468 ◽

Author(s):

Slobodanka Vukosavic ◽

Michel Dubois-Dauphin ◽

Norma Romero ◽

Serge Przedborski

Keyword(s):

Amyotrophic Lateral Sclerosis ◽

Mouse Model ◽

Transgenic Mouse ◽

Transgenic Mouse Model ◽

Familial Amyotrophic Lateral Sclerosis ◽

Lateral Sclerosis

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Light therapy and supplementary riboflavin in the SOD1 transgenic mouse model of familial amyotrophic lateral sclerosis (FALS)

Lasers in Surgery and Medicine ◽

10.1002/lsm.20732 ◽

2009 ◽

Vol 41 (1) ◽

pp. 52-59 ◽

Author(s):

Helina Moges ◽

Olavo M. Vasconcelos ◽

William W. Campbell ◽

Rosemary C. Borke ◽

Jennifer Anne McCoy ◽

...

Keyword(s):

Amyotrophic Lateral Sclerosis ◽

Mouse Model ◽

Transgenic Mouse ◽

Light Therapy ◽

Transgenic Mouse Model ◽

Familial Amyotrophic Lateral Sclerosis ◽

Lateral Sclerosis

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Neuromuscular accumulation of mutant superoxide dismutase 1 aggregates in a transgenic mouse model of familial amyotrophic lateral sclerosis

Neuroscience Letters ◽

10.1016/s0304-3940(03)00893-0 ◽

2003 ◽

Vol 350 (2) ◽

pp. 132-136 ◽

Author(s):

Bradley J. Turner ◽

Elizabeth C. Lopes ◽

Surindar S. Cheema

Keyword(s):

Amyotrophic Lateral Sclerosis ◽

Superoxide Dismutase ◽

Mouse Model ◽

Transgenic Mouse ◽

Transgenic Mouse Model ◽

Familial Amyotrophic Lateral Sclerosis ◽

Superoxide Dismutase 1 ◽

Lateral Sclerosis

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Lack of involvement of neuronal nitric oxide synthase in the pathogenesis of a transgenic mouse model of familial amyotrophic lateral sclerosis

Neuroscience ◽

10.1016/s0306-4522(98)00492-8 ◽

1999 ◽

Vol 90 (4) ◽

pp. 1483-1492 ◽

Author(s):

F. Facchinetti ◽

M. Sasaki ◽

F.B. Cutting ◽

J.E. Macdonald ◽

D. Reif ◽

...

Keyword(s):

Nitric Oxide ◽

Amyotrophic Lateral Sclerosis ◽

Nitric Oxide Synthase ◽

Mouse Model ◽

Transgenic Mouse ◽

Neuronal Nitric Oxide Synthase ◽

Transgenic Mouse Model ◽

Familial Amyotrophic Lateral Sclerosis ◽

Oxide Synthase ◽

Lateral Sclerosis

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Degeneration of corticospinal and bulbospinal systems in the superoxide dismutase 1G93A G1H transgenic mouse model of familial amyotrophic lateral sclerosis

Neuroscience Letters ◽

10.1016/s0304-3940(02)00944-8 ◽

2002 ◽

Vol 332 (2) ◽

pp. 99-102 ◽

Author(s):

D.W. Zang ◽

S.S. Cheema

Keyword(s):

Amyotrophic Lateral Sclerosis ◽

Superoxide Dismutase ◽

Mouse Model ◽

Transgenic Mouse ◽

Transgenic Mouse Model ◽

Familial Amyotrophic Lateral Sclerosis ◽

Lateral Sclerosis

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Numerical simulation of motor neuron excitability in a transgenic mouse model of familial amyotrophic lateral sclerosis

Modelling in Medicine and Biology VI ◽

10.2495/bio050221 ◽

2005 ◽

Author(s):

N. Marzocchi ◽

S. Severi ◽

M. Pieri ◽

C. Zona ◽

S. Cavalcanti

Keyword(s):

Numerical Simulation ◽

Amyotrophic Lateral Sclerosis ◽

Mouse Model ◽

Motor Neuron ◽

Transgenic Mouse ◽

Transgenic Mouse Model ◽

Familial Amyotrophic Lateral Sclerosis ◽

Neuron Excitability ◽

Motor Neuron Excitability ◽

Lateral Sclerosis

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Midbrain dopaminergic neuronal degeneration in a transgenic mouse model of familial amyotrophic lateral sclerosis

Annals of Neurology ◽

10.1002/ana.410410413 ◽

1997 ◽

Vol 41 (4) ◽

pp. 497-504 ◽

Author(s):

V. Kostic ◽

M. E. Gurney ◽

H.-X. Deng ◽

T. Siddique ◽

C. J. Epstein ◽

...

Keyword(s):

Amyotrophic Lateral Sclerosis ◽

Mouse Model ◽

Transgenic Mouse ◽

Neuronal Degeneration ◽

Transgenic Mouse Model ◽

Familial Amyotrophic Lateral Sclerosis ◽

Lateral Sclerosis

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Protein Oxidative Damage in a Transgenic Mouse Model of Familial Amyotrophic Lateral Sclerosis

Journal of Neurochemistry ◽

10.1046/j.1471-4159.1998.71052041.x ◽

2002 ◽

Vol 71 (5) ◽

pp. 2041-2048 ◽

Author(s):

Paula K. Andrus ◽

Timothy J. Fleck ◽

Mark E. Gurney ◽

Edward D. Hall

Keyword(s):

Amyotrophic Lateral Sclerosis ◽

Mouse Model ◽

Oxidative Damage ◽

Transgenic Mouse ◽

Transgenic Mouse Model ◽

Familial Amyotrophic Lateral Sclerosis ◽

Lateral Sclerosis

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Protein-bound crotonaldehyde accumulates in the spinal cord of superoxide dismutase-1 mutation-associated familial amyotrophic lateral sclerosis and its transgenic mouse model

Neuropathology ◽

10.1111/j.1440-1789.2006.00746.x ◽

2007 ◽

Vol 27 (1) ◽

pp. 49-61 ◽

Author(s):

Noriyuki Shibata ◽

Motoko Kawaguchi ◽

Koji Uchida ◽

Akiyoshi Kakita ◽

Hitoshi Takahashi ◽

...

Keyword(s):

Spinal Cord ◽

Amyotrophic Lateral Sclerosis ◽

Superoxide Dismutase ◽

Mouse Model ◽

Transgenic Mouse ◽

Transgenic Mouse Model ◽

Familial Amyotrophic Lateral Sclerosis ◽

Superoxide Dismutase 1 ◽

Lateral Sclerosis

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