Critical care outcomes in pulmonary atresia and intact ventricular septum undergoing single-ventricle palliation

2010 ◽  
Vol 20 (03) ◽  
pp. 290-296 ◽  
Author(s):  
Mark A. Walsh ◽  
Kentaro Asoh ◽  
Glen S. Van Arsdell ◽  
Tilman Humpl
Keyword(s):  
Critical Care ◽  
Single Ventricle ◽  
Pulmonary Atresia ◽  
Ventricular Septum ◽  
Intact Ventricular Septum ◽  
Critical Care Outcomes ◽  
Care Outcomes ◽  
Single Ventricle Palliation

Pulmonary Atresia/Intact Ventricular Septum: Influence of Coronary Anatomy on Single-Ventricle Outcome

2014 ◽  
Vol 98 (4) ◽  
pp. 1371-1377 ◽  
Author(s):  
Eva W. Cheung ◽  
Marc E. Richmond ◽  
Mariel E. Turner ◽  
Emile A. Bacha ◽  
Alejandro J. Torres
Keyword(s):  
Single Ventricle ◽  
Pulmonary Atresia ◽  
Ventricular Septum ◽  
Intact Ventricular Septum ◽  
Coronary Anatomy

Perioperative and Anesthetic Considerations in Pulmonary Atresia With Intact Ventricular Septum

2017 ◽  
Vol 22 (3) ◽  
pp. 256-264 ◽  
Author(s):  
Stephen Gleich ◽  
Gregory J. Latham ◽  
Denise Joffe ◽  
Faith J. Ross
Keyword(s):  
Pulmonary Valve ◽  
Anesthetic Management ◽  
Treatment Options ◽  
Pulmonary Atresia ◽  
Ventricular Septum ◽  
Intact Ventricular Septum ◽  
Disease Treatment ◽  
Obstructive Lesion ◽  
Anesthetic Considerations ◽  
Single Ventricle Palliation

Pulmonary atresia with intact ventricular septum (PA/IVS) is a rare right-heart obstructive lesion with a wide anatomic and physiologic spectrum of disease, ranging from simple membranous pulmonary valve atresia with a fully developed right ventricle (RV) to a severely hypoplastic RV and ventriculocoronary (RV-coronary) fistulas. Affected neonates are dependent on prostaglandin for adequate pulmonary blood flow. Depending on the severity of disease, treatment options range from transcatheter pulmonary valve perforation and ultimate biventricular repair to staged single-ventricle palliation. Cardiac transplantation is recommended in the most severe cases. This review will discuss the perioperative and anesthetic management of patients with PA/IVS and highlight the challenges in management.

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