A “congenitally corrected” variant of Ebstein’s anomaly

2018 ◽  
Vol 28 (4) ◽  
pp. 608-610
Author(s):  
Rengin Çetin Güvenç ◽  
Gökmen Akgün ◽  
Tolga S. Güvenç
Keyword(s):  
Tricuspid Valve ◽  
Ebstein’S Anomaly ◽  
Tricuspid Annulus ◽  
Ebstein's Anomaly ◽  
Valve Function ◽  
Leaflet Coaptation

AbstractEbstein’s anomaly is a rare CHD that is characterised by caudal displacement of the functional tricuspid annulus and a dysfunctional tricuspid valve owing to a failure of proper leaflet coaptation. We present a balanced variant of Ebstein’s anomaly, in which the overgrowth of the septal leaflet had allowed proper coaptation of the tricuspid leaflets, thus preserving the valve function.

Percutaneous tricuspid valve-in-valve implantation in Ebstein's anomaly: One-year follow-up of valve function

2014 ◽  
Vol 174 (2) ◽  
pp. e77-e78 ◽  
Author(s):  
Colin Cunnington ◽  
J. Andreas Hoschtitzky ◽  
Ragheb Hasan ◽  
Bernard Clarke ◽  
Vaikom S. Mahadevan
Keyword(s):  
Tricuspid Valve ◽  
Ebstein’S Anomaly ◽  
Ebstein's Anomaly ◽  
Valve Function ◽  
Valve In Valve ◽  
One Year ◽  
Valve Implantation

scholarly journals Successful One and One-half Ventricular Circulation with Bioprosthetic Tricuspid Valve Replacement and Total Chordal Preservation in a Patient with Ebstein’s Anomaly: A Video Presentation

2021 ◽  
Vol 5 (02) ◽  
pp. 147-150
Author(s):  
Ujjwal K. Chowdhury ◽  
Sukhjeet Singh ◽  
Niwin George ◽  
Lakshmi Kumari Sankhyan ◽  
Sandeep Sharan ◽  
...  
Keyword(s):  
Right Ventricle ◽  
Tricuspid Valve ◽  
Ebstein’S Anomaly ◽  
Anterior Leaflet ◽  
Tricuspid Annulus ◽  
Tricuspid Valve Replacement ◽  
Rotational Displacement ◽  
Atrioventricular Junction ◽  
Ebstein's Anomaly ◽  
The Right

AbstractEbstein’s anomaly is a rare congenital malformation of the right ventricle and tricuspid valve which is characterized by several features that can exhibit an infinite spectrum of malformation.The abnormalities include: i) adherence of the tricuspid leaflets to the underlying myocardium (failure of delamination); ii) anterior and apical rotational displacement of the functional tricuspid annulus (septal > posterior > anterior leaflet); iii) dilatation of the right atrioventricular junction (the true tricuspid annulus) with variable degrees of hypertrophy and thinning of the wall; iv) dilatation of the “atrialized” portion of the right ventricle; and v) redundancy, fenestration, and tethering of the anterior leaflet.

scholarly journals Ebstein’s Anomaly Corrected by Tissue Valve: Case Report

1970 ◽  
Vol 1 (1) ◽  
pp. 112-114
Author(s):  
SAMA Sabur ◽  
Z Rashid ◽  
A Fazel ◽  
MMG Chowdhury ◽  
M Zaman ◽  
...  
Keyword(s):  
Tricuspid Valve ◽  
Congenital Heart ◽  
Heart Diseases ◽  
Ebstein’S Anomaly ◽  
Tricuspid Valve Repair ◽  
Valve Repair ◽  
Ebstein's Anomaly ◽  
Wpw Syndrome ◽  
Tissue Valve ◽  
Bidirectional Glenn Shunt

Ebstein’s anomaly is a rare form of congenital heart disease with incidence of 1% of all congenital heart diseases. There are two modes of surgical correction of Ebstein’s anomaly: either biventricular repair with or without tricuspid valve replacement, or palliative univentricular repair consisting of bidirectional Glenn shunt or Fontan procedure. We treated a case of severe form of Ebstein’s anomaly with ASD secundum with WPW syndrome. Radiofrequency ablation was done to treat WPW syndrome preoperatively. Celermajer’s index is a prognostic indicator for tricuspid valve repair or replacement. On 04.03.08 tricuspid valve was replaced with 31 mm Carpentier-Edwards bovine pericardial valve under cardiopulmonary bypass. Postoperative period was uneventful. Follow up echo done on 01.06.08 which revealed normally functioning tissue valve found in tricuspid position TR Grade I. So, in conclusion, preoperative evaluation and workout of Celermajer’s index is essential before surgical intervention for decision of tricuspid valve repair or replacement. Last but not the least, any event of arrhythmia should be properly evaluated.Key words: Ebstein’s anomaly, WPW (Wolff- Parkinson-White) Syndrome, Celermajer’s index, Tissue valve. DOI: http://dx.doi.org/10.3329/cardio.v1i1.8213 Cardiovasc. j. 2008; 1(1) : 112-114  

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