Isolated ventricular inversion with hypoplastic right ventricle and pulmonary stenosis in an adolescent with situs solitus: a rare combination

2021 ◽  
pp. 1-3
Author(s):  
Anand K. Mishra ◽  
Sanjeev H. Naganur ◽  
Ruchit Patel ◽  
Vidur Bansal ◽  
Pratyaksha Rana
Keyword(s):  
Right Ventricle ◽  
Rare Case ◽  
Pulmonary Stenosis ◽  
Cardiac Malformation ◽  
Rare Combination ◽  
Congenital Cardiac Malformation ◽  
Hypoplastic Right Ventricle ◽  
Situs Solitus ◽  
Atrioventricular Discordance ◽  
Isolated Ventricular Inversion

Abstract Isolated ventricular inversion with situs solitus is a severe and rare congenital cardiac malformation characterised by an atrioventricular discordance but with ventriculo-arterial concordance. Here, we present the rare case of an adolescent with isolated ventricular inversion and hypoplasia of the left-sided morphological right ventricle and pulmonary stenosis, a first of its kind to be reported in the literature.

scholarly journals Double-Outlet Right Ventricle in a Chianina Calf

Animals ◽  
2021 ◽  
Vol 11 (2) ◽  
pp. 318
Author(s):  
Domenico Caivano ◽  
Maria Chiara Marchesi ◽  
Piero Boni ◽  
Noemi Venanzi ◽  
Giovanni Angeli ◽  
...  
Keyword(s):  
Right Ventricle ◽  
Septal Defect ◽  
Heart Defects ◽  
Double Outlet Right Ventricle ◽  
Cardiac Malformation ◽  
Septal Defects ◽  
Congenital Cardiac Malformation ◽  
The Right ◽  
Similar Complex ◽  
Echocardiographic Findings

Congenital heart defects have been occasionally reported in cattle and ventricular septal defect represents the most frequently encountered anomaly. The double-outlet right ventricle is a rare congenital ventriculoarterial malformation reported only in certain cattle breeds. We describe this rare and complex congenital cardiac malformation observed in a 10-day-old male Chianina calf. Clinical examination showed tachycardia, tachypnea, jugular pulses, cyanotic mucous membranes and a right apical systolic murmur. Transthoracic echocardiography revealed severe dilation of the right-sided cardiac chambers with a markedly hypoplastic left ventricle. Both aorta and pulmonary artery leaving the right ventricle in parallel alignment with the tricuspid valve were suggestive of a dual-outlet right ventricle. Interventricular and interatrial septal defects were also visualized. Post-mortem examination confirmed the echocardiographic findings. To the authors’ knowledge, a similar complex congenital cardiac malformation has not been reported in calves of the Chianina breed to date.

Hypoplastic right ventricle with mild pulmonary stenosis in an adult

1992 ◽  
Vol 37 (2) ◽  
pp. 260-262 ◽  
Author(s):  
K. Prasad ◽  
Mandeep Singh ◽  
S. Radhakrishnan
Keyword(s):  
Right Ventricle ◽  
Pulmonary Stenosis ◽  
Hypoplastic Right Ventricle

Aortopulmonary window, critical pulmonary stenosis, and hypoplastic right ventricle

2008 ◽  
Vol 97 (7) ◽  
pp. 467-469 ◽  
Author(s):  
Martin Koestenberger ◽  
Bert Nagel ◽  
Gerhard Cvirn ◽  
Albrecht Beitzke
Keyword(s):  
Right Ventricle ◽  
Pulmonary Stenosis ◽  
Aortopulmonary Window ◽  
Hypoplastic Right Ventricle ◽  
Critical Pulmonary Stenosis

Incomplete isolation of the left innominate artery from the right aortic arch: a rare case of double-outlet right ventricle with pulmonary stenosis

2019 ◽  
Vol 29 (5) ◽  
pp. 717-719
Author(s):  
Jun Sato ◽  
Atsuko Kato ◽  
Naoki Ohashi
Keyword(s):  
Right Ventricle ◽  
Aortic Arch ◽  
Rare Case ◽  
Surgical Repair ◽  
Pulmonary Stenosis ◽  
Innominate Artery ◽  
Double Outlet Right Ventricle ◽  
Right Aortic Arch ◽  
Female Infant ◽  
The Right

AbstractIsolation of the left innominate artery from the right aortic arch is a rare anomaly. Herein, we present an even rarer case of incomplete isolation of the proximal left innominate artery with the right aortic arch in a 3-month-old female infant with a double-outlet right ventricle and pulmonary stenosis. Surgical repair at 6 months of age was successful, leading to the restoration of adequate flow in the left arm.

scholarly journals Late Presentation of Aortopulmonary Window with Tetralogy of Fallot: Report of a Very Rare Case

2021 ◽  
pp. 1-3
Author(s):  
Muhammad Ishtiaque Sayeed Al-Manzo ◽  
Prodip Kumar Biswas ◽  
M.A.K. Azad ◽  
Eliyas Patwary ◽  
Jesmin Hossain ◽  
...  
Keyword(s):  
Tetralogy Of Fallot ◽  
Rare Case ◽  
Surgical Repair ◽  
Preoperative Evaluation ◽  
Late Presentation ◽  
Aortopulmonary Window ◽  
Cardiac Malformation ◽  
Congenital Cardiac Malformation

Aortopulmonary window (APW) itself is a rare congenital cardiac malformation and its association with Tetralogy of Fallot (TOF) makes it more uncommon. We report a case of APW with TOF who presented at 4-year 10 months of age. As the boy was still in operable state, after thorough preoperative evaluation successful surgical repair was done.

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