scholarly journals Double-Outlet Right Ventricle in a Chianina Calf

Animals ◽  
2021 ◽  
Vol 11 (2) ◽  
pp. 318
Author(s):  
Domenico Caivano ◽  
Maria Chiara Marchesi ◽  
Piero Boni ◽  
Noemi Venanzi ◽  
Giovanni Angeli ◽  
...  
Keyword(s):  
Right Ventricle ◽  
Septal Defect ◽  
Heart Defects ◽  
Double Outlet Right Ventricle ◽  
Cardiac Malformation ◽  
Septal Defects ◽  
Congenital Cardiac Malformation ◽  
The Right ◽  
Similar Complex ◽  
Echocardiographic Findings

Congenital heart defects have been occasionally reported in cattle and ventricular septal defect represents the most frequently encountered anomaly. The double-outlet right ventricle is a rare congenital ventriculoarterial malformation reported only in certain cattle breeds. We describe this rare and complex congenital cardiac malformation observed in a 10-day-old male Chianina calf. Clinical examination showed tachycardia, tachypnea, jugular pulses, cyanotic mucous membranes and a right apical systolic murmur. Transthoracic echocardiography revealed severe dilation of the right-sided cardiac chambers with a markedly hypoplastic left ventricle. Both aorta and pulmonary artery leaving the right ventricle in parallel alignment with the tricuspid valve were suggestive of a dual-outlet right ventricle. Interventricular and interatrial septal defects were also visualized. Post-mortem examination confirmed the echocardiographic findings. To the authors’ knowledge, a similar complex congenital cardiac malformation has not been reported in calves of the Chianina breed to date.

Triple Outlet Right Ventricle, With Duplication of the Aortic Root and Intrapericardial Ascending Aorta

2017 ◽  
Vol 11 (4) ◽  
pp. NP94-NP98 ◽  
Author(s):  
Ashish Katewa ◽  
Balswaroop Sahu ◽  
Vishal Jain ◽  
Robert H. Anderson
Keyword(s):  
Computed Tomography ◽  
Right Ventricle ◽  
Aortic Root ◽  
Double Outlet Right Ventricle ◽  
Ascending Aorta ◽  
Cardiac Malformation ◽  
Aortic Valves ◽  
Congenital Cardiac Malformation ◽  
Infundibular Stenosis ◽  
The Right

We present a case of a highly unusual congenital cardiac malformation, namely, triple outlet right ventricle with duplication of the aortic root and the intrapericardial component of the ascending aorta. A girl, aged five, presented with complaints of cyanosis and effort intolerance and was diagnosed with double-outlet right ventricle and subpulmonary infundibular stenosis. Intraoperatively, we noted that the aortic root was guarded by two separate aortic valves, oriented anteroposteriorly relative to each other, and separated within the right ventricle by a muscle bar. Postoperative interrogation by both echocardiography and computed tomography confirmed the surgical findings. To the best of our knowledge, our case is the first example of duplication of the aortic root to produce triple outlet right ventricle.

Sectional anatomy of the ventricular septal defect in double outlet right ventricle—correlation of magnetic resonance images from autopsied hearts with anatomic sections

1993 ◽  
Vol 3 (2) ◽  
pp. 118-123 ◽  
Author(s):  
Shi-Joon Yoo ◽  
Siew Yen Ho ◽  
Philip J. Kilner ◽  
Jeong-Wook Seo ◽  
Robert H. Anderson
Keyword(s):  
Ventricular Septal Defect ◽  
Right Ventricle ◽  
Septal Defect ◽  
Double Outlet Right Ventricle ◽  
Magnetic Resonance Images ◽  
Cross Sectional ◽  
Posterior Limb ◽  
Imaging Characteristics ◽  
Cross Sectional Imaging ◽  
The Right

AbstractA ventricular septal defect is, almost always, an integral part of double outlet right ventricle and has been classified into the subaortic, subpulmonary, doubly committed and non-committed varieties. This study was performed to correlate the cross-sectional imaging characteristics of such ventricular septal defect in double outlet right ventricles using pathological specimens. The extent and the orientation of the outlet septum were the most important in the differentiation of the four varieties of ventricular septal defect. In the subaortic variety, the outlet septum fused with the left anterior margin of the defect, this being marked by the anterior limb of the septomarginal trabeculation. In the subpulmonary variety, the outlet septum fused with the right posterior margin of the defect, this being the posterior limb of the septomarginal trabeculation. The outlet septum was vestigial in case with doubly committed defects. In those with non-committed defects, the defect was not shown in those images or sections which demonstrated the outlet septum.

scholarly journals Cardiac Septal Defects in Children: Hemodynamics, Clinical Manifestations and Detection

2021 ◽  
Vol 5 (4) ◽  
Author(s):  
Ria Nova ◽  
Sukman Tulus Putra ◽  
Siti Nurmaini ◽  
Radiyati Umi Partan
Keyword(s):  
Clinical Examination ◽  
Congenital Heart ◽  
Septal Defect ◽  
Heart Defects ◽  
Clinical Manifestations ◽  
Ventricular Septal Defects ◽  
Hemodynamic Changes ◽  
Septal Defects ◽  
Cardiac Septal Defects ◽  
The Right

Cardiac septal defect in children is one of the congenital heart defects characterized by atrial septal defects (ASD), ventricular septal defects (VSD) and defects in both atrial and ventricular septum (AVSD). The hemodynamic changes that occur are caused by a left to the right shunt. Differences in location, size of the defect and pulmonary vascular resistance make hemodynamic differences and clinical manifestations between the three types of cardiac septal defects. Detection of cardiac septal defects can be done by clinical examination by listening to the characteristic heart sounds and murmurs for each defect. However, clinical examination alone is often still difficult to determine the type of cardiac septal defect so that several supporting examinations such as photothorax, ECG, echocardiogram and cardiac catheterization need to be done to help establish the diagnosis.

scholarly journals Cardiac Septal Defects in Children: Hemodynamics, Clinical Manifestations and Detection

2021 ◽  
Vol 5 (6) ◽  
pp. 608-613
Author(s):  
Ria Nova ◽  
Sukman Tulus Putra ◽  
Siti Nurmaini ◽  
Radiyati Umi Partan
Keyword(s):  
Clinical Examination ◽  
Congenital Heart ◽  
Septal Defect ◽  
Heart Defects ◽  
Clinical Manifestations ◽  
Ventricular Septal Defects ◽  
Hemodynamic Changes ◽  
Septal Defects ◽  
Cardiac Septal Defects ◽  
The Right

Cardiac septal defect in children is one of the congenital heart defects characterized by atrial septal defects (ASD), ventricular septal defects (VSD) and defects in both atrial and ventricular septum (AVSD). The hemodynamic changes that occur are caused by a left to the right shunt. Differences in location, size of the defect and pulmonary vascular resistance make hemodynamic differences and clinical manifestations between the three types of cardiac septal defects. Detection of cardiac septal defects can be done by clinical examination by listening to the characteristic heart sounds and murmurs for each defect. However, clinical examination alone is often still difficult to determine the type of cardiac septal defect so that several supporting examinations such as photothorax, ECG, echocardiogram and cardiac catheterization need to be done to help establish the diagnosis.

scholarly journals A case of an uncorrected double outlet right ventricle with ventricular septal defect in pregnancy

2019 ◽  
Vol 8 (9) ◽  
pp. 3805
Author(s):  
Kedar M. Tilak ◽  
Uma N. Wankhede
Keyword(s):  
Congenital Heart Disease ◽  
Right Ventricle ◽  
Congenital Heart ◽  
Multidisciplinary Approach ◽  
Septal Defect ◽  
Heart Diseases ◽  
Double Outlet Right Ventricle ◽  
Congenital Heart Diseases ◽  
The Right ◽  
In Pregnancy

Congenital Heart Diseases (CHD) lead to various changes in the normal mechanisms of hemodynamics. Pregnancy in women with CHDs is rare. Double Outlet Right Ventricle (DORV) is a rare disorder, in which both the aorta and the pulmonary artery arise from the right ventricle. We present a case of a thirty-year-old pregnant woman who presented to us with 22 weeks of amenorrhea. She had DORV with VSD, which was undiagnosed till she came to our hospital. Double Outlet Right Ventricle (DORV) is a rare congenital heart disease. Pregnancy in a patient with DORV needs early diagnosis and a stepwise multidisciplinary approach for successful outcomes.

A Woman with Double Chamber Right Ventricle

2021 ◽  
Vol 7 (1) ◽  
pp. 63-67
Author(s):  
Furqon Satria Adi Pradana ◽  
Lucia Kris Dinarti ◽  
Putrika Prastuti Ratna Gharini
Keyword(s):  
Right Ventricle ◽  
Congenital Heart ◽  
Septal Defect ◽  
Heart Defects ◽  
Transoesophageal Echocardiography ◽  
Surgical Closure ◽  
Muscle Band ◽  
The Right ◽  
Double Chamber

Introduction: An additional membrane or muscle band inside right ventricle divides it into two chambers, the proximal and distal one. It is a rare congenital malformation which makes up approximately 0.5-1 per cent of all congenital heart defects. The double chambers right ventricle most often present in children but rarely in adults. Transoesophageal Echocardiography is the most effective tool in diagnosing a DCRV.Case presentation: A 36 years old woman, diagnosed with large ventricular septal defect by transthoracic echocardiography, underwent a TOE to complement the preparation of surgical closure. The TOE finding instead revealed a septum or membrane that divide the right ventricle into two separate chambers, later confirmed by a cardiac computer tomographic scan and cardiac cathetherization. The patient underwent surgery with VSD closure and resection of the septum without complications. Echocardiography paramater became normal albeit still had some septal tissue left in order to limit sudden surge of blood flow into pulmonary artery. Follow up indicate patient has no symptom associated with the surgeryConclusion: The patient was diagnosed with double chamber right ventricle during preparation for surgery by TOE examination. We present this case in order to emphasize the rarity of this congenital heart disease

Echocardiographic Diagnosis of Congenital Membranous Ventricular Septal Aneurysm in the Dog and Cat

2005 ◽  
Vol 41 (4) ◽  
pp. 215-220 ◽  
Author(s):  
William P. Thomas
Keyword(s):  
Ventricular Septal Defect ◽  
Right Ventricle ◽  
Cardiac Dysfunction ◽  
Congenital Heart ◽  
Septal Defect ◽  
Incidental Finding ◽  
Heart Defects ◽  
Thin Membrane ◽  
Echocardiographic Examination ◽  
The Right

Membranous ventricular septal aneurysm was diagnosed by echocardiography in 17 dogs and three cats. The aneurysm appeared as a thin membrane protruding into the right ventricle from the margins of a congenital ventricular septal defect (VSD). The aneurysm was intact in nine dogs and two cats and perforated by a small VSD in eight dogs and one cat. Other congenital heart defects were present in seven dogs. In all animals, the aneurysm was an incidental finding observed during echocardiographic examination, and it did not appear to directly cause any cardiac dysfunction.

Tetralogy of Fallot: nosological, morphological, and morphogenetic considerations

2013 ◽  
Vol 23 (6) ◽  
pp. 858-866 ◽  
Author(s):  
Robert H. Anderson ◽  
Diane E. Spicer ◽  
Jorge M. Giroud ◽  
Timothy J. Mohun
Keyword(s):  
Ventricular Septal Defect ◽  
Right Ventricle ◽  
Tetralogy Of Fallot ◽  
Septal Defect ◽  
Morphological Changes ◽  
Double Outlet Right Ventricle ◽  
125Th Anniversary ◽  
Initial Description ◽  
The Right ◽  
Subpulmonary Stenosis

AbstractIt is timely, in the 125th anniversary of the initial description by Fallot of the hearts most frequently seen in patients presenting with “la maladie bleu”, that we revisit his descriptions, and discuss his findings in the light of ongoing controversies. Fallot described three hearts in his initial publication, and pointed to the same tetralogy of morphological features that we recognise today, namely, an interventricular communication, biventricular connection of the aorta, subpulmonary stenosis, and right ventricular hypertrophy. In one of the hearts, he noted that the aorta arose exclusively from the right ventricle. In other words, one of his initial cases exhibited double-outlet right ventricle. When we now compare findings in hearts with the features of the tetralogy, we can observe significant variations in the nature of the borders of the plane of deficient ventricular septation when viewed from the aspect of the right ventricle. We also find that this plane, usually described as the ventricular septal defect, is not the same as the geometric plane separating the cavities of the right and left ventricles. This means that the latter plane, the interventricular communication, is not necessarily the same as the ventricular septal defect. We are now able to provide further insights into these features by examining hearts prepared from developing mice. Additional molecular investigations will be required, however, to uncover the mechanisms responsible for producing the morphological changes underscoring tetralogy of Fallot.

Repair of double outlet right ventricle with doubly-committed ventricular septal defect

2001 ◽  
Vol 11 (4) ◽  
pp. 415-419 ◽  
Author(s):  
Hideki Uemura ◽  
Toshikatsu Yagihara ◽  
Takayuki Kadohama ◽  
Youichi Kawahira ◽  
Yoshiro Yoshikawa
Keyword(s):  
Ventricular Septal Defect ◽  
Right Ventricle ◽  
Septal Defect ◽  
Pulmonary Stenosis ◽  
Pulmonary Arteries ◽  
Ventricular Outflow Tract ◽  
Double Outlet Right Ventricle ◽  
Left Ventricular ◽  
Aortic Orifice ◽  
The Right

Objective: To investigate our surgical results of intraventricular rerouting in patients having double outlet right ventricle with doubly-committed ventricular septal defect. Methods: We undertook repair in 8 patients with this particular feature. Of these, 2 patients had pulmonary stenosis, and another had interruption of the aortic arch. The subarterial defect was unequivocally related to both the aortic and the pulmonary orifices in all, albeit slightly deviated towards the aortic orifice in one, and towards the pulmonary orifice in another. Intraventricular rerouting was carried out via incisions to the right atrium and the pulmonary trunk. To ensure reconstruction of an unobstructed pulmonary pathway, a limited right ventriculotomy was made in 5. Results: All patients survived the procedure, and are currently doing well, with follow-up of 25 to 194 months, with a mean of 117 ± 68 months. Catheterization carried out 16 ± 6 months after repair demonstrated excellent ventricular parameters. Mean pulmonary arterial pressure was 16 ± 7 mmHg, being higher than 20 mmHg in 2 patients. No significant obstruction was found between the right ventricle and the pulmonary arteries. A pressure gradient across the left ventricular outflow tract became significant in one patient in whom a small outlet septum was present, and a heart-shaped baffle had been used for intraventricular rerouting. Reoperation was eventually needed in this patient for treatment of the obstruction, which proved to be progressive. Conclusion: Precise recognition of the morphologic features is of paramount importance when choosing the optimal options for biventricular repair in patients with double outlet right ventricle and doubly-committed interventricular communication.

Abstract 2335: Transposition Of The Great Arteries And Double Outlet Right Ventricle Have Related Early Developmental Origins: Fundamental Insights From In Vivo Imaging

Circulation ◽  
2007 ◽  
Vol 116 (suppl_16) ◽  
Author(s):  
Colin K Phoon ◽  
Ruiping Ji ◽  
Piyali Dhar Chowdhury
Keyword(s):  
Right Ventricle ◽  
Cardiac Function ◽  
Heart Defects ◽  
Left Pulmonary Artery ◽  
Ultrasound Biomicroscopy ◽  
Double Outlet Right Ventricle ◽  
Doppler Imaging ◽  
Truncus Arteriosus ◽  
The Right

Congenital heart defects (CHD) are the most common birth defect. Proper retinoic acid (RA) signaling is required for normal development, and RA excess produces conotruncal CHD such as transposition of the great arteries (TGA) and double outlet right ventricle (DORV). We hypothesized that origins and evolution of TGA and DORV follow specific developmental patterns, definable in vivo by noninvasive ultrasound biomicroscopy (UBM)-Doppler imaging. Timed-pregnant ICR mice were injected with 70 mg/kg IP RA at 8.5 days post-conception (E8.5). Individual embryos were tracked with 40 MHz UBM-Doppler longitudinally on 5 consecutive days (E11.5–15.5: N=34 injected, N=8 uninjected controls). CHD included TGA (24%) and DORV (21%, all with right aorta, left pulmonary artery), as well as ventricular septal defect (VSD, defined at E15.5) and double-inlet left ventricle. External gross examination and histology confirmed ~90% concordance of UBM diagnosis of CHD, here (at E15.5) and in separate experiments (E11.5–15.5, N=111). All E11.5 embryos showed normal cardiac looping, with a normal unseptated heart and outflow tract (OFT) - the truncus arteriosus -arising from the right ventricle/bulbus cordis. Of embryos destined for TGA, 7/8 showed partial septation of the distal truncus into parallel OFT at E12.5; 4 showed DORV at E12.5 before evolving into TGA by E13.5. Of embryos destined for DORV, 6/7 showed partial septation of the distal truncus into parallel OFT at E12.5 as well. Thus, abnormal septation commences in the more distal truncus arteriosus as early as E12.5. In contrast, embryos destined for normal OFT development showed partial OFT septation in spiral (non-parallel) fashion, with complete/near-complete OFT septation and morphology at E13.5. All TGA/DORV embryos displayed normal cardiac function. CONCLUSIONS. TGA and DORV are developmentally related, differing only in complete (TGA) vs. incomplete (DORV) leftward truncal shift. Given normal heart, proximal OFT, and cardiac function, flow streams do not explain TGA/DORV morphogenesis. Corresponding to 4–6 weeks’ human gestation, these first in vivo data support longstanding hypotheses of TGA/DORV embryogenesis, and implicate RA signaling in the pathogenesis of abnormal truncal septation and shift.

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