scholarly journals Late Presentation of Aortopulmonary Window with Tetralogy of Fallot: Report of a Very Rare Case

2021 ◽  
pp. 1-3
Author(s):  
Muhammad Ishtiaque Sayeed Al-Manzo ◽  
Prodip Kumar Biswas ◽  
M.A.K. Azad ◽  
Eliyas Patwary ◽  
Jesmin Hossain ◽  
...  
Keyword(s):  
Tetralogy Of Fallot ◽  
Rare Case ◽  
Surgical Repair ◽  
Preoperative Evaluation ◽  
Late Presentation ◽  
Aortopulmonary Window ◽  
Cardiac Malformation ◽  
Congenital Cardiac Malformation

Aortopulmonary window (APW) itself is a rare congenital cardiac malformation and its association with Tetralogy of Fallot (TOF) makes it more uncommon. We report a case of APW with TOF who presented at 4-year 10 months of age. As the boy was still in operable state, after thorough preoperative evaluation successful surgical repair was done.

The current surgical perspective to repair of atrioventricular septal defect with common atrioventricular junction

2010 ◽  
Vol 20 (S3) ◽  
pp. 120-127 ◽  
Author(s):  
Tom R. Karl ◽  
Sylvio C. J. Provenzano ◽  
Graham R. Nunn ◽  
Robert H. Anderson
Keyword(s):  
Tetralogy Of Fallot ◽  
Septal Defect ◽  
Surgical Repair ◽  
Atrioventricular Septal Defect ◽  
Indications For Surgery ◽  
Cardiac Malformation ◽  
Technical Aspects ◽  
Atrioventricular Junction ◽  
Congenital Cardiac Malformation ◽  
Surgery Timing

AbstractAtrioventricular septal defect with common atrioventricular junction is a relatively common congenital cardiac malformation. It sometimes presents challenging surgical problems, especially when seen in combination with tetralogy of Fallot. We describe herein our current concepts regarding surgical repair of atrioventricular septal defect with and without tetralogy, discussing indications for surgery, timing, technical aspects, and outcomes.

scholarly journals Tetralogy of Fallot with Scimitar syndrome in VACTERL: a very rare association

2017 ◽  
Vol 5 (1) ◽  
pp. 269
Author(s):  
Puneet Anand
Keyword(s):  
Congenital Anomaly ◽  
Tetralogy Of Fallot ◽  
Management Strategy ◽  
Septal Defect ◽  
Early Embryogenesis ◽  
Scimitar Syndrome ◽  
Cardiac Malformation ◽  
Rare Congenital Anomaly ◽  
Rare Association ◽  
Congenital Cardiac Malformation

The most common congenital cardiac malformation that occurs in VACTERL association is ventricular septal defect. Scimitar syndrome is a very rare congenital anomaly of the heart occurring due to maldevelopment of the lung bud or the pulmonary vascularization during early embryogenesis. The occurrence of Scimitar syndrome in VACTERL and its association with another cardiac congenital anomaly such as Tetralogy of Fallot (TOF) is extremely rare. The association of Tetralogy of Fallot with Scimitar syndrome alters the management strategy. Hereby, a very rare combination of Scimitar syndrome and tetralogy of Fallot in a four-year-old boy with VACTERL is presented, who underwent a successful single-stage surgical correction.

scholarly journals A forme fruste of Shone’s anomaly in a 65 year-old patient

2020 ◽  
Vol 11 (1) ◽  
Author(s):  
Sherif E Moustafa ◽  
Jacques Lesperance ◽  
Jean-Lucien Rouleau ◽  
Gilbert Gosselin
Keyword(s):  
Cardiac Catheterization ◽  
Rare Case ◽  
Left Heart ◽  
Cardiac Malformation ◽  
Incomplete Form ◽  
Congenital Cardiac Malformation ◽  
Multiple Levels ◽  
Malformation Complex

Shone’s anomaly, a congenital cardiac malformation complex, consists of multiple levels of left heart obstruction. A rare case of an incomplete form of this anomaly discovered incidentally during cardiac catheterization for an unrelated event is described.

scholarly journals A Rare Case of Chronic Expanding Intrapericardial Hematoma with Refractory Right-sided Heart Failure 30 Years after the Surgical Repair of Tetralogy of Fallot

2021 ◽  
Author(s):  
Satoshi Nakawatase ◽  
Yoshinori Asae ◽  
Yoshiyuki Miyamoto ◽  
Masaoki Miyamoto ◽  
Yasushi Okumoto ◽  
...  
Keyword(s):  
Heart Failure ◽  
Tetralogy Of Fallot ◽  
Rare Case ◽  
Surgical Repair

Aortopulmonary Window with Subaortic Fibrous Stenosis and Septal Defect: Surgery through a Minimal Right Vertical Infra-Axillary Thoracotomy

2011 ◽  
Vol 14 (4) ◽  
pp. 264 ◽  
Author(s):  
Jun Pan ◽  
Qing-Guo Li ◽  
Qing Zhou ◽  
Jie Zhang ◽  
Qiang Wang ◽  
...  
Keyword(s):  
Minimally Invasive Surgery ◽  
Cardiopulmonary Bypass ◽  
Ventricular Septal Defect ◽  
Minimally Invasive ◽  
Invasive Surgery ◽  
Septal Defect ◽  
Subaortic Stenosis ◽  
Aortopulmonary Window ◽  
Cardiac Malformation ◽  
Congenital Cardiac Malformation

Aortopulmonary window with subaortic stenosis and ventricular septal defect is an uncommon congenital cardiac malformation that is repaired using cardiopulmonary bypass. The authors describe a 3-year-old patient on whom we performed surgery through a minimal right vertical infra-axillary thoracotomy. This minimally invasive surgery is likely to be applicable in a few cases.

scholarly journals Amiodarone-induced thyrotoxicosis in a pediatric patient: A rare and demanding clinical case

2019 ◽  
Vol 11 (3) ◽  
Author(s):  
Sofia Oliveira ◽  
Bernardo Marques ◽  
Sérgio Laranjo ◽  
Lurdes Lopes
Keyword(s):  
Pediatric Patient ◽  
Rare Case ◽  
Thyroid Dysfunction ◽  
Specific Treatment ◽  
Paroxysmal Supraventricular Tachycardia ◽  
Amiodarone Therapy ◽  
Cardiac Malformation ◽  
Congenital Cardiac Malformation

Thyroid dysfunction is one of the most common adverse effects of amiodarone therapy, ranging from subclinical changes to overt clinical thyrotoxicosis (AIT) and/or hypothyroidism. Due to its heterogeneity, AIT lasts as a defiant entity, leading to a thorny treatment course, particularly in pediatrics. AIT can be classified as either type 1, type 2 or mixed form based on its pathophysiology. Differentiating between the main AIT subtypes is quite relevant, since there is specific treatment for both, however, this distinction may be difficult in clinical practice. We describe a rare case of AIT in a pediatric patient, with an uncommon congenital cardiac malformation, that started amiodarone therapy due to paroxysmal supraventricular tachycardia. AIT was reported 26 months after drug onset, with a sudden and explosive emerging. This case highlights the current AIT management challenges on the highdemanding pediatric field pursuing, ultimately, an enhanced patient´'s care.

scholarly journals Prenatal ultrasound diagnosis of fetal giant left ventricular aneurysm： A case report

2021 ◽  
Author(s):  
Wenjing Guo ◽  
Dengcai Zhang ◽  
Tingting Yao ◽  
Bin Ma ◽  
Tian-gang Li
Keyword(s):  
Case Report ◽  
Prenatal Diagnosis ◽  
Rare Case ◽  
Left Ventricular ◽  
Left Ventricular Aneurysm ◽  
Ventricular Aneurysm ◽  
Prenatal Ultrasonography ◽  
Cardiac Malformation ◽  
Congenital Cardiac Malformation ◽  
Ultrasound Technology

Fetal ventricular aneurysm is a rare congenital cardiac malformation that can occur in various cardiac cavities and often exists in isolation without other malformations. Modern ultrasound technology can assist the prenatal diagnosis of ventricular aneurysm. Herein, we will present a rare case of a giant left ventricular aneurysm detected by prenatal ultrasonography.

Isolated ventricular inversion with hypoplastic right ventricle and pulmonary stenosis in an adolescent with situs solitus: a rare combination

2021 ◽  
pp. 1-3
Author(s):  
Anand K. Mishra ◽  
Sanjeev H. Naganur ◽  
Ruchit Patel ◽  
Vidur Bansal ◽  
Pratyaksha Rana
Keyword(s):  
Right Ventricle ◽  
Rare Case ◽  
Pulmonary Stenosis ◽  
Cardiac Malformation ◽  
Rare Combination ◽  
Congenital Cardiac Malformation ◽  
Hypoplastic Right Ventricle ◽  
Situs Solitus ◽  
Atrioventricular Discordance ◽  
Isolated Ventricular Inversion

Abstract Isolated ventricular inversion with situs solitus is a severe and rare congenital cardiac malformation characterised by an atrioventricular discordance but with ventriculo-arterial concordance. Here, we present the rare case of an adolescent with isolated ventricular inversion and hypoplasia of the left-sided morphological right ventricle and pulmonary stenosis, a first of its kind to be reported in the literature.

scholarly journals Aorto-pulmonary Window, a Rare Congenital Heart Disease: Case Report

2021 ◽  
pp. 17-21
Author(s):  
M. Lakhrissi ◽  
A. Ayad ◽  
M. Kmari ◽  
A. Ourrai ◽  
A. Hassani ◽  
...  
Keyword(s):  
Respiratory Symptoms ◽  
Congenital Heart ◽  
Ascending Aorta ◽  
Pulmonary Vascular Disease ◽  
Aortopulmonary Window ◽  
Cardiac Malformation ◽  
Heart Murmurs ◽  
Associated Lesions ◽  
Congenital Cardiac Malformation ◽  
Disease Case

Aortopulmonary window (APW) is an uncommon congenital cardiac malformation, accounting for 0.1% of all congenital cardiac diseases. It is a defect between the ascending aorta and the trunk of the pulmonary artery. Such abnormality may occur as an isolated lesion or it can be associated with other cardiac abnormalities in one third to one half of cases. Clinical and hemodynamic presentation of this condition depends on the size of the defect and on the associated lesions. It is usually fatal in infancy or childhood if untreated with the development of irreversible pulmonary hypertension. Once the diagnosis is made, surgery must be performed quickly to avoid irreversible pulmonary vascular disease. We report the case of a 5-month-old infant with APW who was referred to our center by respiratory symptoms and heart murmurs.

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