Transjugular intrahepatic portosystemic shunt prior to renal transplantation in a child with autosomal-recessive polycystic kidney disease and portal hypertension: A case report

2001 ◽  
Vol 5 (3) ◽  
pp. 210-214 ◽  
Author(s):  
Nadine Benador ◽  
Paul Grimm ◽  
Joel Lavine ◽  
Philip Rosenthal ◽  
Vivian Reznik ◽  
...  
Keyword(s):  
Case Report ◽  
Portal Hypertension ◽  
Renal Transplantation ◽  
Kidney Disease ◽  
Polycystic Kidney Disease ◽  
Transjugular Intrahepatic Portosystemic Shunt ◽  
Autosomal Recessive ◽  
Portosystemic Shunt ◽  
Polycystic Kidney ◽  
Intrahepatic Portosystemic Shunt

scholarly journals Occurrence of Portal Hypertension and Its Clinical Course in Patients With Molecularly Confirmed Autosomal Recessive Polycystic Kidney Disease (ARPKD)

2020 ◽  
Vol 8 ◽  
Author(s):  
Dorota Wicher ◽  
Ryszard Grenda ◽  
Mikołaj Teisseyre ◽  
Marek Szymczak ◽  
Paulina Halat-Wolska ◽  
...  
Keyword(s):  
Portal Hypertension ◽  
Kidney Disease ◽  
Polycystic Kidney Disease ◽  
Autosomal Recessive ◽  
Clinical Course ◽  
Polycystic Kidney

Autosomal-recessive polycystic kidney disease in children

2016 ◽  
Vol 7 (4) ◽  
pp. 45-49 ◽  
Author(s):  
Elvira F Andreeva ◽  
Nadejda D Savenkova ◽  
Mohamed A Tilouche ◽  
Natalya Y Natochina ◽  
Igor V Dug
Keyword(s):  
Portal Hypertension ◽  
Kidney Disease ◽  
Arterial Hypertension ◽  
Polycystic Kidney Disease ◽  
Autosomal Recessive ◽  
Varicose Veins ◽  
Clinical Manifestations ◽  
Polycystic Kidney ◽  
Stage Renal Disease ◽  
Neonates And Infants

The aim of the study was to assess the features of development of renal and extrarenal cysts, arterial hypertension, syndrome of portal hypertension in autosomal recessive polycystic kidney disease (ARPKD) in children. Patients and me­thods. With the aim of establishing the type of inheritance of polycystic kidney disease the genealogical analysis of 12 families, clinical ultrasound of the kidneys and abdominal organs, computed tomography. The study included 14 children with ARPKD. Conducted follow-up study of 14 children with ARPKD to determine the age by the detection of cysts based on ultrasound, the features of the initial clinical manifestations and course, complications and outcome.Results: the Age of the children back to the time of detection of the cysts in the kidneys based on ultrasound when ARPKD was 2.3 ± 0.4 month. Identified a high incidence of arterial hypertension in neonates and infants with ARPKD at 92.9%. Extrarenal location of the cysts is set at 71.4%. Syndrome of portal hypertension, bleeding from varicose veins of esophagus and stomach, melanau installed in 5 (35,7%) children. Of the 14 in 5 (35,7%) patients diagnosed ARPKD children with liver fibrosis, which has a favorable prognosis without the formation of renal failure in infants and early childhood, 9 (64,3%) diagnosed with classic ARPKD in neonates and infants that is characterized by progression to end-stage renal disease in the first year of life.

Morbidity from Congenital Hepatic Fibrosis after Renal Transplantation for Autosomal Recessive Polycystic Kidney Disease

2002 ◽  
Vol 2 (4) ◽  
pp. 360-365 ◽  
Author(s):  
Khalid Khan ◽  
Sara Jane Schwarzenberg ◽  
Harvey L. Sharp ◽  
Arthur J. Matas ◽  
Blanche M. Chavers
Keyword(s):  
Renal Transplantation ◽  
Kidney Disease ◽  
Polycystic Kidney Disease ◽  
Hepatic Fibrosis ◽  
Autosomal Recessive ◽  
Congenital Hepatic Fibrosis ◽  
Polycystic Kidney

scholarly journals Prenatal diagnosis of autosomal recessive polycystic kidney disease. A case report.

1999 ◽  
Vol 66 (3) ◽  
pp. 188-190
Author(s):  
Katsuya Mine ◽  
Shunji Suzuki ◽  
Shouichi Watanabe ◽  
Rintaro Sawa ◽  
Yoshio Yoneyama ◽  
...  
Keyword(s):  
Case Report ◽  
Prenatal Diagnosis ◽  
Kidney Disease ◽  
Polycystic Kidney Disease ◽  
Autosomal Recessive ◽  
Polycystic Kidney
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